Diencephalic Syndrome: A Rare Entity with Its Anaesthetic Management and Post-operative Complications of Diabetes Insipidus and Thrombocytopenia
Russell first described the diencephalic syndrome in 1951. It is a rare syndrome and usually presents in children as a cause of failure to thrive despite normal, or even increased appetite, with preservation of linear growth. The treatment options vary from endoscopic biopsy followed by chemotherap...
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European Medical Journal
2022-08-01
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| Series: | European Medical Journal |
| Online Access: | https://emj.emg-health.com/flagship-journal/article/diencephalic-syndrome-a-rare-entity-with-its-anaesthetic-management-and-post-operative-complications-of-diabetes-insipidus-and-thrombocytopenia/ |
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| author | Sakshi Kadian Sarin John Siddharth Chakraborty Sanjay Agrawal |
| author_facet | Sakshi Kadian Sarin John Siddharth Chakraborty Sanjay Agrawal |
| author_sort | Sakshi Kadian |
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| description |
Russell first described the diencephalic syndrome in 1951. It is a rare syndrome and usually presents in children as a cause of failure to thrive despite normal, or even increased appetite, with preservation of linear growth. The treatment options vary from endoscopic biopsy followed by chemotherapy to definitive surgical resection of the tumour. The authors here describe a case of an 8-year-old 10 kg emaciated child who presented with headache, vomiting, rage attacks, decreased weight, and diminution in vision. The child had bilateral optic atrophy; however, hormonal profiles were within normal limits. MRI of the brain gave an impression of craniopharyngioma. |
| format | Article |
| id | doaj-art-cb61eb03a8714fbea7d4e21fbc00f35b |
| institution | Kabale University |
| issn | 2397-6764 |
| language | English |
| publishDate | 2022-08-01 |
| publisher | European Medical Journal |
| record_format | Article |
| series | European Medical Journal |
| spelling | doaj-art-cb61eb03a8714fbea7d4e21fbc00f35b2025-01-20T16:09:05ZengEuropean Medical JournalEuropean Medical Journal2397-67642022-08-0110.33590/emj/22-00037Diencephalic Syndrome: A Rare Entity with Its Anaesthetic Management and Post-operative Complications of Diabetes Insipidus and ThrombocytopeniaSakshi Kadian0Sarin John1Siddharth Chakraborty2Sanjay Agrawal3Department of Anesthesiology and Critical Care, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, IndiaDepartment of Anesthesiology and Critical Care, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, IndiaDepartment of Anesthesiology and Critical Care, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, IndiaDepartment of Anesthesiology and Critical Care, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India Russell first described the diencephalic syndrome in 1951. It is a rare syndrome and usually presents in children as a cause of failure to thrive despite normal, or even increased appetite, with preservation of linear growth. The treatment options vary from endoscopic biopsy followed by chemotherapy to definitive surgical resection of the tumour. The authors here describe a case of an 8-year-old 10 kg emaciated child who presented with headache, vomiting, rage attacks, decreased weight, and diminution in vision. The child had bilateral optic atrophy; however, hormonal profiles were within normal limits. MRI of the brain gave an impression of craniopharyngioma.https://emj.emg-health.com/flagship-journal/article/diencephalic-syndrome-a-rare-entity-with-its-anaesthetic-management-and-post-operative-complications-of-diabetes-insipidus-and-thrombocytopenia/ |
| spellingShingle | Sakshi Kadian Sarin John Siddharth Chakraborty Sanjay Agrawal Diencephalic Syndrome: A Rare Entity with Its Anaesthetic Management and Post-operative Complications of Diabetes Insipidus and Thrombocytopenia European Medical Journal |
| title | Diencephalic Syndrome: A Rare Entity with Its Anaesthetic Management and Post-operative Complications of Diabetes Insipidus and Thrombocytopenia |
| title_full | Diencephalic Syndrome: A Rare Entity with Its Anaesthetic Management and Post-operative Complications of Diabetes Insipidus and Thrombocytopenia |
| title_fullStr | Diencephalic Syndrome: A Rare Entity with Its Anaesthetic Management and Post-operative Complications of Diabetes Insipidus and Thrombocytopenia |
| title_full_unstemmed | Diencephalic Syndrome: A Rare Entity with Its Anaesthetic Management and Post-operative Complications of Diabetes Insipidus and Thrombocytopenia |
| title_short | Diencephalic Syndrome: A Rare Entity with Its Anaesthetic Management and Post-operative Complications of Diabetes Insipidus and Thrombocytopenia |
| title_sort | diencephalic syndrome a rare entity with its anaesthetic management and post operative complications of diabetes insipidus and thrombocytopenia |
| url | https://emj.emg-health.com/flagship-journal/article/diencephalic-syndrome-a-rare-entity-with-its-anaesthetic-management-and-post-operative-complications-of-diabetes-insipidus-and-thrombocytopenia/ |
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