Epidemiology, microbiology and clinical impacts of non-tuberculous mycobacteria in adult patients with cystic fibrosis by Zoltán Örlős, Lilla Katalin Lőrinczi, Balázs Antus, Imre Barta, Zsuzsanna Miklós, Ildikó Horváth

“…Background: Due to its increasing prevalence and suboptimal treatment, non-tuberculous mycobacterial (NTM) infection is an emerging problem in patients with cystic fibrosis (CF). Detailed description of regional NTM prevalence and distribution, and identification of predictors of NTM acquisition in CF are essential to optimise treatment and surveillance guidelines. …”
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Cross-cultural adaptation and validation of the CFAbd-Score for gastrointestinal symptoms in patients with cystic fibrosis by Flávia N.S. Infante, Elizete A. Lomazi, Carlos Zagoya, Franziska Duckstein, Daniela O. Magro, Fernando Pessotto, Antônio F. Ribeiro, José D. Ribeiro, Jochen G. Mainz

Subjects: “…Cystic fibrosis…”
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Lithotripsy of Pancreatic Stones in a Patient with Cystic Fibrosis: Successful Treatment of Abdominal Pain by AA Weiss, JM Greig, S Fache

“…This article reports the case of an 18-year-old native Indian woman with cystic fibrosis who was experiencing pain related to pancreatitis, complicated by pancreatic duct stricture and lithiasis. …”
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Comparative Efficacy of Two Doses of Nebulized Colistimethate for the Eradication of Pseudomonas Aeruginosa in Children with Cystic Fibrosis by Marie-Sophie Brochet, Anne-Catherine McDuff, Jean-François Bussières, Elaine Caron, Geneviève Fortin, Denis Lebel, Jacques-Édouard Marcotte

“…BACKGROUND: Cystic fibrosis (CF) affects the respiratory and digestive systems. …”
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Hypogonadism in a Man With Cystic Fibrosis and an Unusually Low Serum Testosterone: A Cautionary Tale by Khemaporn Lertdetkajorn, MD, Crystal Cobb, DO, Rebecca J. Kapolka, MD, William R. Hunt, MD, Vin Tangpricha, MD, PhD

Subjects: “…cystic fibrosis…”
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Effect of Dead Volume on the Efficiency and the Cost to Deliver Medications in Cystic Fibrosis with Four Disposable Nebulizers by Sharon L Ho, Allan L Coates

“…OBJECTIVES: To evaluate the factors that affect nebulizer efficiency and to compare the relative cost effectiveness of nebulized medications used in the treatment of cystic fibrosis (CF), delivered by four types of disposable jet nebulizers that are widely used in hospitals.…”
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Identification of a Mutation in the Novel Compound Heterozygous CFTR in a Chinese Family with Cystic Fibrosis by Hongxia Shao, Jingna Hua, Qi Wu, Xiaoge Li, Ming Zhang, Herong Wang, Junping Wu, Long Xu, Yi Xie, Li Li, Huaiyong Chen

“…Cystic fibrosis (CF) is one of the most common autosomal recessive disorders among Caucasians of Northern European descent but is uncommon in the Chinese population. …”
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Sex Disparities in Effects of Cystic Fibrosis-Related Diabetes on Clinical Outcomes: A Matched Study by Robert J Miller, Hugh D Tildesley, Pearce G Wilcox, Hongbin Zhang, Stuart H Kreisman

“…BACKGROUND: Cystic fibrosis-related diabetes (CFRD) is an increasingly prevalent comorbidity factor for patients with cystic fibrosis (CF). …”
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Neutrophil extracellular traps are associated with airways inflammation and increased severity of lung disease in cystic fibrosis by Sheonagh M. Law, Gareth Hardisty, Jonathan L. Gillan, Nicola J. Robinson, Donald J. Davidson, Moira K.B. Whyte, Ian Dransfield, Robert D. Gray

“…Background Cystic fibrosis (CF) is characterised by inflammatory lung disease and large numbers of airways neutrophils. …”
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Quantitative and O2 Enhanced MRI of the Pathologic Lung: Findings in Emphysema, Fibrosis, and Cystic Fibrosis by Alfred Stadler, Leopold Stiebellehner, Peter M. Jakob, Johannes F. T. Arnold, Edith Eisenhuber, Isabella von Katzler, Alexander A. Bankier

