Cardiogenic Shock: An Unusual Initial Presentation of Churg-Strauss Syndrome
Churg-Strauss syndrome (CSS) is a rare autoimmune condition, characterized by necrotizing extravascular eosinophil rich granulomatous inflammation of the tissues and disseminated small-medium sized vessel vasculitis in a patient with bronchial asthma and tissue eosinophilia. Though pulmonary involve...
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| Format: | Article |
| Language: | English |
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Wiley
2018-01-01
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| Series: | Case Reports in Rheumatology |
| Online Access: | http://dx.doi.org/10.1155/2018/2076837 |
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| author | M. Apirami J. A. Pratheepan T. Kumanan M. Guruparan G. Selvaratnam |
| author_facet | M. Apirami J. A. Pratheepan T. Kumanan M. Guruparan G. Selvaratnam |
| author_sort | M. Apirami |
| collection | DOAJ |
| description | Churg-Strauss syndrome (CSS) is a rare autoimmune condition, characterized by necrotizing extravascular eosinophil rich granulomatous inflammation of the tissues and disseminated small-medium sized vessel vasculitis in a patient with bronchial asthma and tissue eosinophilia. Though pulmonary involvement is the predominant feature of CSS, extra pulmonary involvement, in particular, cardiac involvement, denotes an adverse outcome. Here we report a 50-year-old female who presented with cardiogenic shock due to an acute coronary event as the initial manifestation of CSS. A subsequent coronary angiogram revealed normal epicardial coronaries. She was a patient with bronchial asthma and developed vasculitic rash, bilateral sensory motor polyneuropathy, and migratory peripheral lung field shadows in the background of peripheral eosinophilia during the course of the illness. She was diagnosed as having CSS based on ACR criteria and aggressively treated with immunosuppressants according to her Five-Factor Score and has shown prompt response to therapy. This case report adds to the literature another rare initial presentation of CSS to the existing array of its clinical manifestations. |
| format | Article |
| id | doaj-art-0505715f1ca040f78f1b1e244c80df25 |
| institution | Kabale University |
| issn | 2090-6889 2090-6897 |
| language | English |
| publishDate | 2018-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Rheumatology |
| spelling | doaj-art-0505715f1ca040f78f1b1e244c80df252025-02-03T01:23:52ZengWileyCase Reports in Rheumatology2090-68892090-68972018-01-01201810.1155/2018/20768372076837Cardiogenic Shock: An Unusual Initial Presentation of Churg-Strauss SyndromeM. Apirami0J. A. Pratheepan1T. Kumanan2M. Guruparan3G. Selvaratnam4Teaching Hospital Jaffna, Jaffna, Sri LankaTeaching Hospital Jaffna, Faculty of Medicine, University of Jaffna, Jaffna, Sri LankaTeaching Hospital Jaffna, Faculty of Medicine, University of Jaffna, Jaffna, Sri LankaTeaching Hospital Jaffna, Jaffna, Sri LankaTeaching Hospital Jaffna, Faculty of Medicine, University of Jaffna, Jaffna, Sri LankaChurg-Strauss syndrome (CSS) is a rare autoimmune condition, characterized by necrotizing extravascular eosinophil rich granulomatous inflammation of the tissues and disseminated small-medium sized vessel vasculitis in a patient with bronchial asthma and tissue eosinophilia. Though pulmonary involvement is the predominant feature of CSS, extra pulmonary involvement, in particular, cardiac involvement, denotes an adverse outcome. Here we report a 50-year-old female who presented with cardiogenic shock due to an acute coronary event as the initial manifestation of CSS. A subsequent coronary angiogram revealed normal epicardial coronaries. She was a patient with bronchial asthma and developed vasculitic rash, bilateral sensory motor polyneuropathy, and migratory peripheral lung field shadows in the background of peripheral eosinophilia during the course of the illness. She was diagnosed as having CSS based on ACR criteria and aggressively treated with immunosuppressants according to her Five-Factor Score and has shown prompt response to therapy. This case report adds to the literature another rare initial presentation of CSS to the existing array of its clinical manifestations.http://dx.doi.org/10.1155/2018/2076837 |
| spellingShingle | M. Apirami J. A. Pratheepan T. Kumanan M. Guruparan G. Selvaratnam Cardiogenic Shock: An Unusual Initial Presentation of Churg-Strauss Syndrome Case Reports in Rheumatology |
| title | Cardiogenic Shock: An Unusual Initial Presentation of Churg-Strauss Syndrome |
| title_full | Cardiogenic Shock: An Unusual Initial Presentation of Churg-Strauss Syndrome |
| title_fullStr | Cardiogenic Shock: An Unusual Initial Presentation of Churg-Strauss Syndrome |
| title_full_unstemmed | Cardiogenic Shock: An Unusual Initial Presentation of Churg-Strauss Syndrome |
| title_short | Cardiogenic Shock: An Unusual Initial Presentation of Churg-Strauss Syndrome |
| title_sort | cardiogenic shock an unusual initial presentation of churg strauss syndrome |
| url | http://dx.doi.org/10.1155/2018/2076837 |
| work_keys_str_mv | AT mapirami cardiogenicshockanunusualinitialpresentationofchurgstrausssyndrome AT japratheepan cardiogenicshockanunusualinitialpresentationofchurgstrausssyndrome AT tkumanan cardiogenicshockanunusualinitialpresentationofchurgstrausssyndrome AT mguruparan cardiogenicshockanunusualinitialpresentationofchurgstrausssyndrome AT gselvaratnam cardiogenicshockanunusualinitialpresentationofchurgstrausssyndrome |