Dystrophic Epidermolysis Bullosa in Pregnancy: A Case Report of the Autosomal Dominant Subtype and Review of the Literature by Nicole Colgrove, Rayan Elkattah, Howard Herrell

“…Epidermolysis bullosa (EB) is a group of inherited blistering skin diseases that vary widely in their pathogenesis and severity. …”
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Novel navigation signal design based on spreading code time shift position modulation by Jiafang KANG, Hongxing WANG, Xiguo LIU, Peilin ZHONG, Bifeng LI

“…A novel navigation signal design method based on spread code time shift position modulation was proposed,which inherits the idea of separating the pilot signal component and the data signal component,and applies time shift position of the spread code to carry data information.The old pattern of using carrier phase to carry information was changed,the power efficiency of data signal components and the performances of the satellite navigation system were improved.Theoretical analysis and simulation results show that the proposed method can significantly improve the transmission rate of data signal component or power ratio of the pilot signal component to data signal component without increasing the total transmission power.Then,the transmission rate,acquisition and tracking performance,positioning accuracy and other technical indicators of the satellite navigation system can be further improved.…”
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Analysis and Verification of Compound SRFPI-LADRC Strategy for an Off-Grid Single-Phase Inverter by Liaoyuan Lin, Haoda Li, Kai Zhu, Lingling Shi, Ping Li

“…Detailed theoretical analyses on the compound strategy and its performance are presented, indicating that it inherits the advantages of the two controllers. Moreover, contrast experiments are carried out to verify the feasibility and superiority of the proposed control strategy. …”
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Seizure, Deafness, and Renal Failure: A Case of Barakat Syndrome by Nasrollah Maleki, Bahman Bashardoust, Manouchehr Iranparvar Alamdari, Zahra Tavosi

“…In conclusion, we need to be aware of rare inherited conditions in a patient with abnormal physical and laboratory findings even though their initial presentation was seizure and hypocalcemia.…”
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Vulvar Malignancy in Neurofibromatosis Syndrome by Angela Musella, Innocenza Palaia, Lavinia Domenici, Assunta Casorelli, Angela Martoccia, Pierluigi Benedetti Panici

“…Type 1 neurofibromatosis (NF1) is a dominantly inherited neurologic disorder that affects primarily the skin, bones, and peripheral nervous system. …”
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Application of Butterfly Clos-Network in Network-on-Chip by Hui Liu, Linquan Xie, Jiansheng Liu, Lei Ding

“…Simulation analyses show that BFC inherits the rich path diversity of Clos network, and it has a better performance than butterfly network in throughput and delay in a quite congested traffic pattern.…”
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Novel wobble-defended M-MULTOPS structure and its application in detecting network abnormal traffic by SUN Zhi-xin1, TANG Yi-wei1, GONG Jing1

“…A new detection method: wobble defended M-MULTOPS（modified-multi-level tree for online packet statistics） structure was presented.Aiming at the change of network traffic in core routers,ABF（adapted bloom filter） algorithm to assemble destination addresses to the IP packets was employed.And it put forward M-MULPOTS struc-ture to analyze results of the ABF algorithm,monitoring changes of network traffic and detecting network flow ab-normity in real time.For making use of the Wobble-defended M-MULTOPS structure,the method can work steadily and exactly,even when the traffic of network is wobbling terribly by the pulse attack.And because the M-MULTOPS inherits the MULTOPS ’s flexible attribution,it declined the spending of system resources at maximum.A detection system em-ploying this method has been run successfully in routers as an individual module.…”
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Leydig Cell Tumor Associated with Testicular Adrenal Rest Tumors in a Patient with Congenital Adrenal Hyperplasia due to 11β-Hydroxylase Deficiency by Nadia Charfi, Mahdi Kamoun, Mouna Feki Mnif, Neila Mseddi, Fatma Mnif, Nozha Kallel, Basma Ben Naceur, Nabila Rekik, Hela Fourati, Emna Daoud, Zainab Mnif, Mourad Hadj Sliman, Tahia Sellami-Boudawara, Mohamed Abid

“…Congenital adrenal hyperplasia (CAH) describes a group of inherited autosomal recessive disorders characterized by enzyme defects in the steroidogenic pathways that lead to the biosynthesis of cortisol, aldosterone, and androgens. …”
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A Rare Case of Severe Congenital RYR1-Associated Myopathy by Nicola Laforgia, Manuela Capozza, Lucrezia De Cosmo, Antonio Di Mauro, Maria Elisabetta Baldassarre, Francesca Mercadante, Anna Laura Torella, Vincenzo Nigro, Nicoletta Resta

“…Congenital myopathies are a group of rare inherited diseases, defined by hypotonia and muscle weakness. …”
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Synergistic effects of mutation and glycosylation on disease progression by Shodai Suzuki, Motoyuki Itoh, Motoyuki Itoh, Motoyuki Itoh