“…Oxygen enhanced MRT is able to demonstrate reduced diffusion capacity and diminished oxygen transport in patients with emphysema and cystic fibrosis. Discussion: results published in literature indicate that T1 mapping and oxygen enhanced MR imaging are promising new methods in functional imaging of the lung and when evaluated in conjunction with the pure morphological images can provide additional valuable information.…”
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The EGFR-ADAM17 Axis in Chronic Obstructive Pulmonary Disease and Cystic Fibrosis Lung Pathology by Marta Stolarczyk, Bob J. Scholte

“…Chronic obstructive pulmonary disease (COPD) and cystic fibrosis (CF) share molecular mechanisms that cause the pathological symptoms they have in common. …”
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Evaluating Adult Cystic Fibrosis Care in BC: Disparities in Access to a Multidisciplinary Treatment Centre by James M. Roberts, Pearce G. Wilcox, Bradley S. Quon

“…Background. Cystic fibrosis (CF) care that is delivered through dedicated, multidisciplinary CF clinics is believed to be partly responsible for improvements in the length and quality of life of persons with CF. …”
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Investigation of some anaerobic bacteria in the sputum of cystic fibrosis patients and healthy people in Tehran, Iran by Homa Hamayeli, Ahya Abdi-Ali, Bahareh Attaran, Morvarid Shafiei, Mohammadreza Modaresi

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Central auditory system assessment in children and adolescents with cystic fibrosis: electrophysiology and central auditory processing by Paula Maria Martins-Duarte, Gabriel Hessel, Antônio Fernando Ribeiro, Fernando Augusto Lima Marson, Maria Francisca Colella-Santos

“…Objective: This study aims to evaluate the central auditory system of children and adolescents with cystic fibrosis through behavioral assessment of central auditory processing and electrophysiological tests to investigate short and long-latency auditory potentials, comparing them with the results obtained in the control group. …”
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Association Between Lung Parenchymal Attenuation in Computed Tomography and Airflow Limitation in Adults with Cystic Fibrosis by Lucía Esteban Baloira, Ester Zamarrón de Lucas, Carlos Carpio Segura, Macarena Lerín Baratas, María Fernández Velilla, María Isabel Torres Sánchez, Inmaculada Pinilla Fernández, Pablo Mariscal Aguilar, Rodolfo Álvarez-Sala Walther, Concepción Prados Sánchez

Subjects: “…cystic fibrosis…”
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Adiponectin Expression Is Modulated by Long-Term Physical Activity in Adult Patients Affected by Cystic Fibrosis by Rita Polito, Ersilia Nigro, Ausilia Elce, Maria Ludovica Monaco, Paola Iacotucci, Vincenzo Carnovale, Marika Comegna, Monica Gelzo, Federica Zarrilli, Gaetano Corso, Giuseppe Castaldo, Aurora Daniele

“…Cystic fibrosis (CF) is a genetic disease characterized by progressive decline of lung function and chronic airway inflammation. …”
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The Role of the High-Sensitivity C-Reactive Protein in Patients with Stable Non-Cystic Fibrosis Bronchiectasis by Meng-Heng Hsieh, Yueh-Fu Fang, Guan-Yuan Chen, Fu-Tsai Chung, Yuan-Chang Liu, Cheng-Hsien Wu, Yu-Chen Chang, Horng-Chyuan Lin

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Incidence rate, clinical profile, and outcomes of COVID-19 in adults with non-cystic fibrosis bronchiectasis by Cristiane Christ Camargo, Fernanda de Miranda Schmitz, Letícia Bauer Jacobsen, Bruna Ziegler, Paulo de Tarso Roth Dalcin

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Relevance of 3D Cholangiography and Transient Elastography to Assess Cystic Fibrosis-Associated Liver Disease? by C. Lemaitre, S. Dominique, E. Billoud, M. Eliezer, H. Montialoux, M. Quillard, G. Riachi, E. Koning, H. Morisse-Pradier, G. Savoye, C. Savoye-Collet, O. Goria

“…Background. Cystic fibrosis-associated liver disease (CFLD) is a major cause of death. …”
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Burkholderia Gladioli – A Predictor of Poor Outcome in Cystic Fibrosis Patients Who Receive Lung Transplants?... by Bradley S Quon, James D Reid, Patrick Wong, Pearce G Wilcox, Amin Javer, Jennifer M Wilson, Robert D Levy

“…A case involving a lung transplant recipient with cystic fibrosis who ultimately died as a result of severe rhinosinusitis due to B gladioli infection in the context of postlung transplant immunosuppression is reported.…”
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