Role of B-Cell Lymphoma/Leukemia 11A in Normal and Malignant Hematopoiesis by Haihang Zhang, Junhao Zeng, Fangling Zhang, Jing Liu, Long Liang

“…B-cell lymphoma/leukemia 11A (BCL11A) is a crucial transcriptional regulator, widely recognized for its role in controlling fetal hemoglobin and its potential as a gene therapy target for inherited hemoglobinopathies. Beyond this, recent studies have also highlighted its key role in the maturation and function of immune cells and erythrocytes, mediated through the regulation of various molecules during hematopoietic development. …”
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Personalized biological treatment with lanadelumab in a patient with recurrent attacks of hereditary angioedema by Artur Gęsicki, Maciej F. Kozlowski, Karolina Żurawska, Weronika Ossowska, Jakub Sikora, Szymon Dyguś, Iwona Poziomkowska-Gęsicka

“…Hereditary angioedema (HAE) is an autosomal dominantly inherited disease caused by deficiency of C1 esterase inhibitor protein type 1 (about 85% of patients with HAE-C1-INH) or type 2 oedema (about 15% of patients with HAE-C1-INH) by C1 inhibitor dysfunction, with normal serum levels (HAE-2). …”
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Tsunami de béton : de l’empreinte à l’emprise sur les paysages littoraux après les catastrophes du 11 mars 2011 by Rémi Scoccimarro

“…From the 1950s onwards, the Sanriku protective coastal works took the form of giant dikes on Japan’s tsunami coast. Disfiguring the inherited landscapes, these dikes also changed the relationship to the sea. …”
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Éducation à la laïcité et enseignement laïque du fait religieux : enjeux d’une pédagogie du discernement by Anne Vézier

“…This teaching would serve to live together, according to the principle inherited by Condorcet that there can be no conflict between knowledge and values ​​(Audigier, 1991). …”
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Writing under the 'Auto/biographical Demand' in Deborah Feldman’s Unorthodox (2012) and Exodus (2015) by Szidonia Haragos

“…It argues that Feldman writes under the 'auto/biographical demand' as the grandchild of Hungarian Holocaust survivors and redeploys the inherited story of gendered suffering during the Holocaust in order to reconfigure her own Jewish American identity. …”
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Genetic factors for breast carcinogenesis by Pedro Enrique Miguel-Soca, Ivis Argüelles González, Marisol Peña González

“…Although these alterations which affect germinal cells produce inherited cancers, in most of the cases somatic cell genes are affected. …”
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Les apprentissages d’un RETEX scientifique et collectif sur l’ouragan Irma (saison cyclonique 2017, Petites-Antilles du Nord, projet ANR TIREX) by Frédéric Leone, Yann Bérard, Stéphanie Defossez, Jérémy Desarthe, Virginie Duvat, Delphine Grancher, Philippe Palany, Narcisse Zahibo

“…In particular, TIREX contributes to improve hurricane warnings, to identify inherited vulnerability factors, to understand the damage processes related to wind and sea, to monitor the dynamics of territorial and human recovery at the individual and collective levels, and more generally to strengthen the adaptation and response capacities of Lesser Antilles societies in the face of hurricanes.…”
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Local Convexity-Preserving C2 Rational Cubic Spline for Convex Data by Muhammad Abbas, Ahmad Abd Majid, Jamaludin Md. Ali

“…Data dependent sufficient constraints are imposed on single shape parameter to conserve the inherited shape feature of data. Remaining two of these shape parameters are used for the modification of convex curve to get a visually pleasing curve according to industrial demand. …”
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The Unified Hydrodynamics and the Pseudorapidity Distributions in Heavy Ion Collisions at BNL-RHIC and CERN-LHC Energies by Z. J. Jiang, J. Wang, K. Ma, H. L. Zhang

“…The leading particles are conventionally taken as the particles which inherit the quantum numbers of colliding nucleons and carry off most of incident energy. …”
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Acute Muscle Trauma due to Overexercise in an Otherwise Healthy Patient with Cystic Fibrosis by Henning Neubauer, Clemens Wirth, Katharina Ruf, Helge Hebestreit, Meinrad Beer

