Intestinal Parasites Infection in Children with Cancer in Ahvaz, Southwest Iran by Roya Salehi Kahyesh, Arash Alghasi, Shekoufe Haddadi, Asaad Sharhani

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Surgical, non-traumatic splenopathies by Ivonne López Masó, Rafael Trinchet Soler, Manuel García Artiles, Ada Arlenis Pérez Mayo

“…Illnesses like idiopatic thrombocytopenic purple, hereditary spherocytosis, sickle cell anemia, beta thalassemia, portal hypertension and other non-traumatic disseases that carry out with congestive splenomegaly and hypersplenism, find an effective alternative with the total or partially splenectomy. …”
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Targeting the Hepcidin-Ferroportin Axis in the Diagnosis and Treatment of Anemias by Elizabeta Nemeth

“…Deficient production of hepcidin causes systemic iron overload in iron-loading anemias such as beta-thalassemia; whereas hepcidin excess contributes to the development of anemia in inflammatory disorders and chronic kidney disease, and may cause erythropoietin resistance. …”
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The Antioxidant Effect of Erythropoietin on Thalassemic Blood Cells by Johnny Amer, Mutaz Dana, Eitan Fibach

“…Because of its stimulating effect on RBC production, erythropoietin (Epo) is used to treat anemia, for example, in patients on dialysis or on chemotherapy. In β-thalassemia, where Epo levels are low relative to the degree of anemia, Epo treatment improves the anemia state. …”
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Sprengel's Deformity Associated with Musculoskeletal Dysfunctions and Renal Anomalies: A Case Report by Mohammad Hossein Kariminasab, Masoud Shayeste-Azar, Majid Sajjadi Saravi, Mehrdad Taghipour Gorgikolai

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Thalassemic DNA-Containing Red Blood Cells Are under Oxidative Stress by Mutaz Dana, Eugenia Prus, Eitan Fibach

“…Using flow cytometry methodology, we measured oxidative status parameters of these cells in patients with β-thalassemia. In each patient studied, these cells had higher content of reactive oxygen species and exposed phosphatidylserine compared with their DNA-free counterparts. …”
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Two Novel Variants in the ATRX Gene Associated with Variable Phenotypes by D. Hettiarachchi, B. A. P. S. Pathirana, P. J. Kumarasiri, V. H. W. Dissanayake

“…The X-linked alpha-thalassemia mental retardation (ATR-X) syndrome is a rare genetic condition caused by mutations in the X‐encoded gene ATRX. …”
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Clinical Application of Partial Splenic Embolization by Yong-Song Guan, Ying Hu

“…Common indications of PSE include hypersplenism with portal hypertension, hereditary spherocytosis, thalassemia, autoimmune hemolytic anemia, splenic trauma, idiopathic thrombocytopenic purpura, splenic hemangioma, and liver cancer. …”
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Iron Overload in Transfusion-Dependent Indonesian Thalassemic Patients by Pandji Irani Fianza, Anita Rahmawati, Sri Hudaya Widihastha, Shofura Afifah, Mohammad Ghozali, Andre Indrajaya, Dilli Marayuzan Akbar Pratama, Dimmy Prasetya, Teddy Arnold Sihite, Mas Rizky A. A. Syamsunarno, Djatnika Setiabudi, Suthat Fucharoen, Ramdan Panigoro

“…Thalassemia is a genetic disease caused by disruption of globin chain synthesis leading to severe anemia and thus regular blood transfusion is necessary. …”
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Varied Age of First Presentation of Sickle Cell Disease: Case Presentations and Review by Alexis Claeys, Susanne Van Steijn, Lydia Van Kesteren, Elizabet Damen, Machiel Van Den Akker

“…Many factors are responsible for the age at which sickle cell disease is diagnosed: doctor’s delay (unfamiliarity with the disease), patient’s delay (education and financial position of the parents, cultural factors), high- versus low-resource country (availability of newborn screening), fetal hemoglobin, reticulocyte count, and genetic modulators, such as SCD genotype, alpha-thalassemia, fetal hemoglobin concentration, and G6PD deficiency. …”
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Acute Sickle Hepatic Crisis after Liver Transplantation in a Patient with Hb SC Disease by J. H. Gillis, S. K. Satapathy, L. Parsa, P. B. Sylvestre, N. Dbouk

