Giant Axonal Neuropathy in a Child with Stop-Gain Variant in GAN Gene by Varunvenkat M. Srinivasan, Rani Manisha, Mayank Nilay, Bhanu Kiran Bhakhri, Dharmendra Kumar Singh

“…On examination, he had kinky hair, nystagmus, with diffuse muscle atrophy, absent tendon reflexes, positive cerebellar signs as well as impairment of higher mental functions. Management and Outcome: Laboratory investigations were largely normal, with magnetic resonance imaging showing features of diffuse white matter abnormality with signal changes noted in the dentate nuclei. …”
Get full text

Methodological approaches to the institutional transformations for the formation and development of the scientific and industrial complex (on the example of the Republic of Belarus... by A. G. Shumilin, I. V. Ustinovich

“…One of the possible ways to solve this problem is scientific-industrial integration, the end result of which in the Republic of Belarus can be an effectively functioning scientific-industrial complex. The aim of the study is to identify and evaluate methodological approaches to the institutional transformations for the formation and development of scientific-industrial complex. …”
Get full text

Zespołowa organizacja pracy (teamwork) w niemieckich bibliotekach uniwersyteckich by Zdzisław Gębołyś

“…The starting point for the discussion is the description of the shortcomings of the ubiquitous functional organizational model used in academic libraries. …”
Get full text

Contributions to the Development of Tetrahedral Mobile Robots with Omnidirectional Locomotion Units by Anca-Corina Simerean, Mihai Olimpiu Tătar

“…The paper begins with a detailed description of the first tetrahedral robot prototype, highlighting its strengths as well as the limitations that led to the need for improvements. …”
Get full text

Economic Exchanges Management in the Exhibition Bilateral Market by K. V. Simonov

“…The combination of these theoretically and practically significant results develops the theory of two-sided exhibition markets, as well as provides scientific support in the format of recommendations and descriptions of tools that help exhibition business practitioners cope with the problem of managing economic exchanges.…”
Get full text

RelAp43, a member of the NF-κB family involved in innate immune response against Lyssavirus infection. by Sophie Luco, Olivier Delmas, Pierre-Olivier Vidalain, Frédéric Tangy, Robert Weil, Hervé Bourhy

“…Taken together, our data provide the description of a novel functional member of the NF-κB family, which plays a key role in the induction of anti-viral innate immune response.…”
Get full text

Implementation of Freedom To Learn in Higher Education: Perceptions of Students, Lecturers, and Administration Staff by Christine Dwi Karya Susilawati, Se Tin Se Tin, Bernard Rhenaldi Sutedja

“…Data was collected through a questionnaire via google link and analyzed descriptively. A total of 2,038 students, 257 lecturers and 190 administrative staff were sampled. …”
Get full text

Word Formation of Dialect Verb Derivatives Motivated by Nouns (on Material of Vocabulary of Amur Region Russian Dialects) by V. T. Sadchenko

“…They belong to the resettlement dialects of secondary formation and are characterized by diversity, high variability and peculiarities of functioning in conditions of long-term inter-project contact on a vast territory. …”
Get full text

Introduction to trophology of walleye pollock by Anatoly F. Volkov

“…Various aspects of walleye pollock feeding at different stages of its ontogenesis are reviewed and discussed. Structure and functional features of its mouth organs are considered with meristic and quantitative description of the filter one. …”
Get full text

Evaluative vocabulary as a method for quality presentation in advertising of children's products by E.A. Vazhdaeva

“…The functioning of lexemes with evaluative semantics in the texts of advertising of products for children aged from 0 to 3 years was analyzed. …”
Get full text

Digital power lines faults monitoring system by A. I. Fedotov, G. V. Vagapov, A. F. Abdullazyanov, A. M. Sharyapov

“…Software base on the mathematical models, as well as taking into account the results of a series of full-scale experiments of modeling various types of single-phase earth faults in the distribution power grids. The main functionalities the developed software presented for the description of solutions. …”
Get full text

Fast Nonparametric Inference of Network Backbones for Weighted Graph Sparsification by Alec Kirkley

“…Here we develop a completely nonparametric framework for inferring the backbone of a weighted network that overcomes these limitations and automatically selects the optimal set of edges to retain using the minimum description length principle. We develop objective functions for global and local network backboning which evaluate the importance of an edge in the context of the whole network and individual node neighborhoods, respectively, and are generalizable to any weight distribution under Bayesian model specifications that fix the average edge weight either exactly or in expectation. …”
Get full text

A Web App for the Animal Culture Database and a Template for Deploying Comparative Trait Databases With Shiny by Kiran Basava, Cristian Román‐Palacios

“…Using the Animal Culture Database (ACDB) as a case study, we highlight the web app's functionality and potential transversal applications for research and deploying other databases. …”
Get full text

An Adaptive Conceptualisation of Artificial Intelligence and the Law, Regulation and Ethics by Ikpenmosa Uhumuavbi

“…The description of a combination of technologies as ‘artificial intelligence’ (AI) is misleading. …”
Get full text

Large-scale outbursts of lakes in the Antarctic oases: current knowledge by A. S. Boronina

“…Through to the ongoing work, albeit irregular, our understanding of functioning of the surface hydrological systems of Antarctic oases is steadily growing.…”
Get full text

A Monument to a Scientific Error: Revisiting Vysotsky’s Version of James Cook’s Death by Alexander K. Zholkovsky

“…Thus, the monorhyme functions as an iconic projection of this structural-semantic construction. …”
Get full text

A schistosome cAMP-dependent protein kinase catalytic subunit is essential for parasite viability. by Brett E Swierczewski, Stephen J Davies

“…Eukaryotes, protozoan, and helminth parasites make extensive use of protein kinases to control cellular functions, suggesting that protein kinases may represent novel targets for the development of anti-parasitic drugs. …”
Get full text

Abbreviated Chinese Words of Coronavirus Era with a Structural-Semantic Component ‘in a Cloud Format’ by Xiaoge Li

“…The article is devoted to the description of the analysis of compound words results built according to the model “云xx”. …”
Get full text

Thorny Way to the East: Expedition to China of Adviser to the Chancellery V. F. Bratishchev in 1757 by Yu. G. Blagoder

“…The article notes the principles of functioning of the administrative system of the Russian Empire in the middle of the 18th century. …”
Get full text

Big Data Applications in Social Media Research: The Experience of Unsuccessful Data Analysis of Ukrainian Facebook by A. Tokarev

“…This article showcases a detailed description of the first stage of research on the discourse of Ukrainian opinion leaders on Facebook conducted by a team of researchers representing MGIMO University, Lomonosov Moscow State University, and Institute of Economy at the Russian Academy of Sciences. …”
Get full text