Giant Appendiceal Leiomyosarcoma: A Rare and Unusual Tumour by Christine Natalia, Cherry E. Koh, Peter J. Lee

“…While carcinoid tumours and adenocarcinomas comprise the majority of appendiceal tumours, rarely, lymphomas or sarcomas may also present in the appendix. Appendiceal leiomyosarcomas are rare, and to date, only a handful of cases have been reported. …”
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Malignant Peripheral Nerve Sheath Tumors in Children with Neurofibromatosis Type 1 by Apostolos Pourtsidis, Dimitrios Doganis, Margarita Baka, Despina Bouhoutsou, Maria Varvoutsi, Maria Synodinou, Panagiota Giamarelou, Helen Kosmidis

“…Malignant peripheral nerve sheath tumors (MPNSTs) are rare in children and account for approximately 5–10% of all soft tissue sarcomas in adults. MPNSTs may occur independently but individuals with neurofibromatosis type 1 (NF1) have a significantly increased risk. …”
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Extraosseous Intradural Chondrosarcoma of the Cervical Spine: A Case Report with Brief Review of Literature by Elizabeth Presutto, Sejal Patel, Joseph Fullmer, Sajeev Ezhapilli

“…One-third of all mesenchymal chondrosarcomas are extraosseous soft tissue sarcomas, rendering this as an uncommon entity. We report a rare case of an extraosseous chondrosarcoma with the cervical spinal canal in a 21-year-old male. …”
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Endometrial Stromal Hyperplasia: An Underrecognized Condition by Efthimios Sivridis, Gerasimos Koutsougeras, Alexandra Giatromanolaki

“…Hyperplasia of the endometrial stroma is a poorly recognized lesion, lacking widespread recognition with most, if not all, such cases sequestrated in the literature as endometrial stromal nodules or low-grade endometrial stromal sarcomas. In this paper, we describe three examples of “endometrial stromal hyperplasia” which have a remarkable morphological similarity with the normally proliferating endometrial stroma and the endometrial stromal neoplasms, but which also possess subtle, but sufficient, differences to justify their taxonomic separation.…”
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Dedifferentiated Liposarcoma Arising in an Esophageal Polyp: A Case Report by Jorge Torres-Mora, Ann Moyer, Mark Topazian, Jeffrey Alexander, Tsung-Teh Wu, Amber Seys, Karen Fritchie

“…Liposarcoma is one of the most common sarcomas in adults, but only rarely presents as an esophageal primary. …”
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Primary Malignant Fibrous Histiocytoma of the Lung: A Case Report by I. Tsangaridou, G. Papamihalis, K. Stathopoulos, O. Konstantinopoulos, L. Thanos

“…Primary malignant fibrous histiocytoma (MFH) of the lung is extremely rare although it is among the most common soft tissue sarcomas in adults. Surgery is the primary mode of therapy, with high rates of local and distant recurrence, while radiation therapy appears to be a very useful adjunct, decreasing local relapse. …”
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Metastatic Uterine Leiomyosarcoma Involving Bilateral Ovarian Stroma without Capsular Involvement Implies a Local Route of Hematogenous Dissemination by Monica Dandapani, Brandon-Luke L. Seagle, Amer Abdullah, Bryce Hatfield, Robert Samuelson, Shohreh Shahabi

“…Uterine sarcomas spread via lymphatic and hematogenous dissemination, direct extension, or transtubal transport. …”
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Giant Ulcerative Dermatofibroma by Turgut Karlidag, Erol Keles, Israfil Orhan, Mehmet Erkan Kaplama, Bengu Cobanoglu

“…Dermatofibrosarcoma protuberans, which is clinically and histopathologically of malignant character, displays difficulties in the diagnosis since it has similarities with basal cell carcinoma, epidermoid carcinoma, and sarcomas. Head and neck involvement is very rare. In this study, a giant dermatofibroma case, which is histopathologically, ulcerative dermatofibroma, the biggest lesion of the head and neck region and seen rarely in the literature that has characteristics similar to dermatofibrosarcoma protuberans, has been presented.…”
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Primary Paratesticular Leiomyosarcoma: A Case Report and Literature Review by Zeineb Naimi, Semia Zarraa, Salma Kammoun, Safia Yahyaoui, Maha Driss, Chiraz Nasr

“…Paratesticular soft tissue sarcomas are very rare malignant mesenchymal tumors. …”
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Case Report of Successful Childbearing after Conservative Surgery for Cervical Mullerian Adenosarcoma by Seiji Kanayama, Masako Nakamura, Hidekazu Oi, Sumire Sugimoto, Yoshikazu Sasaki, Tomoko Uchiyama, Chiho Ohbayashi, Hiroshi Kobayashi