“…Cystic fibrosis (CF) is one of the most common inherited diseases and is caused by mutations in the CFTR gene. …”
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Localized variant of junctional epidermolysis bullosa with R795X mutation by Stefano Bighetti, Luca Bettolini, Sara Rovaris, Antonio Novelli, Paolo Incardona, Piergiacomo Calzavara-Pinton, Simone Caravello, Vincenzo Maione

“…Epidermolysis bullosa (EB) refers to a group of inherited disorders characterized by skin and mucous membrane fragility. …”
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Dental Findings and Treatment in Osteogenesis Imperfecta: A Case Report by Yasemin İspir, Özge Anıl

“…Abstract Osteogenesis imperfecta (OI) is a genetically inherited disease in which increased bone fragility, low bone mass, and connective tissue disorders are seen. …”
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Quand l’art public (dé)fait la ville ? by Pauline Guinard

“…Public art is conceived as a means to reconcile promotion of economic urban growth with overtaking of the divisions inherited from Apartheid. Nevertheless, in the light of an emblematic case study of one of these artworks, it is shown that public art as promoted by the municipality struggles to free itself from the legacy of Apartheid and to create social interaction into public spaces. …”
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Synaptic Plasticity, a Prominent Contributor to the Anxiety in Fragile X Syndrome by Tao Yang, Huan Zhao, Changbo Lu, Xiaoyu Li, Yingli Xie, Hao Fu, Hui Xu

“…Fragile X syndrome (FXS) is an inheritable neuropsychological disease caused by expansion of the CGG trinucleotide repeat affecting the fmr1 gene on X chromosome, resulting in silence of the fmr1 gene and failed expression of FMRP. …”
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Clinical approach to palpitations in pregnancy by Ferha Saeed, Kirun Gunganah, Anna S. Herrey

“…Patients with structural or functional abnormalities or inherited cardiovascular disease are more likely to develop arrhythmia, especially during pregnancy when the mother’s body undergoes extensive physiological adaptations, which further contribute to an increased arrhythmia risk. …”
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Le contrat d’embouchure du delta du Pô : un nouveau défi pour la gestion participative du territoire by Marina Bertoncin, Pierpaolo Faggi, Andrea Pase, Daria Quatrida

“…The Po Delta is located at the eastern end of a territory that inherits whatever happens upstream in the most populated and industrialized area of Italy: the basin of the River Po. …”
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Les institutions et les acteurs en santé au travail au Québec et en France : regard croisé by Nathalie Ferre

“…In establishments, several actors inherit various missions. The scope of the employer’s responsibility is greater in France.…”
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« Breaking Down the Borders of Memory : The Transatlantic Politics of Metatheatre in Sarah Ruhl’s Passion Play » by Noelia Hernando-Real

“…Among the strategies Ruhl employs in Passion Play, especial emphasis is put on the analysis of her use of metatheatre to discuss the importance of inherited role models in identity formation and the role of political leaders in manipulating their subjects’ identity, a fact that, Ruhl seems to acknowledge, is what has marked our history, in Europe as in the United States.…”
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Retinoid Therapy in a Case of Harlequin Ichthyosis with a Short Literature Review by Emad Bahashwan, Jaber Alfaifi, Sahar Elmaghawri Mohamed Moursi, Youssef Elbayoumi Soliman

“…Harlequin ichthyosis (HI) is a genetically inherited epidermal disorder due to the mutation of the ABCA12 gene, which is responsible for lipid transportation, and presents with large keratinised scales characterised by deep erythematous fissures, with ectropion and eclabium. …”
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L’ordre social et son gouvernement en perspective coloniale. Pour une histoire trans-territoriale de l’Espagne contemporaine by François Godicheau, Alina Castellanos Rubio

“…By observing both the logics of transformation of the institutions inherited from the Old Regime common to all these territories, and the particularities that make Cuba an exceptional terrain for economic and political experimentation, this article intends to show that the understanding of the phenomena of the government of the social order, like many others, must undoubtedly take into account the trans-territorial and global dimension of contemporary Spain.…”
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