CLINICAL PATTERNS OF MALABSORPTION SYNDROMES IN CHILDREN by Ginel Baciu, Carmen Baciu, Cristina Maria Mihai, Tatiana Chisnoiu, Ramona Mihaela Stoicescu, Adriana Luminita Balasa, Adriana Mocanu, Lorenza Forna, Alexandru Paul Baciu

“…Celiac disease (51%), cystic fibrosis (32%), and Cow’s milk protein allergy (17%) were the leading causes. …”
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Meconium Peritonitis and Periorchitis: Report of a Prenatal Case by Cem Yaşar Sanhal, İnanç Mendilcioğlu, Adnan Aslan, Murat Özekinci, Mehmet Şimşek

“…Meconium peritonitis may also be caused by viral infections (cytomegalovirus or parvovirus B19) and cystic fibrosis. Here, we report of a patient with fetal meconium peritonitis - periorchitis and perinatal management. …”
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Recent Developments in Sweat Analysis and Its Applications by Saima Jadoon, Sabiha Karim, Muhammad Rouf Akram, Abida Kalsoom Khan, Muhammad Abid Zia, Abdul Rauf Siddiqi, Ghulam Murtaza

“…Moreover, sweat comprises various biomarkers of different diseases including cystic fibrosis and diabetes. Additionally, the normalization of sampled volume of sweat is also necessary for getting efficient and useful results.…”
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Colistin: The phoenix Arises by JM Conly, BL Johnston

“…As a result, the use of polymyxin preparations has been mainly restricted to the treatment of lung infections due to multidrug-resistant (MDR) gram-negative bacteria in patients with cystic fibrosis (6,7). The emergence of bacteria resistant to most classes of commercially available antibiotics and the shortage of novel antimicrobial agents with activity against gram-negative microorganisms have led to the reemergence of polymyxins as a valuable addition to the therapeutic armamentarium. …”
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Study of Query Expansion Techniques and Their Application in the Biomedical Information Retrieval by A. R. Rivas, E. L. Iglesias, L. Borrajo

“…A corpus belonging to MEDLINE, called Cystic Fibrosis, is used as a knowledge source. Experimental results show that the proposed combinations of techniques greatly enhance the efficiency obtained by traditional queries.…”
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Inhalation Techniques Used in Patients with Respiratory Failure Treated with Noninvasive Mechanical Ventilation by Patrycja Rzepka-Wrona, Szymon Skoczynski, Dawid Wrona, Adam Barczyk

“…The administration of aerosolized medication is a basic therapy for patients with numerous respiratory tract diseases, including obstructive airway diseases (OADs), cystic fibrosis (CF), and infectious airway diseases. …”
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Burkholderia cepacia Complex: Emerging Multihost Pathogens Equipped with a Wide Range of Virulence Factors and Determinants by Sílvia A. Sousa, Christian G. Ramos, Jorge H. Leitão

“…Bcc bacteria are endowed with an extraordinary metabolic diversity and emerged in the 1980s as life-threatening and difficult-to-treat pathogens among patients suffering from cystic fibrosis. More recently, these bacteria became recognized as a threat to hospitalized patients suffering from other diseases, in particular oncological patients. …”
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A Case Report of Pulmonary Exacerbation after Initiation of Lumacaftor/Ivacaftor Therapy in a CF Female with Complicated Lung Disease by Elpis Hatziagorou, Eleana Kouroukli, Vasiliki Georgopoulou, John Tsanakas

“…Novel targeted treatments for Cystic Fibrosis give rise to new hope for an ever-growing number of CF patients with various mutations. …”
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Clinical benefits and risks of remote patient monitoring: an overview and assessment of methodological rigour of systematic reviews for selected patient groups by Constanze Wartenberg, Helen Elden, Malte Frerichs, Lennart L Jivegård, Kajsa Magnusson, Georgios Mourtzinis, Ola Nyström, Kajsa Quitz, Helen Sjöland, Therese Svanberg, Helena Vallo Hult

“…For four patient groups (children with complex needs, children with cystic fibrosis, specialist maternity care, and sleep apnea), systematic reviews of adequate quality concluded that scientific evidence on clinical patient benefits of remote monitoring is very limited. …”
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Acute fibrinous and organizing pneumonia after lung transplantation: A case report of treatment with infliximab and tocilizumab and literature review by Christophe Abellan, Foteini Ioakeim, Alessio Casutt, Benoit Lechartier, Zisis Balmpouzis, Samuel Rotman, Leslie Noirez, Isabelle Rochat, John-David Aubert, Angela Koutsokera

