Rosai-Dorfman Disease Involving Multiple Organs: An Unusual Case with Poor Prognosis
Rosai-Dorfman disease is a rare, benign histiocytic proliferative disorder that usually affects the lymph nodes. Although extranodal involvement has been reported in diverse sites, manifestation in the cardiovascular system is extremely rare. Specifically, cardiac involvement in Rosai-Dorfman diseas...
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Format: | Article |
Language: | English |
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Wiley
2016-01-01
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Series: | Case Reports in Medicine |
Online Access: | http://dx.doi.org/10.1155/2016/3920516 |
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author | Fandresena Arilala Sendrasoa Irina Mamisoa Ranaivo Onivola Raharolahy Malalaniaina Andrianarison Naina Harinjara Razanakoto Lala Soavina Ramarozatovo Fahafahantsoa Rapelanoro Rabenja |
author_facet | Fandresena Arilala Sendrasoa Irina Mamisoa Ranaivo Onivola Raharolahy Malalaniaina Andrianarison Naina Harinjara Razanakoto Lala Soavina Ramarozatovo Fahafahantsoa Rapelanoro Rabenja |
author_sort | Fandresena Arilala Sendrasoa |
collection | DOAJ |
description | Rosai-Dorfman disease is a rare, benign histiocytic proliferative disorder that usually affects the lymph nodes. Although extranodal involvement has been reported in diverse sites, manifestation in the cardiovascular system is extremely rare. Specifically, cardiac involvement in Rosai-Dorfman disease is an extraordinarily infrequent event. We describe a case of a 36-year-old female who presented Rosai-Dorfman disease of multiple organs including the heart, with poor prognosis. |
format | Article |
id | doaj-art-9c26cd1bacd24bbbac688530e8f0800a |
institution | Kabale University |
issn | 1687-9627 1687-9635 |
language | English |
publishDate | 2016-01-01 |
publisher | Wiley |
record_format | Article |
series | Case Reports in Medicine |
spelling | doaj-art-9c26cd1bacd24bbbac688530e8f0800a2025-02-03T06:13:21ZengWileyCase Reports in Medicine1687-96271687-96352016-01-01201610.1155/2016/39205163920516Rosai-Dorfman Disease Involving Multiple Organs: An Unusual Case with Poor PrognosisFandresena Arilala Sendrasoa0Irina Mamisoa Ranaivo1Onivola Raharolahy2Malalaniaina Andrianarison3Naina Harinjara Razanakoto4Lala Soavina Ramarozatovo5Fahafahantsoa Rapelanoro Rabenja6Department of Dermatology, Joseph Raseta Befelatanana Hospital, 101 Antananarivo, MadagascarDepartment of Dermatology, Joseph Raseta Befelatanana Hospital, 101 Antananarivo, MadagascarDepartment of Dermatology, Joseph Raseta Befelatanana Hospital, 101 Antananarivo, MadagascarDepartment of Dermatology, Joseph Raseta Befelatanana Hospital, 101 Antananarivo, MadagascarDepartment of Dermatology, Joseph Raseta Befelatanana Hospital, 101 Antananarivo, MadagascarDepartment of Dermatology, Joseph Raseta Befelatanana Hospital, 101 Antananarivo, MadagascarDepartment of Dermatology, Joseph Raseta Befelatanana Hospital, 101 Antananarivo, MadagascarRosai-Dorfman disease is a rare, benign histiocytic proliferative disorder that usually affects the lymph nodes. Although extranodal involvement has been reported in diverse sites, manifestation in the cardiovascular system is extremely rare. Specifically, cardiac involvement in Rosai-Dorfman disease is an extraordinarily infrequent event. We describe a case of a 36-year-old female who presented Rosai-Dorfman disease of multiple organs including the heart, with poor prognosis.http://dx.doi.org/10.1155/2016/3920516 |
spellingShingle | Fandresena Arilala Sendrasoa Irina Mamisoa Ranaivo Onivola Raharolahy Malalaniaina Andrianarison Naina Harinjara Razanakoto Lala Soavina Ramarozatovo Fahafahantsoa Rapelanoro Rabenja Rosai-Dorfman Disease Involving Multiple Organs: An Unusual Case with Poor Prognosis Case Reports in Medicine |
title | Rosai-Dorfman Disease Involving Multiple Organs: An Unusual Case with Poor Prognosis |
title_full | Rosai-Dorfman Disease Involving Multiple Organs: An Unusual Case with Poor Prognosis |
title_fullStr | Rosai-Dorfman Disease Involving Multiple Organs: An Unusual Case with Poor Prognosis |
title_full_unstemmed | Rosai-Dorfman Disease Involving Multiple Organs: An Unusual Case with Poor Prognosis |
title_short | Rosai-Dorfman Disease Involving Multiple Organs: An Unusual Case with Poor Prognosis |
title_sort | rosai dorfman disease involving multiple organs an unusual case with poor prognosis |
url | http://dx.doi.org/10.1155/2016/3920516 |
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