Safe Skin Management during Open Hepatectomy in a Patient with Recessive Dystrophic Congenital Epidermolysis Bullosa
Congenital epidermolysis bullosa is a rare, genetic condition in which even slight stimulation can cause blistering of the skin or mucosa. While previous reports of treatments requiring general anesthesia in these patients were focused on anesthesia-related procedures, such as endotracheal intubatio...
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| Main Authors: | , , , , , , , , , |
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| Format: | Article |
| Language: | English |
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Wiley
2018-01-01
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| Series: | Case Reports in Surgery |
| Online Access: | http://dx.doi.org/10.1155/2018/1786786 |
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| author | Ikuo Watanobe Hiroko Kida Yuuki Sekine Masaya Kawai Shozo Miyano Michio Machida Toshiaki Kitabatake Hiroyuki Sugo Yoshifumi Lee Kuniaki Kojima |
| author_facet | Ikuo Watanobe Hiroko Kida Yuuki Sekine Masaya Kawai Shozo Miyano Michio Machida Toshiaki Kitabatake Hiroyuki Sugo Yoshifumi Lee Kuniaki Kojima |
| author_sort | Ikuo Watanobe |
| collection | DOAJ |
| description | Congenital epidermolysis bullosa is a rare, genetic condition in which even slight stimulation can cause blistering of the skin or mucosa. While previous reports of treatments requiring general anesthesia in these patients were focused on anesthesia-related procedures, such as endotracheal intubation, no report has described specific management required for these patients during surgery, such as preparation of the surgical site, fixation of infusion lines and other tubes, and adjustment of the operation table. This is probably the first report to address these issues. This report presents a case of recessive dystrophic congenital epidermolysis bullosa in which open hepatectomy was safely performed. |
| format | Article |
| id | doaj-art-51c00703b06e487ea28cae6ad37f3ff5 |
| institution | Kabale University |
| issn | 2090-6900 2090-6919 |
| language | English |
| publishDate | 2018-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Surgery |
| spelling | doaj-art-51c00703b06e487ea28cae6ad37f3ff52025-02-03T06:01:02ZengWileyCase Reports in Surgery2090-69002090-69192018-01-01201810.1155/2018/17867861786786Safe Skin Management during Open Hepatectomy in a Patient with Recessive Dystrophic Congenital Epidermolysis BullosaIkuo Watanobe0Hiroko Kida1Yuuki Sekine2Masaya Kawai3Shozo Miyano4Michio Machida5Toshiaki Kitabatake6Hiroyuki Sugo7Yoshifumi Lee8Kuniaki Kojima9Department of General Surgery, Juntendo University Nerima Hospital, 3-1-10 Takanodai, Nerima-ku, Tokyo 177-8521, JapanDepartment of Nursing, Juntendo University Nerima Hospital, 3-1-10 Takanodai, Nerima-ku, Tokyo 177-8521, JapanDepartment of General Surgery, Juntendo University Nerima Hospital, 3-1-10 Takanodai, Nerima-ku, Tokyo 177-8521, JapanDepartment of General Surgery, Juntendo University Nerima Hospital, 3-1-10 Takanodai, Nerima-ku, Tokyo 177-8521, JapanDepartment of General Surgery, Juntendo University Nerima Hospital, 3-1-10 Takanodai, Nerima-ku, Tokyo 177-8521, JapanDepartment of General Surgery, Juntendo University Nerima Hospital, 3-1-10 Takanodai, Nerima-ku, Tokyo 177-8521, JapanDepartment of General Surgery, Juntendo University Nerima Hospital, 3-1-10 Takanodai, Nerima-ku, Tokyo 177-8521, JapanDepartment of General Surgery, Juntendo University Nerima Hospital, 3-1-10 Takanodai, Nerima-ku, Tokyo 177-8521, JapanDepartment of General Surgery, Juntendo University Nerima Hospital, 3-1-10 Takanodai, Nerima-ku, Tokyo 177-8521, JapanDepartment of General Surgery, Juntendo University Nerima Hospital, 3-1-10 Takanodai, Nerima-ku, Tokyo 177-8521, JapanCongenital epidermolysis bullosa is a rare, genetic condition in which even slight stimulation can cause blistering of the skin or mucosa. While previous reports of treatments requiring general anesthesia in these patients were focused on anesthesia-related procedures, such as endotracheal intubation, no report has described specific management required for these patients during surgery, such as preparation of the surgical site, fixation of infusion lines and other tubes, and adjustment of the operation table. This is probably the first report to address these issues. This report presents a case of recessive dystrophic congenital epidermolysis bullosa in which open hepatectomy was safely performed.http://dx.doi.org/10.1155/2018/1786786 |
| spellingShingle | Ikuo Watanobe Hiroko Kida Yuuki Sekine Masaya Kawai Shozo Miyano Michio Machida Toshiaki Kitabatake Hiroyuki Sugo Yoshifumi Lee Kuniaki Kojima Safe Skin Management during Open Hepatectomy in a Patient with Recessive Dystrophic Congenital Epidermolysis Bullosa Case Reports in Surgery |
| title | Safe Skin Management during Open Hepatectomy in a Patient with Recessive Dystrophic Congenital Epidermolysis Bullosa |
| title_full | Safe Skin Management during Open Hepatectomy in a Patient with Recessive Dystrophic Congenital Epidermolysis Bullosa |
| title_fullStr | Safe Skin Management during Open Hepatectomy in a Patient with Recessive Dystrophic Congenital Epidermolysis Bullosa |
| title_full_unstemmed | Safe Skin Management during Open Hepatectomy in a Patient with Recessive Dystrophic Congenital Epidermolysis Bullosa |
| title_short | Safe Skin Management during Open Hepatectomy in a Patient with Recessive Dystrophic Congenital Epidermolysis Bullosa |
| title_sort | safe skin management during open hepatectomy in a patient with recessive dystrophic congenital epidermolysis bullosa |
| url | http://dx.doi.org/10.1155/2018/1786786 |
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