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Direct ring fluorination of 3-substituted 5-(1,3-dioxane) acetal isoxazoles: application to the formal synthesis of a bioactive fluorinated isoxazole by Bacheley, Lucas, Guillamot, Gérard, Phansavath, Phannarath, Ratovelomanana-Vidal, Virginie

“…This method was transposed to gram-scale and has been applied to the formal synthesis of a bioactive compound that increases CFTR (Cystic Fibrosis Transmembrane Conductance Regulator) activity.…”
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Extensive Mycobacterium abscessus Pneumonia in an Immunocompetent Infant with No Underlying Lung Pathology by Morouge M. Alramadhan, James R. Murphy, Michael L. Chang

“…Pulmonary infection due to Mycobacterium abscessus occurs in patients with cystic fibrosis, but rarely in immunocompetent children without underlying lung pathology. …”
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Molecular Basis for Mucolytic Therapy by Bonnie Dasgupta, Malcolm King

“…Airway obstruction in cystic fibrosis (CF) lung disease is accompanied by the accumulation of thick and viscous secretions resulting from chronic infection and inflammation, promoting recurrent exacerbations. …”
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PPARγ as a Potential Target to Treat Airway Mucus Hypersecretion in Chronic Airway Inflammatory Diseases by Yongchun Shen, Lei Chen, Tao Wang, Fuqiang Wen

“…Airway mucus hypersecretion (AMH) is a key pathophysiological feature of chronic airway inflammatory diseases such as bronchial asthma, cystic fibrosis, and chronic obstructive pulmonary disease. …”
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Diretrizes para desenvolvimento da competência em informação para pessoas com fibrose cística by Eliane Rodrigues Mota Orelo, Elizete Vieira Vitorino

“…A Coleta de dados se deu no acervo da Biblioteca Universitária da UFSC, no portal Scielo Brasil, no Portal Capes, nas bases de dados Ebsco e Web Of Science e, nas revistas nacionais de Biblioteconomia e Ciência da Informação, os termos de busca foram: “Information Literacy”, “Competência em Informação” “Cystic Fibrosis” e “Fibrose Cística”. Realizou-se entrevistas semiestruturadas via plataforma “google meet”, com pessoas com Fibrose Cística, acima de 18 anos de idade, residentes no estado de SC. …”
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Mycobacterium avium Infection of Multinucleated Giant Cells Reveals Association of Bacterial Survival to Autophagy and Cholesterol Utilization by Jayanthi J. Joseph, Amy Leestemaker-Palmer, Soheila Kazemi, Lia Danelishvili, Luiz E. Bermudez

“…Mycobacterium avium subsp. hominissuis (M. avium) is an opportunistic environmental pathogen that typically infects patients with existing lung conditions such as cystic fibrosis or COPD. Pulmonary M. avium infection generates peribronchial granulomas that contain infected macrophages and multinucleated giant cells (MGCs). …”
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Polymorphonuclear Leukocytes or Hydrogen Peroxide Enhance Biofilm Development of Mucoid Pseudomonas aeruginosa by Qi Tan, Qing Ai, Qi Xu, Fang Li, Jialin Yu

“…P. aeruginosa cells usually undergo mucoid conversion during chronic lung infection in patients with cystic fibrosis (CF) and resist destruction by polymorphonuclear leukocytes (PMNs), which release free oxygen radicals (ROS), such as H2O2. …”
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Azole-Induced Myositis after Combined Lung-Liver Transplantation by Sofie Happaerts, Michiel Wieërs, Ward Vander Mijnsbrugge, Laurent Godinas, Dirk Van Raemdonck, Laurens J. Ceulemans, Robin Vos, Geert M. Verleden

“…Our patient was a 38-year-old man who received a single sequential lung transplantation and liver transplantation because of end-stage cystic fibrosis. He presented to our emergency room with acute pain in both forearms at 3 weeks after voriconazole was initiated for invasive pulmonary aspergillosis infection. …”
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Treatment of Cytomegalovirus Infection with Cidofovir and CMV Immune Globulin in a Lung Transplant Recipient by Heinrike Wilkens, Martina Sester

“…A CMV-seronegative 42-year-old man with cystic fibrosis received a lung from a CMV-seropositive donor. …”
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Montelukast: More than a Cysteinyl Leukotriene Receptor Antagonist? by Gregory R. Tintinger, Charles Feldman, Annette J. Theron, Ronald Anderson

“…If so, montelukast is potentially useful in the chemotherapy of intermittent asthma, chronic obstructive pulmonary disease, cystic fibrosis, and viral bronchiolitis, which, to a large extent, involve airway epithelial cell/neutrophil interactions. …”
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