Diffuse Supravalvular Aortic Stenosis: Surgical Repair in Adulthood
We present the case of a 54-year-old woman in which a diffuse congenital supravalvular aortic stenosis (SVAS) was associated with a severe aortic valve incompetence and heavy calcification of the aortic annulus. Repair consisted in resection of the ascending aorta, patch augmentation of the hypoplas...
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Main Authors: | , , , , , |
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Format: | Article |
Language: | English |
Published: |
Wiley
2009-01-01
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Series: | Cardiology Research and Practice |
Online Access: | http://dx.doi.org/10.4061/2009/976190 |
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Summary: | We present the case of a 54-year-old woman in which a diffuse congenital supravalvular aortic stenosis (SVAS) was associated with a severe aortic valve incompetence and heavy calcification of the aortic annulus. Repair consisted in resection of the ascending aorta, patch augmentation of the hypoplastic aortic root and annulus, placement of a 20 mm Dacron tubular graft (Vascutek, Renfrewshire, UK) and aortic valve replacement with a mechanical prosthesis (Sorin, Turin, Italy). Follow-up echocardiography demonstrated normal prosthetic valve function and a postoperative three-dimensional computed tomographic scan showed a normal shape of the reconstructed ascending aorta. |
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ISSN: | 2090-0597 |