Tracheomalacia Treatment Using a Large-Diameter, Custom-Made Airway Stent in a Case with Mounier-Kuhn Syndrome
Mounier-Kuhn Syndrome (MKS) is a rare congenital disease that presents with abnormal enlargement in the central airways. In MKS, tracheomegaly is accompanied by difficulty in expelling recurrent lung infections and bronchiectasia. We presented a patient with MKS where commercially made stents were i...
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| Format: | Article |
| Language: | English |
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Wiley
2014-01-01
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| Series: | Case Reports in Pulmonology |
| Online Access: | http://dx.doi.org/10.1155/2014/910135 |
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| author | Cengiz Özdemir Sinem Nedime Sökücü Levent Karasulu Sedat Altın Levent Dalar |
| author_facet | Cengiz Özdemir Sinem Nedime Sökücü Levent Karasulu Sedat Altın Levent Dalar |
| author_sort | Cengiz Özdemir |
| collection | DOAJ |
| description | Mounier-Kuhn Syndrome (MKS) is a rare congenital disease that presents with abnormal enlargement in the central airways. In MKS, tracheomegaly is accompanied by difficulty in expelling recurrent lung infections and bronchiectasia. We presented a patient with MKS where commercially made stents were inadequate for stabilization and a custom-made, self-expandable metallic stent with a diameter of 28 mm and length of 100 mm was used. Chest pain that was thought to develop due to the stent and that disappeared after stent removal may be considered the main complication leading to stent removal. Continuous positive airway pressure therapy (CPAP) therapy was planned for the control of symptoms, which re-emerged after stent removal. This case is presented as an example that complications developing due to the stent as well as patient noncompliance may lead to stent removal, even when useful results are obtained from treatment of MKS. |
| format | Article |
| id | doaj-art-7270196dca8a4a3b981fd4c3e3dc3460 |
| institution | Kabale University |
| issn | 2090-6846 2090-6854 |
| language | English |
| publishDate | 2014-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Pulmonology |
| spelling | doaj-art-7270196dca8a4a3b981fd4c3e3dc34602025-02-03T06:06:02ZengWileyCase Reports in Pulmonology2090-68462090-68542014-01-01201410.1155/2014/910135910135Tracheomalacia Treatment Using a Large-Diameter, Custom-Made Airway Stent in a Case with Mounier-Kuhn SyndromeCengiz Özdemir0Sinem Nedime Sökücü1Levent Karasulu2Sedat Altın3Levent Dalar4Yedikule Chest Disease and Thoracic Surgery Research and Training Hospital, 34760 Istanbul, TurkeyYedikule Chest Disease and Thoracic Surgery Research and Training Hospital, 34760 Istanbul, TurkeyYedikule Chest Disease and Thoracic Surgery Research and Training Hospital, 34760 Istanbul, TurkeyYedikule Chest Disease and Thoracic Surgery Research and Training Hospital, 34760 Istanbul, TurkeyDepartment of Pulmonary Medicine, School of Medicine, Istanbul Bilim University, 34394 Istanbul, TurkeyMounier-Kuhn Syndrome (MKS) is a rare congenital disease that presents with abnormal enlargement in the central airways. In MKS, tracheomegaly is accompanied by difficulty in expelling recurrent lung infections and bronchiectasia. We presented a patient with MKS where commercially made stents were inadequate for stabilization and a custom-made, self-expandable metallic stent with a diameter of 28 mm and length of 100 mm was used. Chest pain that was thought to develop due to the stent and that disappeared after stent removal may be considered the main complication leading to stent removal. Continuous positive airway pressure therapy (CPAP) therapy was planned for the control of symptoms, which re-emerged after stent removal. This case is presented as an example that complications developing due to the stent as well as patient noncompliance may lead to stent removal, even when useful results are obtained from treatment of MKS.http://dx.doi.org/10.1155/2014/910135 |
| spellingShingle | Cengiz Özdemir Sinem Nedime Sökücü Levent Karasulu Sedat Altın Levent Dalar Tracheomalacia Treatment Using a Large-Diameter, Custom-Made Airway Stent in a Case with Mounier-Kuhn Syndrome Case Reports in Pulmonology |
| title | Tracheomalacia Treatment Using a Large-Diameter, Custom-Made Airway Stent in a Case with Mounier-Kuhn Syndrome |
| title_full | Tracheomalacia Treatment Using a Large-Diameter, Custom-Made Airway Stent in a Case with Mounier-Kuhn Syndrome |
| title_fullStr | Tracheomalacia Treatment Using a Large-Diameter, Custom-Made Airway Stent in a Case with Mounier-Kuhn Syndrome |
| title_full_unstemmed | Tracheomalacia Treatment Using a Large-Diameter, Custom-Made Airway Stent in a Case with Mounier-Kuhn Syndrome |
| title_short | Tracheomalacia Treatment Using a Large-Diameter, Custom-Made Airway Stent in a Case with Mounier-Kuhn Syndrome |
| title_sort | tracheomalacia treatment using a large diameter custom made airway stent in a case with mounier kuhn syndrome |
| url | http://dx.doi.org/10.1155/2014/910135 |
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