“…It occurs predominantly in patients with homozygous (Hb SS) sickle cell anemia and to a lesser degree in patients with Hb SC disease, sickle cell trait, and Hb S beta thalassemia. Patients commonly present with jaundice, right upper quadrant pain, nausea, low-grade fever, tender hepatomegaly, and mild to moderate elevations in serum AST, ALT, and bilirubin. …”
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Pyruvate Kinase Deficiency Causing Priapism by Vinay Hanyalu Shankar, Bharadwaj Adithya-Sateesh, Nicole Gousy, Girma Ayele, Freyr Petursson, Rediet Atalay, Miriam Michael

“…This differs greatly as priapism has been frequently reported in patients with other chronic hemoglobinopathies such as sickle cell disease, thalassemia, and G6PD with and without splenectomy. …”
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Usability test of the “Denia-IS” mobile application for sustainability high-risk pregnancy early detection in rural areas by Dwi Anggraeni Mekar, Triyanto Endang, Iskandar Asep, Fatoni Amin, Niyomdecha Najwa

“…The exclusion criteria in this study were a history of chronic hypertension, chronic bleeding, thalassemia, and suffering from malaria. For usability evaluation, 120 respondents were recruited from the outpatient clinic. …”
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Nutritional Evaluation of Pediatric Patients with Sickle Cell Disease Treated with Hydroxyurea by Belkis Lázara Rodríguez Jorge, Lucía Morejón Díaz, Yoandra León Rayas, María Santa Cruz

“…<br /><strong>Results:</strong> 15 patients were studied, there was a predominance of females (60 %) and adolescents represented 80 % of the patients in the study. 10 patients (66.7 %) presented the homozygous form; the Sβ thalassemia and SC variant were represented with 2 and 3 patients, respectively. …”
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Cardiovascular Characterization of Children and Adolescents with Sickle Cell Anemia by Nancy González Vales, Ximena Laura Graña, Lucía Díaz Morejón, Tamara Sánchez Estrada, Belkis Rodríguez Jorge, Ifraín Machín Caride

“…The correlation between baseline hemoglobin and nutritional status showed a prevalence of 66.7 % for eutrophic children, with SB thalassemia predominating with 80 %. 57 % presented cardiovascular repercussion mainly the group of 7 to 10 years with 63.6 %.…”
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Overexpression of MiR-183/96/182 Triggers Retina-Like Fate in Human Bone Marrow-Derived Mesenchymal Stem Cells (hBMSCs) in Culture by Mohammad-Reza Mahmoudian-Sani, Fatemeh Forouzanfar, Samira Asgharzade, Nilufar Ghorbani

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Prevalence and clinical profile of hepatitis C virus infections in multitransfused thalassemic patients in the capital twin cities of Pakistan by Z. Z. Piracha, U. Saeed, R. Uppal, M. R. Uppal, A. Ahmad Khan, M. Abdullah, K. Mari, A. Basra, S. S. Gilani, M. N. Tariq, D. U. Ozsahin, B. Uzun, I. Ozsahin

“…Patients with beta thalassemia, who rely on lifelong blood transfusions, are particularly vulnerable to HCV infections. …”
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Frequency of Red Blood Cell Alloimmunization in Patients with Sickle Cell Disease in Palestine by Fekri Samarah, Mahmoud A. Srour, Dirgham Yaseen, Kamal Dumaidi

“…Of the SCD patients, 62 (53.4%) patients were HbSS and 54 (46.6%) patients were sickle β-thalassemia (S/β-thal). There were 53 (45.7%) females and 63 (54.3%) males. …”
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Association of Xmn I Polymorphism and Hemoglobin E Haplotypes on Postnatal Gamma Globin Gene Expression in Homozygous Hemoglobin E by Supachai Ekwattanakit, Yuwarat Monteerarat, Suchada Riolueang, Kalaya Tachavanich, Vip Viprakasit

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A liquid chromatography-high-resolution mass spectrometry method for separation and identification of hemoglobin variant subunits with mass shifts less than 1 Da by Ainslie Chen, Ryan M. Aquino, Hector A. Vidal, Carolyn V. Wong, Ruben Y. Luo

“…Results: Seven heterozygous Hb variant samples (Hb C with α-thalassemia trait, Hb E, Hb D-Punjab, Hb G-Accra, Hb G-Siriraj, Hb Tarrant, and Hb G-Waimanalo) were selected to demonstrate the LC separation of Hb variant and normal subunits with mass shifts of less than 1 Da. …”
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