Rosai-Dorfman Disease Involving Multiple Organs: An Unusual Case with Poor Prognosis

Rosai-Dorfman disease is a rare, benign histiocytic proliferative disorder that usually affects the lymph nodes. Although extranodal involvement has been reported in diverse sites, manifestation in the cardiovascular system is extremely rare. Specifically, cardiac involvement in Rosai-Dorfman diseas...

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Main Authors: Fandresena Arilala Sendrasoa, Irina Mamisoa Ranaivo, Onivola Raharolahy, Malalaniaina Andrianarison, Naina Harinjara Razanakoto, Lala Soavina Ramarozatovo, Fahafahantsoa Rapelanoro Rabenja
Format: Article
Language:English
Published: Wiley 2016-01-01
Series:Case Reports in Medicine
Online Access:http://dx.doi.org/10.1155/2016/3920516
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author Fandresena Arilala Sendrasoa
Irina Mamisoa Ranaivo
Onivola Raharolahy
Malalaniaina Andrianarison
Naina Harinjara Razanakoto
Lala Soavina Ramarozatovo
Fahafahantsoa Rapelanoro Rabenja
author_facet Fandresena Arilala Sendrasoa
Irina Mamisoa Ranaivo
Onivola Raharolahy
Malalaniaina Andrianarison
Naina Harinjara Razanakoto
Lala Soavina Ramarozatovo
Fahafahantsoa Rapelanoro Rabenja
author_sort Fandresena Arilala Sendrasoa
collection DOAJ
description Rosai-Dorfman disease is a rare, benign histiocytic proliferative disorder that usually affects the lymph nodes. Although extranodal involvement has been reported in diverse sites, manifestation in the cardiovascular system is extremely rare. Specifically, cardiac involvement in Rosai-Dorfman disease is an extraordinarily infrequent event. We describe a case of a 36-year-old female who presented Rosai-Dorfman disease of multiple organs including the heart, with poor prognosis.
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institution Kabale University
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publishDate 2016-01-01
publisher Wiley
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series Case Reports in Medicine
spelling doaj-art-9c26cd1bacd24bbbac688530e8f0800a2025-02-03T06:13:21ZengWileyCase Reports in Medicine1687-96271687-96352016-01-01201610.1155/2016/39205163920516Rosai-Dorfman Disease Involving Multiple Organs: An Unusual Case with Poor PrognosisFandresena Arilala Sendrasoa0Irina Mamisoa Ranaivo1Onivola Raharolahy2Malalaniaina Andrianarison3Naina Harinjara Razanakoto4Lala Soavina Ramarozatovo5Fahafahantsoa Rapelanoro Rabenja6Department of Dermatology, Joseph Raseta Befelatanana Hospital, 101 Antananarivo, MadagascarDepartment of Dermatology, Joseph Raseta Befelatanana Hospital, 101 Antananarivo, MadagascarDepartment of Dermatology, Joseph Raseta Befelatanana Hospital, 101 Antananarivo, MadagascarDepartment of Dermatology, Joseph Raseta Befelatanana Hospital, 101 Antananarivo, MadagascarDepartment of Dermatology, Joseph Raseta Befelatanana Hospital, 101 Antananarivo, MadagascarDepartment of Dermatology, Joseph Raseta Befelatanana Hospital, 101 Antananarivo, MadagascarDepartment of Dermatology, Joseph Raseta Befelatanana Hospital, 101 Antananarivo, MadagascarRosai-Dorfman disease is a rare, benign histiocytic proliferative disorder that usually affects the lymph nodes. Although extranodal involvement has been reported in diverse sites, manifestation in the cardiovascular system is extremely rare. Specifically, cardiac involvement in Rosai-Dorfman disease is an extraordinarily infrequent event. We describe a case of a 36-year-old female who presented Rosai-Dorfman disease of multiple organs including the heart, with poor prognosis.http://dx.doi.org/10.1155/2016/3920516
spellingShingle Fandresena Arilala Sendrasoa
Irina Mamisoa Ranaivo
Onivola Raharolahy
Malalaniaina Andrianarison
Naina Harinjara Razanakoto
Lala Soavina Ramarozatovo
Fahafahantsoa Rapelanoro Rabenja
Rosai-Dorfman Disease Involving Multiple Organs: An Unusual Case with Poor Prognosis
Case Reports in Medicine
title Rosai-Dorfman Disease Involving Multiple Organs: An Unusual Case with Poor Prognosis
title_full Rosai-Dorfman Disease Involving Multiple Organs: An Unusual Case with Poor Prognosis
title_fullStr Rosai-Dorfman Disease Involving Multiple Organs: An Unusual Case with Poor Prognosis
title_full_unstemmed Rosai-Dorfman Disease Involving Multiple Organs: An Unusual Case with Poor Prognosis
title_short Rosai-Dorfman Disease Involving Multiple Organs: An Unusual Case with Poor Prognosis
title_sort rosai dorfman disease involving multiple organs an unusual case with poor prognosis
url http://dx.doi.org/10.1155/2016/3920516
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