Predictors of frequency of CF care in the US Cystic Fibrosis Foundation Patient Registry. by Alexandra C Hinton, Edmund H Sears, Jonathan B Zuckerman, Sara Lopez-Pintado

“…<h4>Introduction</h4>Prolonged gaps in care of >12-months are frequent among people with cystic fibrosis (pwCF) and are associated with reduced lung function. …”
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Serum Hepcidin Level as a Marker of Iron Status in Children with Cystic Fibrosis by Monika Kałużna-Czyż, Urszula Grzybowska-Chlebowczyk, Halina Woś, Sabina Więcek

“…Material and Methods. 46 children with cystic fibrosis and 31 healthy controls were enrolled. …”
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Impact of elexacaftor-tezacaftor-ivacaftor in lung transplantation for cystic fibrosis in the United States by Tahuanty A. Pena, MD, MS, Brittany Wright, PharmD, Kalpaj R. Parekh, MBBS, Julia Kleney-Tait, MD, PhD

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Bacterial interactions underpin worsening lung function in cystic fibrosis-associated infections by Damian W. Rivett, Lauren R. Hatfield, Helen Gavillet, Michelle Hardman, Christopher van der Gast

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Metastatic Bladder Cancer Presenting with Persistent Hematuria in Young Man with Cystic Fibrosis by Premal Patel, Harvey R. Rabin, Michael M. Vickers, Michael D. Parkins

“…We report a case of metastatic bladder cancer developing in a young man with cystic fibrosis (CF) that was initially diagnosed as ureterolithiasis and managed as renal colic. …”
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Scoping review: relationship between glucose tolerance and pulmonary decline in cystic fibrosis by Raina Tomoda, Deborah Jane Holmes-Walker

“… Cystic fibrosis-related diabetes (CFRD) causes deterioration of cystic fibrosis (CF) lung disease, thereby increasing mortality. …”
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Additive Effect of Dornase Alfa and Nacystelyn on Transportability and Viscoelasticity of Cystic Fibrosis Sputum by Feng Sun, Shusheng Tai, Thomas Lim, Ulrich Baumann, Malcolm King

“…OBJECTIVE: To investigate the effect of dornase alfa (DA), Nacystelyn (NAL) and their combination on mucociliary transportability and mucus viscoelasticity of cystic fibrosis (CF) sputum, and to assess whether the combination possesses an additive effect.…”
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Anti-inflammatory and immunomodulating effects of clarithromycin in patients with cystic fibrosis lung disease by Alexander L. Pukhalsky, Galina V. Shmarina, Nikolai I. Kapranov, Svetlana N. Kokarovtseva, Daria Pukhalskaya, Natalia J. Kashirskaja

“…BACKGROUND and aim: Macrolide antibiotics are widely used in the treatment of suppurative lung diseases including cystic fibrosis (CF), the most common inherited fatal disease in the Caucasian population. …”
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Efficacy of melatonin treatment in a cystic fibrosis mouse model of airway infection by Kristen R. Schaefer, Sara Rogers, Zachary Faber, Thomas J. Kelley

“…Abstract Approaches to mitigate the severity of infections and of immune responses are still needed for the treatment of cystic fibrosis (CF) even with the success of highly effective modulator therapies. …”
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Improvement of nutrient absorption may enhance systemic oxidative stress in cystic fibrosis patients by Galina V. Shmarina, Alexander L. Pukhalsky, Svetlana N. Kokarovtseva, Daria A. Pukhalskaya, Elena A. Kalashnikova, Nikolaï I. Kapranov, Natalia J. Kashirskaja

“…Background: The life expectancy of patients with cystic fibrosis (CF) is largely dependent on the pulmonary disease severity and progress. …”
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Spirometry-Related Pain and Distress in Adolescents and Young Adults with Cystic Fibrosis: The Role of Acceptance by Annabelle Casier, Liesbet Goubert, Tine Vervoort, Marleen Theunis, Danielle Huse, Frans De Baets, Dirk Matthys, Geert Crombez

