From Recurrent Syncope to Sudden Cardiac Death: Clinical Characteristics in a Chinese Patient Carrying a Plakophilin-2 Gene Mutation

We report a case of Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC) which illustrates the natural progression of disease in the absence of availability of an implanted cardiac defibrillator (ICD). Electrocardiograms and cardiac imaging show the progress of ARVC and these clinical milestones o...

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Main Authors: Wenling Liu, Xiaoliang Qiu, Wen Liu, Dayi Hu, Tiangang Zhu, Chunling Wang, Dominik Beer, Li Zhang
Format: Article
Language:English
Published: Wiley 2013-01-01
Series:Case Reports in Cardiology
Online Access:http://dx.doi.org/10.1155/2013/246891
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author Wenling Liu
Xiaoliang Qiu
Wen Liu
Dayi Hu
Tiangang Zhu
Chunling Wang
Dominik Beer
Li Zhang
author_facet Wenling Liu
Xiaoliang Qiu
Wen Liu
Dayi Hu
Tiangang Zhu
Chunling Wang
Dominik Beer
Li Zhang
author_sort Wenling Liu
collection DOAJ
description We report a case of Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC) which illustrates the natural progression of disease in the absence of availability of an implanted cardiac defibrillator (ICD). Electrocardiograms and cardiac imaging show the progress of ARVC and these clinical milestones of disease are presented herein.
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institution Kabale University
issn 2090-6404
2090-6412
language English
publishDate 2013-01-01
publisher Wiley
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series Case Reports in Cardiology
spelling doaj-art-219ec51549e946ae9ea62e9625cabb622025-02-03T01:10:05ZengWileyCase Reports in Cardiology2090-64042090-64122013-01-01201310.1155/2013/246891246891From Recurrent Syncope to Sudden Cardiac Death: Clinical Characteristics in a Chinese Patient Carrying a Plakophilin-2 Gene MutationWenling Liu0Xiaoliang Qiu1Wen Liu2Dayi Hu3Tiangang Zhu4Chunling Wang5Dominik Beer6Li Zhang7Peking University People’s Hospital, Beijing 100044, ChinaPeking University People’s Hospital, Beijing 100044, ChinaPeking University People’s Hospital, Beijing 100044, ChinaPeking University People’s Hospital, Beijing 100044, ChinaPeking University People’s Hospital, Beijing 100044, ChinaChina Meitan General Hospital, Beijing, ChinaLankenau Medical Center, Lankenau Institute for Medical Research, Wynnewood, PA, USALankenau Medical Center, Lankenau Institute for Medical Research, Wynnewood, PA, USAWe report a case of Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC) which illustrates the natural progression of disease in the absence of availability of an implanted cardiac defibrillator (ICD). Electrocardiograms and cardiac imaging show the progress of ARVC and these clinical milestones of disease are presented herein.http://dx.doi.org/10.1155/2013/246891
spellingShingle Wenling Liu
Xiaoliang Qiu
Wen Liu
Dayi Hu
Tiangang Zhu
Chunling Wang
Dominik Beer
Li Zhang
From Recurrent Syncope to Sudden Cardiac Death: Clinical Characteristics in a Chinese Patient Carrying a Plakophilin-2 Gene Mutation
Case Reports in Cardiology
title From Recurrent Syncope to Sudden Cardiac Death: Clinical Characteristics in a Chinese Patient Carrying a Plakophilin-2 Gene Mutation
title_full From Recurrent Syncope to Sudden Cardiac Death: Clinical Characteristics in a Chinese Patient Carrying a Plakophilin-2 Gene Mutation
title_fullStr From Recurrent Syncope to Sudden Cardiac Death: Clinical Characteristics in a Chinese Patient Carrying a Plakophilin-2 Gene Mutation
title_full_unstemmed From Recurrent Syncope to Sudden Cardiac Death: Clinical Characteristics in a Chinese Patient Carrying a Plakophilin-2 Gene Mutation
title_short From Recurrent Syncope to Sudden Cardiac Death: Clinical Characteristics in a Chinese Patient Carrying a Plakophilin-2 Gene Mutation
title_sort from recurrent syncope to sudden cardiac death clinical characteristics in a chinese patient carrying a plakophilin 2 gene mutation
url http://dx.doi.org/10.1155/2013/246891
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