Emerin deficiency does not exacerbate cardiomyopathy in a murine model of Emery–Dreifuss muscular dystrophy caused by an LMNA gene mutation

Abstract Emery–Dreifuss muscular dystrophy (EDMD), caused by mutations in genes encoding nuclear envelope proteins, is clinically characterized by muscular dystrophy, early joint contracture, and life-threatening cardiac abnormalities. To elucidate the pathophysiological mechanisms underlying striat...

Full description

Saved in:
Bibliographic Details
Main Authors: Eiji Wada, Kohei Matsumoto, Nao Susumu, Megumi Kato, Yukiko K. Hayashi
Format: Article
Language:English
Published: Elsevier 2023-11-01
Series:Journal of Physiological Sciences
Subjects:
Online Access:https://doi.org/10.1186/s12576-023-00886-0
Tags: Add Tag
No Tags, Be the first to tag this record!