Clinical outcomes of surgical management for rare types of progressive familial intrahepatic cholestasis: a case series

Clinical outcomes of surgical management for rare types of progressive familial intrahepatic cholestasis: a case series

Abstract Background Progressive familial intrahepatic cholestasis (PFIC) is a heterogeneous group of genetic autosomal recessive diseases that cause severe cholestasis, which progresses to cirrhosis and liver failure, in infancy or early childhood. We herein report the clinical outcomes of surgical...

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Bibliographic Details
Main Authors: Kazunori Masahata, Takehisa Ueno, Kazuhiko Bessho, Tasuku Kodama, Ryo Tsukada, Ryuta Saka, Yuko Tazuke, Shuji Miyagawa, Hiroomi Okuyama
Format: Article
Language:English
Published: Japan Surgical Society 2022-01-01
Series:Surgical Case Reports
Subjects:
Progressive familial intrahepatic cholestasis
Liver transplantation
Cholestasis
Pediatrics
Online Access:https://doi.org/10.1186/s40792-022-01365-1
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https://doi.org/10.1186/s40792-022-01365-1

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