Diffuse Supravalvular Aortic Stenosis: Surgical Repair in Adulthood

We present the case of a 54-year-old woman in which a diffuse congenital supravalvular aortic stenosis (SVAS) was associated with a severe aortic valve incompetence and heavy calcification of the aortic annulus. Repair consisted in resection of the ascending aorta, patch augmentation of the hypoplas...

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Bibliographic Details
Main Authors: Giovanni Ferlan, Claudio De Pasquale, Concetta Losito, Annalisa Fiorella, Nicola Marraudino, Francesco Tunzi
Format: Article
Language:English
Published: Wiley 2009-01-01
Series:Cardiology Research and Practice
Online Access:http://dx.doi.org/10.4061/2009/976190
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Summary:We present the case of a 54-year-old woman in which a diffuse congenital supravalvular aortic stenosis (SVAS) was associated with a severe aortic valve incompetence and heavy calcification of the aortic annulus. Repair consisted in resection of the ascending aorta, patch augmentation of the hypoplastic aortic root and annulus, placement of a 20 mm Dacron tubular graft (Vascutek, Renfrewshire, UK) and aortic valve replacement with a mechanical prosthesis (Sorin, Turin, Italy). Follow-up echocardiography demonstrated normal prosthetic valve function and a postoperative three-dimensional computed tomographic scan showed a normal shape of the reconstructed ascending aorta.
ISSN:2090-0597