“…OBJECTIVE: To investigate the occurrence of spirometry-related pain and distress in adolescents and young adults with cystic fibrosis (CF), and to investigate the role of acceptance of illness in spirometry-related pain and distress.…”
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Sternum Length and Rib Cage Dimensions Compared with Bodily Proportions in Adults with Cystic Fibrosis by Louis-Philippe Laurin, Vincent Jobin, François Bellemare

“…BACKGROUND: A greater structural expansion of the rib cage in females compared with males has been described in cystic fibrosis (CF) patients; however, conflicting data exist as to whether an elongation of the bony ribs and sternum contributes to this expansion.…”
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Antimicrobial Properties of Mesenchymal Stem Cells: Therapeutic Potential for Cystic Fibrosis Infection, and Treatment by Morgan T. Sutton, David Fletcher, Santosh K. Ghosh, Aaron Weinberg, Rolf van Heeckeren, Sukhmani Kaur, Zhina Sadeghi, Adonis Hijaz, Jane Reese, Hillard M. Lazarus, Donald P. Lennon, Arnold I. Caplan, Tracey L. Bonfield

“…Cystic fibrosis (CF) is a genetic disease in which the battle between pulmonary infection and inflammation becomes the major cause of morbidity and mortality. …”
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Scoliosis Surgery in Cystic Fibrosis: Surgical Considerations and the Multidisciplinary Approach of a Rare Case by George I. Mataliotakis, Athanasios I. Tsirikos, Karen Pearson, Don S. Urquhart, Carolyn Smith, Andrew Fall

“…Spinal deformity in patients with cystic fibrosis (CF) is usually mild requiring no treatment. …”
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The effect of triple CFTR modulator therapy and azithromycin on ion channels and inflammation in cystic fibrosis by Suhad Bani Melhim, Lisa E.J. Douglas, James A. Reihill, Damian G. Downey, S. Lorraine Martin

“…Background Inflammation in cystic fibrosis (CF) airways is difficult to treat with well-established regimens often including azithromycin (AZ) as an immunomodulatory drug. …”
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Evaluation of functional capacity and level of physical activity in adolescent and adult patients with cystic fibrosis by Inaê Cherobin, Paulo Dalcin, Bruna Ziegler

Subjects: “…Cystic Fibrosis…”
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Noninvasive Methods, including Transient Elastography, for the Detection of Liver Disease in Adults with Cystic Fibrosis by Matthew D Sadler, Pam Crotty, Linda Fatovich, Stephanie Wilson, Harvey R Rabin, Robert P Myers

“…BACKGROUND: Liver disease is the third leading cause of mortality in patients with cystic fibrosis (CF). However, detection of CF-associated liver disease (CFLD) is challenging.…”
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Toll Like Receptors 4 and 2 Expression in the Bronchial Mucosa of Patients with Cystic Fibrosis by Hans-Peter Hauber, Meri K Tulic, Anne Tsicopoulos, Benoit Wallaert, Ron Olivenstein, Patrick Daigneault, Qutayba Hamid

“…BACKGROUND: Cystic fibrosis (CF) is a lung disease characterized by chronic infection with Gram-negative bacteria Pseudomonas aeruginosa and Gram-positive bacteria Staphylococcus aureus. …”
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Tools used to measure quality of life in adults with cystic fibrosis– a systematic review by Dorota Snop-Perkowska, Jakub Świtalski, Katarzyna Wnuk, Paweł Olszewski, Anna Augustynowicz

Subjects: “…Cystic fibrosis…”
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Tumor necrosis factor-α/interleukin-10 balance in normal and cystic fibrosis children by Galina V. Shmarina, Alexander L. Pukhalsky, Svetlana N. Kokarovtseva, Daria A. Pukhalskaya, Lidia A. Shabalova, Nikolai I. Kapranov, Natalia J. Kashirskaja

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