Klippel-Trenaunay Syndrome Causing Life-Threatening GI Bleeding: A Case Report and Review of the Literature
Klippel-Trenaunay syndrome (KTS) is a rare congenital syndrome of vascular malformations and soft tissue and bone hypertrophy. Vascular malformations can affect multiple organ systems. Involvement of the gastrointestinal (GI) tract is uncommon in KTS, but it can be a source of life-threatening bleed...
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| Format: | Article |
| Language: | English |
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Wiley
2013-01-01
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| Series: | Case Reports in Gastrointestinal Medicine |
| Online Access: | http://dx.doi.org/10.1155/2013/813653 |
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| author | Salih Samo Muhammed Sherid Husein Husein Samian Sulaiman Margaret Yungbluth John A. Vainder |
| author_facet | Salih Samo Muhammed Sherid Husein Husein Samian Sulaiman Margaret Yungbluth John A. Vainder |
| author_sort | Salih Samo |
| collection | DOAJ |
| description | Klippel-Trenaunay syndrome (KTS) is a rare congenital syndrome of vascular malformations and soft tissue and bone hypertrophy. Vascular malformations can affect multiple organ systems. Involvement of the gastrointestinal (GI) tract is uncommon in KTS, but it can be a source of life-threatening bleeding. We report a case of a 32-year-old male with a known diagnosis of KTS who presented with a life-threatening rectal bleeding and was treated with proctosigmoidectomy and massive blood products transfusion. He expired after a long hospitalization. We then review the literature on KTS and management of some of its complications. |
| format | Article |
| id | doaj-art-de82bc34e6384bf9a720ec37b5f280b9 |
| institution | Kabale University |
| issn | 2090-6528 2090-6536 |
| language | English |
| publishDate | 2013-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Gastrointestinal Medicine |
| spelling | doaj-art-de82bc34e6384bf9a720ec37b5f280b92025-02-03T01:24:06ZengWileyCase Reports in Gastrointestinal Medicine2090-65282090-65362013-01-01201310.1155/2013/813653813653Klippel-Trenaunay Syndrome Causing Life-Threatening GI Bleeding: A Case Report and Review of the LiteratureSalih Samo0Muhammed Sherid1Husein Husein2Samian Sulaiman3Margaret Yungbluth4John A. Vainder5Department of Internal Medicine, Division of Gastroenterology, Saint Francis Hospital Evanston Program, University of Illinois at Chicago, 355 Ridge Avenue, Evanston, IL 60202, USADepartment of Internal Medicine, Division of Gastroenterology, CGH Medical Center, 100 East LeFevre Road, Sterling, IL 61081, USADepartment of Internal Medicine, Division of Gastroenterology, University of Tishreen, Aleppo Street, P.O. Box 2230, Latakia, SyriaDepartment of Internal Medicine, Division of Gastroenterology, Saint Francis Hospital Evanston Program, University of Illinois at Chicago, 355 Ridge Avenue, Evanston, IL 60202, USADepartment of Pathology, Saint Francis Hospital Evanston Program, University of Illinois at Chicago, 355 Ridge Avenue, Evanston, IL 60202, USADepartment of Internal Medicine, Division of Gastroenterology, Saint Francis Hospital Evanston Program, University of Illinois at Chicago, 355 Ridge Avenue, Evanston, IL 60202, USAKlippel-Trenaunay syndrome (KTS) is a rare congenital syndrome of vascular malformations and soft tissue and bone hypertrophy. Vascular malformations can affect multiple organ systems. Involvement of the gastrointestinal (GI) tract is uncommon in KTS, but it can be a source of life-threatening bleeding. We report a case of a 32-year-old male with a known diagnosis of KTS who presented with a life-threatening rectal bleeding and was treated with proctosigmoidectomy and massive blood products transfusion. He expired after a long hospitalization. We then review the literature on KTS and management of some of its complications.http://dx.doi.org/10.1155/2013/813653 |
| spellingShingle | Salih Samo Muhammed Sherid Husein Husein Samian Sulaiman Margaret Yungbluth John A. Vainder Klippel-Trenaunay Syndrome Causing Life-Threatening GI Bleeding: A Case Report and Review of the Literature Case Reports in Gastrointestinal Medicine |
| title | Klippel-Trenaunay Syndrome Causing Life-Threatening GI Bleeding: A Case Report and Review of the Literature |
| title_full | Klippel-Trenaunay Syndrome Causing Life-Threatening GI Bleeding: A Case Report and Review of the Literature |
| title_fullStr | Klippel-Trenaunay Syndrome Causing Life-Threatening GI Bleeding: A Case Report and Review of the Literature |
| title_full_unstemmed | Klippel-Trenaunay Syndrome Causing Life-Threatening GI Bleeding: A Case Report and Review of the Literature |
| title_short | Klippel-Trenaunay Syndrome Causing Life-Threatening GI Bleeding: A Case Report and Review of the Literature |
| title_sort | klippel trenaunay syndrome causing life threatening gi bleeding a case report and review of the literature |
| url | http://dx.doi.org/10.1155/2013/813653 |
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