Unusual Course of Scimitar Syndrome Preceded by Lung Hypoplasia
In patients with Scimitar syndrome, right pulmonary artery hypoplasia is considered to lead to right lung hypoplasia because of decrease in blood flow. However, there are no reports wherein the change was actually detected. Thus, the exact developmental mechanism of right pulmonary artery hypoplasia...
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| Format: | Article |
| Language: | English |
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Wiley
2019-01-01
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| Series: | Case Reports in Pediatrics |
| Online Access: | http://dx.doi.org/10.1155/2019/8927243 |
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| _version_ | 1832567854476558336 |
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| author | Yusuke Hoshino Junichi Arai |
| author_facet | Yusuke Hoshino Junichi Arai |
| author_sort | Yusuke Hoshino |
| collection | DOAJ |
| description | In patients with Scimitar syndrome, right pulmonary artery hypoplasia is considered to lead to right lung hypoplasia because of decrease in blood flow. However, there are no reports wherein the change was actually detected. Thus, the exact developmental mechanism of right pulmonary artery hypoplasia and right lung hypoplasia in patients with Scimitar syndrome is unclear. We experienced a case of Scimitar syndrome preceding right lung hypoplasia, and right pulmonary artery hypoplasia gradually revealed with time. We hypothesized that, in our patient, the lung hypoplasia led to pulmonary artery hypoplasia due to decrease in blood flow. If there are no differences in the diameter of the left and right pulmonary artery in patients with Scimitar syndrome at birth, we propose the necessity of careful observation due to the possibility that pulmonary artery hypoplasia may develop in the future. |
| format | Article |
| id | doaj-art-3534f68d043e4af8a739f8e562d9b1d5 |
| institution | Kabale University |
| issn | 2090-6803 2090-6811 |
| language | English |
| publishDate | 2019-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Pediatrics |
| spelling | doaj-art-3534f68d043e4af8a739f8e562d9b1d52025-02-03T01:00:22ZengWileyCase Reports in Pediatrics2090-68032090-68112019-01-01201910.1155/2019/89272438927243Unusual Course of Scimitar Syndrome Preceded by Lung HypoplasiaYusuke Hoshino0Junichi Arai1Department of Neonatology, Ibaraki Children’s Hospital, 3-3-1 Futabadai, Mito-city, Ibaraki 311-4145, JapanDepartment of Neonatology, Ibaraki Children’s Hospital, 3-3-1 Futabadai, Mito-city, Ibaraki 311-4145, JapanIn patients with Scimitar syndrome, right pulmonary artery hypoplasia is considered to lead to right lung hypoplasia because of decrease in blood flow. However, there are no reports wherein the change was actually detected. Thus, the exact developmental mechanism of right pulmonary artery hypoplasia and right lung hypoplasia in patients with Scimitar syndrome is unclear. We experienced a case of Scimitar syndrome preceding right lung hypoplasia, and right pulmonary artery hypoplasia gradually revealed with time. We hypothesized that, in our patient, the lung hypoplasia led to pulmonary artery hypoplasia due to decrease in blood flow. If there are no differences in the diameter of the left and right pulmonary artery in patients with Scimitar syndrome at birth, we propose the necessity of careful observation due to the possibility that pulmonary artery hypoplasia may develop in the future.http://dx.doi.org/10.1155/2019/8927243 |
| spellingShingle | Yusuke Hoshino Junichi Arai Unusual Course of Scimitar Syndrome Preceded by Lung Hypoplasia Case Reports in Pediatrics |
| title | Unusual Course of Scimitar Syndrome Preceded by Lung Hypoplasia |
| title_full | Unusual Course of Scimitar Syndrome Preceded by Lung Hypoplasia |
| title_fullStr | Unusual Course of Scimitar Syndrome Preceded by Lung Hypoplasia |
| title_full_unstemmed | Unusual Course of Scimitar Syndrome Preceded by Lung Hypoplasia |
| title_short | Unusual Course of Scimitar Syndrome Preceded by Lung Hypoplasia |
| title_sort | unusual course of scimitar syndrome preceded by lung hypoplasia |
| url | http://dx.doi.org/10.1155/2019/8927243 |
| work_keys_str_mv | AT yusukehoshino unusualcourseofscimitarsyndromeprecededbylunghypoplasia AT junichiarai unusualcourseofscimitarsyndromeprecededbylunghypoplasia |