“…Mullerian adenosarcoma (MA) is a rare tumor variant with low malignancy potential and is reported to account for 8% of all uterine sarcomas. Cervical MAs are reported to occur in relatively younger patients with the mean age of 27 years, while those in the uterine corpus generally present in postmenopausal women. …”
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Primary Osteosarcoma of the Breast: A Case Report by Anna Rizzi, Alberto Soregaroli, Claudia Zambelli, Fausto Zorzi, Stefano Mutti, Claudio Codignola, Paola Bertocchi, Alberto Zaniboni

“…Treatment follows the model of sarcomas affecting other locations and must be planned in a multidisciplinary fashion. …”
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Retroperitoneal Malignant Peripheral Nerve Sheath Tumor Replacing an Absent Kidney in a Child by Samin Alavi, M. T. Arzanian, Yalda Nilipour

“…Malignant peripheral nerve sheath tumors (MPNSTs) are nonrhabdomyosarcoma soft tissue sarcomas with rare occurrence in children specially in the retroperitoneum. …”
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A Case of Myxoid Liposarcoma of the Retroperitoneum: A Challenging Tumour for Diagnosis and Treatment by Emanuele Grasso, Fabio Marino, Michele Bottalico, Michele Simone

“…Retroperitoneal sarcomas are rare neoplasms that account for only 1%-2% of all solid tumors and liposarcomas represent the most frequent histological type. …”
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Paravertebral Burkitt's Lymphoma in a Child: An Unusual Presentation by C. Hoyoux, P. Forget, C. Piette, M. F. Dresse, B. Florkin, L. Rausin, A. Thiry

“…Paravertebral malignant tumors constitute 4.8% of cancer cases in pediatric oncology and are mostly composed of neuroblastoma (46.4%) and soft tissue sarcomas (35.7%). We describe the case of a Caucasian 6-year-old boy who was admitted for middle back pain radiated to limbs and progressively increasing weakness of the legs, suggesting a spinal cord disease. …”
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Rapid Multiorgan Dissemination of Low-Grade Myxofibrosarcoma: A Case Report by Yasutaka Murahashi, Mitsunori Kaya, Tamotsu Soma, Mikito Sasaki, Satoshi Nagoya, Takuro Wada, Toshihiko Yamashita

“…Myxofibrosarcoma is one of the most common sarcomas in the extremities of elderly people. It is characterized by a high frequency of local recurrence due to an infiltrative growth property. …”
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Periocular Myxoma in a Child by Dolores Ríos y Valles-Valles, Ana María Vera-Torres, Héctor A. Rodríguez-Martínez, Abelardo A. Rodríguez-Reyes

“…Midfacial myxomas should be differentiated from other benign and malignant tumors such as dermoid, hamartoma, neurofibroma, nasolacrimal duct cyst, and sarcomas in particular embryonal rhabdomyosarcoma. …”
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Myxoid Liposarcoma of the Greater Omentum. Case Report and Literature Review by Alexander Marchena Rodríguez, Flavia Linares Tovar, Jorge Carlos González Fariñas

“…It is the most frequent of the soft tissue sarcomas in adults. Themost frequent location is in the lower extremities, the abdominal is rare.It reaches enormous proportions. …”
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Beta-Human Chorionic Gonadotropin Producing Osteosarcoma of the Sacrum in a 26-Year-Old Woman: A Case Report and Review of the Literature by Ryan Glass, Jaya Ruth Asirvatham, Leonard Kahn, Mohamed Aziz

“…However, very few cases have been reported in sarcomas. We present the case of a 26-year-old female who presented with a metastatic osteosarcoma. …”
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A Rare Occurrence of Primary Hepatic Leiomyosarcoma Associated with Epstein Barr Virus Infection in an AIDs Patient by Haritha Chelimilla, Kanthi Badipatla, Ariyo Ihimoyan, Masooma Niazi

“…Close association of Epstein Barr virus (EBV) induced soft tissue sarcomas is proven, especially in the presence of immunosuppression encountered in HIV/AIDS patients and in posttransplant patients. …”
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A case of cavernous hemangioma with focal proliferation of endothelium of the left atrium by M.V. Voitsekhivska, I.V. Irkin, G.G. Prus, O.S. Chumak, V.O. Kuts, M.V. Shymanko, G.I. Darvish, O.J. Zharinov

“…When the tumor of the heart is detected during non-invasive methods of heart visualisation the physicians should be alerted about the possibility of not only the most common type of tumor (myxoma), but also more rare heart tumors such as hemangioma, rabdomioma, lipoma, fibroma and sarcoma…”
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