Study on Management of Blood Transfusion Therapy in Patients with Hereditary Spherocytosis by Shiyue Ma, Lingjian Tang, Chaoli Wu, Hui Tang, Xue Pu, Jinhong Niu

“…Hereditary spherocytosis (HS) is a chronic hemolytic disorder caused by inherited defects in the red blood cell membrane. This study discusses the treatment strategy for the decline in hemoglobin level in three HS probands with moderately severe or severe hemolysis and summarizes the appropriate laboratory tests that help improve clinical management of blood transfusion in HS patients. …”
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Cardiac manifestation of phenylketonuria in adulthood by Péter Homródi, Emese Tóth-Zsámboki, Róbert Gábor Kiss, Orsolya Lovász, Gábor Zoltán Duray

“…Conclusion: PKU is a rare inherited amino acid metabolic disease with widespread complications affecting multiple organ systems. …”
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Exploring patient-centered barriers to hemophilia care in Southern Nigeria: Study Protocol by Eguzo K, Ekwere T, Kirikareye B, Okoye H, Egharevba P, Oluoha C

“… Background: Hemophilia is a rare, inherited bleeding disorder which affects about three out of every one million Nigerians. …”
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ZÂRÎ’NİN MÂNZÛME-İ ŞEMÂİL-İ ŞERÎF’İNDE HZ. PEYGAMBER’İN AHLAKI by Hakan Temir, Muhammed Karaca

“…Because nations often inherited their cultural heritage with poetry and transferred them to the next generations with poetry. …”
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Need for judicious selection of runoff inputs in a global flood model by Jayesh Parmar, Mohit Prakash Mohanty, Subhankar Karmakar

“…These widely adopted GFMs, capable of producing flood characteristics, require runoff input typically derived from land surface models (LSMs) or global hydrological models (GHMs), which are prone to inherit cascading uncertainties. Moreover, the utilization of a single runoff input into a GFM can produce biased and misinterpreted flood hazards due to underestimation or overestimation of GFM outputs. …”
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Phenotypic diversity of bread wheat lines with introgressions from the diploid cereal Aegilops speltoides for technological properties of grain and f lour by L. V. Shchukina, I. F. Lapochkina, T. A. Pshenichnikova

“…These lines can be used for baking bread. Line 82/00i inherited from Ae. speltoides a soft-grain endosperm, which indicates the introgression of the Ha-Sp gene, homoeoallelic to the Ha gene of bread wheat, into ‘Rodina’. …”
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Pathogenetic therapeutic approaches for endocrine diseases based on antisense oligonucleotides and RNA-interference by Olga Golounina, Ildar Minniakhmetov, Ramil Salakhov, Rita Khusainova, Ekaterina Zakharova, Igor Bychkov, Natalia Mokrysheva

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Epidemiology, management and patient needs in myasthenia gravis: an Italian multistakeholder consensus based on Delphi methodology by Renato Mantegazza, Giuseppe Limongelli, Carlotta Galeone, Francesco Habetswallner, Raffaele Iorio, Giuseppina Annicchiarico, Maria Bonaria Uccheddu, Paolo Mariani

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NEGATION, INCLUDING, GRADUAL OBLIVION: STATE STRATEGIES ON SOVIET HERITAGE IN GEORGIA, ARMENIA AND AZERBAIJAN by A. A. Tokarev

“…The difference lies in the ratio between pro-Soviet and anti-Soviet elements.Azerbaijanseems to maintain a pro-Soviet narrative more than the others. It inherited the Soviet cult of personality and combined this practice with a completely non-Soviet (Eastern) tradition of political dynasties covered by the election system.The Armenian political tradition includes reference to Soviet Armenia as theSecondRepublic, which distinguishes the country from the neighbors who consider themselves to be the successors of the democratic republics that emerged during the Civil War inRussia. …”
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Age-related aspects of glioma: current understanding. Literature review by Serhii P. Luhovskyi, Tetiana Y. Kvitnytska-Ryzhova

“…Pediatric-type and adult-type low-grade gliomas (pLGG and aLGG) differ in location, biological behavior, and molecular-genetic profiles. Inherited syndromes (e.g., NF-1, TSC) associated with glioma development are linked to specific LGG subtypes occurring in childhood, adolescence, and adulthood. …”
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Prevalence and spectrum of haemoglobinopathies in females of reproductive age group- A first tertiary care center experience in Punjab, North India by Vikram Narang, Anshul Jain, Sumit Grover, Ankita Soni, Monika Narang, Ashima Taneja

