A New Presentation: Aphallia, Vesicoureteral Reflux, Rectovesical Fistula, and Adrenal Insufficiency
Aphallia or penile agenesis is a rare congenital malformation with an estimated incidence rate of 1 in 10 to 30 million births. More than half of aphallia cases have associated anomalies including caudal axis, cardiovascular, genitourinary, and gastrointestinal anomalies. The penile agenesis associa...
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Format: | Article |
Language: | English |
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Wiley
2020-01-01
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Series: | Case Reports in Pediatrics |
Online Access: | http://dx.doi.org/10.1155/2020/8826520 |
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author | R. El Qadiry A. Lalaoui H. Nassih A. Bourrahouat I. Ait Sab |
author_facet | R. El Qadiry A. Lalaoui H. Nassih A. Bourrahouat I. Ait Sab |
author_sort | R. El Qadiry |
collection | DOAJ |
description | Aphallia or penile agenesis is a rare congenital malformation with an estimated incidence rate of 1 in 10 to 30 million births. More than half of aphallia cases have associated anomalies including caudal axis, cardiovascular, genitourinary, and gastrointestinal anomalies. The penile agenesis associated with adrenal insufficiency has never been reported in an infant. We report a rare case of a newborn that was diagnosed as a case of aphallia with vesicorectal fistula and vesicoureteral reflux, complicated by adrenal insufficiency with salt-wasting crisis. |
format | Article |
id | doaj-art-4a16687c5ee14d07bc8af5004e1cd53e |
institution | Kabale University |
issn | 2090-6803 2090-6811 |
language | English |
publishDate | 2020-01-01 |
publisher | Wiley |
record_format | Article |
series | Case Reports in Pediatrics |
spelling | doaj-art-4a16687c5ee14d07bc8af5004e1cd53e2025-02-03T06:43:31ZengWileyCase Reports in Pediatrics2090-68032090-68112020-01-01202010.1155/2020/88265208826520A New Presentation: Aphallia, Vesicoureteral Reflux, Rectovesical Fistula, and Adrenal InsufficiencyR. El Qadiry0A. Lalaoui1H. Nassih2A. Bourrahouat3I. Ait Sab4Pediatric B Department–Mother-Child Pole, Mohammed VI University Hospital, Marrakesh, MoroccoPediatric B Department–Mother-Child Pole, Mohammed VI University Hospital, Marrakesh, MoroccoPediatric B Department–Mother-Child Pole, Mohammed VI University Hospital, Marrakesh, MoroccoPediatric B Department–Mother-Child Pole, Mohammed VI University Hospital, Marrakesh, MoroccoPediatric B Department–Mother-Child Pole, Mohammed VI University Hospital, Marrakesh, MoroccoAphallia or penile agenesis is a rare congenital malformation with an estimated incidence rate of 1 in 10 to 30 million births. More than half of aphallia cases have associated anomalies including caudal axis, cardiovascular, genitourinary, and gastrointestinal anomalies. The penile agenesis associated with adrenal insufficiency has never been reported in an infant. We report a rare case of a newborn that was diagnosed as a case of aphallia with vesicorectal fistula and vesicoureteral reflux, complicated by adrenal insufficiency with salt-wasting crisis.http://dx.doi.org/10.1155/2020/8826520 |
spellingShingle | R. El Qadiry A. Lalaoui H. Nassih A. Bourrahouat I. Ait Sab A New Presentation: Aphallia, Vesicoureteral Reflux, Rectovesical Fistula, and Adrenal Insufficiency Case Reports in Pediatrics |
title | A New Presentation: Aphallia, Vesicoureteral Reflux, Rectovesical Fistula, and Adrenal Insufficiency |
title_full | A New Presentation: Aphallia, Vesicoureteral Reflux, Rectovesical Fistula, and Adrenal Insufficiency |
title_fullStr | A New Presentation: Aphallia, Vesicoureteral Reflux, Rectovesical Fistula, and Adrenal Insufficiency |
title_full_unstemmed | A New Presentation: Aphallia, Vesicoureteral Reflux, Rectovesical Fistula, and Adrenal Insufficiency |
title_short | A New Presentation: Aphallia, Vesicoureteral Reflux, Rectovesical Fistula, and Adrenal Insufficiency |
title_sort | new presentation aphallia vesicoureteral reflux rectovesical fistula and adrenal insufficiency |
url | http://dx.doi.org/10.1155/2020/8826520 |
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