Bimelic Hirayama Disease: Clinical Dilemma Solved by Imaging
Hirayama disease (juvenile muscular atrophy of distal upper extremity) is a cervical myelopathy predominantly affecting adolescent males. It is characterized by progressive muscular weakness and atrophy of unilateral or asymmetrically bilateral distal upper limbs. We report a case of an 18-year-male...
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| Format: | Article |
| Language: | English |
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Wiley
2013-01-01
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| Series: | Case Reports in Medicine |
| Online Access: | http://dx.doi.org/10.1155/2013/606894 |
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| author | Shalabh Jain Siddharth Yadav Swarna Gupta Ritu Gupta |
| author_facet | Shalabh Jain Siddharth Yadav Swarna Gupta Ritu Gupta |
| author_sort | Shalabh Jain |
| collection | DOAJ |
| description | Hirayama disease (juvenile muscular atrophy of distal upper extremity) is a cervical myelopathy predominantly affecting adolescent males. It is characterized by progressive muscular weakness and atrophy of unilateral or asymmetrically bilateral distal upper limbs. We report a case of an 18-year-male painter, who presented with gradually progressive, symmetrical bilateral weakness of hands and forearm for the last two years. On the basis of clinical examination, a provisional diagnosis of lower motor neuron type of symmetrical distal weakness due to heavy metal intoxication was kept. However, imaging studies helped in making a definitive diagnosis of Hirayama disease. The patient was advised cervical collar, and there was no progression in symptoms after six months of followup. Due to the rarity of bilateral symmetrical involvement in Hirayama disease, it remains obscured or unsuspected clinically, and MRI plays a pivotal role in diagnosis. |
| format | Article |
| id | doaj-art-11870e1434b746a6a91aef1724a96659 |
| institution | Kabale University |
| issn | 1687-9627 1687-9635 |
| language | English |
| publishDate | 2013-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Medicine |
| spelling | doaj-art-11870e1434b746a6a91aef1724a966592025-02-03T06:10:58ZengWileyCase Reports in Medicine1687-96271687-96352013-01-01201310.1155/2013/606894606894Bimelic Hirayama Disease: Clinical Dilemma Solved by ImagingShalabh Jain0Siddharth Yadav1Swarna Gupta2Ritu Gupta3Department of Radiodiagnosis, VMMC and Safdarjung Hospital, New Delhi 110029, IndiaDepartment of General Surgery, VMMC and Safdarjung Hospital, New Delhi 110029, IndiaDepartment of Radiodiagnosis, VMMC and Safdarjung Hospital, New Delhi 110029, IndiaDepartment of Otorhinolaryngology, VMMC and Safdarjung Hospital, New Delhi 110029, IndiaHirayama disease (juvenile muscular atrophy of distal upper extremity) is a cervical myelopathy predominantly affecting adolescent males. It is characterized by progressive muscular weakness and atrophy of unilateral or asymmetrically bilateral distal upper limbs. We report a case of an 18-year-male painter, who presented with gradually progressive, symmetrical bilateral weakness of hands and forearm for the last two years. On the basis of clinical examination, a provisional diagnosis of lower motor neuron type of symmetrical distal weakness due to heavy metal intoxication was kept. However, imaging studies helped in making a definitive diagnosis of Hirayama disease. The patient was advised cervical collar, and there was no progression in symptoms after six months of followup. Due to the rarity of bilateral symmetrical involvement in Hirayama disease, it remains obscured or unsuspected clinically, and MRI plays a pivotal role in diagnosis.http://dx.doi.org/10.1155/2013/606894 |
| spellingShingle | Shalabh Jain Siddharth Yadav Swarna Gupta Ritu Gupta Bimelic Hirayama Disease: Clinical Dilemma Solved by Imaging Case Reports in Medicine |
| title | Bimelic Hirayama Disease: Clinical Dilemma Solved by Imaging |
| title_full | Bimelic Hirayama Disease: Clinical Dilemma Solved by Imaging |
| title_fullStr | Bimelic Hirayama Disease: Clinical Dilemma Solved by Imaging |
| title_full_unstemmed | Bimelic Hirayama Disease: Clinical Dilemma Solved by Imaging |
| title_short | Bimelic Hirayama Disease: Clinical Dilemma Solved by Imaging |
| title_sort | bimelic hirayama disease clinical dilemma solved by imaging |
| url | http://dx.doi.org/10.1155/2013/606894 |
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