“…Background: Thalassemia and hemoglobinopathies are a group of inherited conditions characterized by abnormalities in the synthesis or structure of hemoglobin (Hb). …”
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Przestrzenio-czas i czaso-kultura. Uwagi o komplementarności przestrzeni, kultury, czasu i krajobrazu by Jacek L. Łapiński

“…A cultural landscape is a manifestation of collective national remembrance which was inherited through generations, society, and ethnic groups. …”
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Von Hippel-Lindau (VHL) inactivation in sporadic clear cell renal cancer: associations with germline VHL polymorphisms and etiologic risk factors. by Lee E Moore, Michael L Nickerson, Paul Brennan, Jorge R Toro, Erich Jaeger, Jessica Rinsky, Summer S Han, David Zaridze, Vsevolod Matveev, Vladimir Janout, Hellena Kollarova, Vladimir Bencko, Marie Navratilova, Neonilia Szeszenia-Dabrowska, Dana Mates, Laura S Schmidt, Petra Lenz, Sara Karami, W Marston Linehan, Maria Merino, Stephen Chanock, Paolo Boffetta, Wong-Ho Chow, Frederic M Waldman, Nathaniel Rothman

“…Alteration prevalence did not differ by histopathologic characteristics or occupational exposure to trichloroethylene. ccRCC cases with particular VHL germline polymorphisms were more likely to have VHL inactivation through promoter hypermethylation than through sequence alterations in tumor DNA, suggesting that the presence of these SNPs may represent an example of facilitated epigenetic variation (an inherited propensity towards epigenetic variation) in renal tissue. …”
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The status of women in the Ancient East: peculiarities of marriage and family relations in Mesopotamia by I. A. Lohvynenko, Ye. S. Lohvynenko

“…On the basis of the analysis of the legislation of the state institutions of the time, the purpose of marriage was determined, that is the birth and upbringing of children who were to inherit and multiply the family property and perform the necessary sacred rites, which were to help the dead in the afterlife. …”
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US Deterrence against Russia and China (based on strategic documents of J. Biden administration) by V. I. Batyuk

“…In addition to the alliances inherited from the Cold War, the Biden administration is seeking to develop new ‘bloc structures’ in the Indo-Pacific region, in particular the Quadrilateral Security Dialogue (QUAD). …”
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A Case of Status Epilepticus in a Patient Experiencing an Acute Attack of Hereditary Angioedema by Danielle Weinberg, Steven Gayda, Kyle Hultz, Hanan Atia, Brian Kohen, Eric Boccio

“…Hereditary angioedema is inherited in an autosomal dominant pattern and results in a quantitative deficiency (HAE type I) or dysfunction (HAE type II) of the C1-esterase inhibitor (C1-INH) protein. …”
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Successful management of refractory epilepsy in creatine transporter deficiency with cannabidiol and clobazam: A case report by Maria Borrell‐Pichot, Carmen Fons, Susana Boronat, Alba Sierra‐Marcos

“…Abstract Creatine transporter deficiency (CRTR‐D) is a rare X‐linked inherited disease belonging to the group of cerebral creatine deficiency disorders. …”
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Evaluation of a national framework for rational use of medicines in Kazakhstan and its role in improving medicine use practices at the organizational and national levels by Gulzira Zhussupova, Ainur Aiypkhanova, Saule Zhaldybayeva, Dinara Satmbekova, Tamila Akhayeva, Sholpan Kaliyeva

“…Abstract Background Kazakhstan inherited the Semashko health system model, known for the centralized adoption of rules at the Ministry of Health (MoH) level that regulate the healthcare system. …”
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Alström syndrome: the journey to diagnosis by Akshat Sinha, Kerry Leeson-Beevers, Catherine Lewis, Elizabeth Loughery, Tarekegn Geberhiwot

“…Abstract Background Alström syndrome (AS) is a recessively inherited genetic condition which is ultra-rare and extremely complex. …”
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Case Report of Gastrointestinal Bleeding in an Adult with Chronic Visceral Acid Sphingomyelinase Deficiency by David Cassiman, Louis Libbrecht, Wouter Meersseman, Alexander Wilmer

“…Acid sphingomyelinase deficiency (ASMD, also known as Niemann-Pick Type A and Type B disease) is a rare, inherited metabolic disorder. Liver-related issues, including cirrhosis and variceal haemorrhage, are a leading cause of early mortality in individuals with chronic forms of ASMD. …”
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