“…It is regulated by multiple glycosyltransferases and can be influenced by various factors. Inherited missense mutations in glycosylated proteins such as NOTCH3, Low-density lipoprotein receptor (LDLR), and Amyloid precursor protein (APP) could affect their glycosylation states, leading to cerebral small vessel disease, hypercholesterolemia, and Alzheimer’s disease, respectively. …”
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An Unusual Occurrence of Hepatic Granulomas and Secondary Sitosterolemia in Turner Syndrome by JayaKrishna Chintanaboina, Pragnesh R. Shah, Thomas R. Riley

“…One patient had sitosterolemia, a rare inherited autosomal recessive disorder of cholesterol metabolism, after she ingested β-sitosterol supplement and had worsening liver function tests and lipid panel. …”
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Outdoor Theatrical Shows in the Remarkable Landscapes of the Chinese Mountains, Between Reinvention of a Tradition and Development of Tourism: the Example of the ‘Tianmen Fox Fairy... by Wei Xiang, Philippe Bachimon, Pierre Dérioz

“…A kitsch ‘mass’ show, it constitutes both a commercial reality of a new China and the postmodern modality of a cultural approach inherited from an official socialist discourse that is today legitimizing its actions by attaching itself to tradition.…”
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CAUSES AND CORRECTION OF PUBLISHING MALPRACTICE IN “STUDENT SCIENCE” by L. V. Kanayeva

“…The article discusses the “publication disease” of student science as a deviation phenomenon of the period of education reforming, and as a phenomenon inherited from the current scientific practice. Using case study method, the author analyzes two versions of students’ publications that represent the extreme levels of the deviant range in student publications. …”
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L’art et la science à l’épreuve du paysage by Catherine Chomarat-Ruiz

“…Thus, far to appeal to a simple articulation of art and science or to overcome the opposition – which would lead to testing it – the landscape challenges us to rethink the organization of the sciences relative to landscape, and beyond, the configuration of the fields of knowledge inherited from the nineteenth century.…”
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Case Report: Neonatal onset intractable diarrhea and hypoproteinemia due to intestinal malrotation and chronic midgut volvulus by Cuifang Zheng, Song Sun, Ying Gong, Shijian Miao, Kuiran Dong, Ying Huang

“…Congenital diarrhea and enteropathies (CODEs) are a rare heterogeneous group of inherited disorders that typically present with severe chronic diarrhea during the first weeks of life. …”
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The Ariege ‘Refuge’: Advantage and Diversity of a Host Topography by William Berthomière, Christophe Imbert

“…Drawing on the life histories of refugee activists in the French department of Ariège, we reveal a complex territoriality that, depending on the spaces considered, produces singular and distinct forms of mobilisation, inherited from past migratory experiences, the engagement of neo-rurals and the social networks linking mountains, valleys, piedmont towns and the Toulouse conurbation. …”
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Runoff Prediction Based on VMD-LSTM-ARMA Model by LUO Cankun, LIU Hao, HUANG Xin, SHAO Zhuang

“…To increase the accuracy of runoff prediction,a combined prediction model is proposed to solve the problems of runoff prediction.This model consists of the variational mode decomposition (VMD),long and short-term memory (LSTM) network,and autoregressive moving average (ARMA).To reduce the complexity of the incoming traffic,the runoff data is decomposed into three modal components with different frequencies by VMD.The low-frequency modal component inherits the temporal properties of the data and can be processed by constructing the LSTM prediction model,while the two high-frequency sequences are stationary time series and can be processed by constructing the ARMA prediction model.The prediction results of the three subsequences are superimposed to predict the runoff.Finally,the hourly flow data of Dongjiang Hydrometric Station of Xiangjiang river tributary in 2020 are used to forecast the inflow flow,and the results of comparative experiments with other algorithms show that the constructed model can effectively improve the accuracy of the hydrological forecast.…”
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Paese che vai usanza che trovi, tra cosmo e campanile by Pietro Clemente

“…The second one is a general rediscovery of the originality and richness of local cultures inherited from the past, that even today mark not only the sense of places and of belonging to them, but constitute a key resource for the younger generations’ imagination of the future and of their dwelling in it. …”
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McArdle's Disease Presenting as Unexplained Dyspnea in a Young Woman by Nha Voduc, Katherine A Webb, Christine D'Arsigny, Ian McBride, Denis E O'Donnell

“…McArdle's disease is a rare, inherited deficiency of myophosphorylase, an enzyme required for the utilization of glycogen. …”
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“Iran’s Shiite Influence Belt Policy: The Example of Bahraini Shiites by Orhan Karaoğlu

“… Along with the Persian perspective inherited from the Persian Empire, Shi'ism has significantly influenced and continues to influence the geopolitical and geo-cultural education of present-day Iran. …”
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