From Recurrent Syncope to Sudden Cardiac Death: Clinical Characteristics in a Chinese Patient Carrying a Plakophilin-2 Gene Mutation
We report a case of Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC) which illustrates the natural progression of disease in the absence of availability of an implanted cardiac defibrillator (ICD). Electrocardiograms and cardiac imaging show the progress of ARVC and these clinical milestones o...
Saved in:
Main Authors: | , , , , , , , |
---|---|
Format: | Article |
Language: | English |
Published: |
Wiley
2013-01-01
|
Series: | Case Reports in Cardiology |
Online Access: | http://dx.doi.org/10.1155/2013/246891 |
Tags: |
Add Tag
No Tags, Be the first to tag this record!
|
_version_ | 1832564808748105728 |
---|---|
author | Wenling Liu Xiaoliang Qiu Wen Liu Dayi Hu Tiangang Zhu Chunling Wang Dominik Beer Li Zhang |
author_facet | Wenling Liu Xiaoliang Qiu Wen Liu Dayi Hu Tiangang Zhu Chunling Wang Dominik Beer Li Zhang |
author_sort | Wenling Liu |
collection | DOAJ |
description | We report a case of Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC) which illustrates the natural progression of disease in the absence of availability of an implanted cardiac defibrillator (ICD). Electrocardiograms and cardiac imaging show the progress of ARVC and these clinical milestones of disease are presented herein. |
format | Article |
id | doaj-art-219ec51549e946ae9ea62e9625cabb62 |
institution | Kabale University |
issn | 2090-6404 2090-6412 |
language | English |
publishDate | 2013-01-01 |
publisher | Wiley |
record_format | Article |
series | Case Reports in Cardiology |
spelling | doaj-art-219ec51549e946ae9ea62e9625cabb622025-02-03T01:10:05ZengWileyCase Reports in Cardiology2090-64042090-64122013-01-01201310.1155/2013/246891246891From Recurrent Syncope to Sudden Cardiac Death: Clinical Characteristics in a Chinese Patient Carrying a Plakophilin-2 Gene MutationWenling Liu0Xiaoliang Qiu1Wen Liu2Dayi Hu3Tiangang Zhu4Chunling Wang5Dominik Beer6Li Zhang7Peking University People’s Hospital, Beijing 100044, ChinaPeking University People’s Hospital, Beijing 100044, ChinaPeking University People’s Hospital, Beijing 100044, ChinaPeking University People’s Hospital, Beijing 100044, ChinaPeking University People’s Hospital, Beijing 100044, ChinaChina Meitan General Hospital, Beijing, ChinaLankenau Medical Center, Lankenau Institute for Medical Research, Wynnewood, PA, USALankenau Medical Center, Lankenau Institute for Medical Research, Wynnewood, PA, USAWe report a case of Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC) which illustrates the natural progression of disease in the absence of availability of an implanted cardiac defibrillator (ICD). Electrocardiograms and cardiac imaging show the progress of ARVC and these clinical milestones of disease are presented herein.http://dx.doi.org/10.1155/2013/246891 |
spellingShingle | Wenling Liu Xiaoliang Qiu Wen Liu Dayi Hu Tiangang Zhu Chunling Wang Dominik Beer Li Zhang From Recurrent Syncope to Sudden Cardiac Death: Clinical Characteristics in a Chinese Patient Carrying a Plakophilin-2 Gene Mutation Case Reports in Cardiology |
title | From Recurrent Syncope to Sudden Cardiac Death: Clinical Characteristics in a Chinese Patient Carrying a Plakophilin-2 Gene Mutation |
title_full | From Recurrent Syncope to Sudden Cardiac Death: Clinical Characteristics in a Chinese Patient Carrying a Plakophilin-2 Gene Mutation |
title_fullStr | From Recurrent Syncope to Sudden Cardiac Death: Clinical Characteristics in a Chinese Patient Carrying a Plakophilin-2 Gene Mutation |
title_full_unstemmed | From Recurrent Syncope to Sudden Cardiac Death: Clinical Characteristics in a Chinese Patient Carrying a Plakophilin-2 Gene Mutation |
title_short | From Recurrent Syncope to Sudden Cardiac Death: Clinical Characteristics in a Chinese Patient Carrying a Plakophilin-2 Gene Mutation |
title_sort | from recurrent syncope to sudden cardiac death clinical characteristics in a chinese patient carrying a plakophilin 2 gene mutation |
url | http://dx.doi.org/10.1155/2013/246891 |
work_keys_str_mv | AT wenlingliu fromrecurrentsyncopetosuddencardiacdeathclinicalcharacteristicsinachinesepatientcarryingaplakophilin2genemutation AT xiaoliangqiu fromrecurrentsyncopetosuddencardiacdeathclinicalcharacteristicsinachinesepatientcarryingaplakophilin2genemutation AT wenliu fromrecurrentsyncopetosuddencardiacdeathclinicalcharacteristicsinachinesepatientcarryingaplakophilin2genemutation AT dayihu fromrecurrentsyncopetosuddencardiacdeathclinicalcharacteristicsinachinesepatientcarryingaplakophilin2genemutation AT tiangangzhu fromrecurrentsyncopetosuddencardiacdeathclinicalcharacteristicsinachinesepatientcarryingaplakophilin2genemutation AT chunlingwang fromrecurrentsyncopetosuddencardiacdeathclinicalcharacteristicsinachinesepatientcarryingaplakophilin2genemutation AT dominikbeer fromrecurrentsyncopetosuddencardiacdeathclinicalcharacteristicsinachinesepatientcarryingaplakophilin2genemutation AT lizhang fromrecurrentsyncopetosuddencardiacdeathclinicalcharacteristicsinachinesepatientcarryingaplakophilin2genemutation |