Aquagenic Wrinkling of the Palms in a Patient with Cystic Fibrosis by Inês Aparício Martins, Miguel Santos-Coelho, Cândida Fernandes

Subjects: “…Cystic Fibrosis…”
Get full text

Adrenal Insufficiency in Cystic Fibrosis: A Rare Phenomenon? by Sébastien Préville-Ratelle, Adèle Coriati, Aurélie Ménard, Isabelle Bourdeau, François Tremblay, Yves Berthiaume

“…The prevalence of adrenal insufficiency (AI) in cystic fibrosis (CF) is unknown. The frequent use of glucocorticoids (inhaled or systemic) may induce the long-term suppression of the hypothalamic-pituitary-adrenal axis. …”
Get full text

Metabolomic profiling of saliva from cystic fibrosis patients by M. Caterino, M. Costanzo, A. Castaldo, P. Iacotucci, V. Carnovale, M. Ruoppolo, M. Gelzo, G. Castaldo

Subjects: “…Cystic fibrosis…”
Get full text

Catamenial Hemoptysis and Pneumothoraces in a Patient with Cystic Fibrosis by Chris M Parker, Robert Nolan, M Diane Lougheed

“…A 32-year-old woman with cystic fibrosis, who over a period of several months had experienced recurrent catamenial hemoptysis and pneumothoraces, including an episode of life-threatening hemoptysis that coincided with menstruation, is presented. …”
Get full text

The concentration of calprotectin in the stools of children with diagnosed cystic fibrosis by Sabina Więcek, Halina Woś, Bożena Kordys-Darmolińska, Magda Sankiewicz-Szkółka, Urszula Grzybowska-Chlebowczyk

Subjects: “…cystic fibrosis…”
Get full text

Cepacia Syndrome in a Non-Cystic Fibrosis Patient by Naomi Hauser, Jose Orsini

“…The potential for this pathogen to infect non-cystic fibrosis patients is limited and its epidemiology is poorly understood. …”
Get full text

Protease-activated receptor 1 in the pathogenesis of cystic fibrosis by Sarath Ranganathan, Philip Sutton, Sophie Day, Poshmaal Dhar, Kristy Azzopardi, Muhammad A Saeed, Sohinee Sarkar, Jia-Xi Han

“…Background The most common cause of death in those with cystic fibrosis (CF) is respiratory failure due to bronchiectasis resulting from repeated cycles of respiratory infection and inflammation. …”
Get full text

The Role of Serine Proteases and Antiproteases in the Cystic Fibrosis Lung by Matthew S. Twigg, Simon Brockbank, Philip Lowry, S. Peter FitzGerald, Clifford Taggart, Sinéad Weldon

“…Cystic fibrosis (CF) lung disease is an inherited condition with an incidence rate of approximately 1 in 2500 new born babies. …”
Get full text

The Involvement of Glycosaminoglycans in Airway Disease Associated with Cystic Fibrosis by Emer P. Reeves, David A. Bergin, Michelle A. Murray, Noel G. McElvaney

“…Individuals with cystic fibrosis (CF) present with severe airway destruction and extensive bronchiectasis. …”
Get full text

Update of Faecal Markers of Inflammation in Children with Cystic Fibrosis by Jung M. Lee, Steven T. Leach, Tamarah Katz, Andrew S. Day, Adam Jaffe, Chee Y. Ooi

Get full text

Hepatic Abscess due to Burkholderia (Pseudomonas) cepacia in Cystic Fibrosis by Kristin L Fraser, Robert H Hyland, D Elizabeth Tullis

“…Two patients with cystic fibrosis are described who developed hepatic abscesses clue to B cepacia. …”
Get full text

Piperacillin-Induced Immune Hemolytic Anemia in an Adult with Cystic Fibrosis by Mahesh Bandara, David B. Seder, George Garratty, Regina M. Leger, Jonathan B. Zuckerman

“…We report a case of drug-induced immune hemolytic anemia (DIIHA) in an adult female with cystic fibrosis (CF), complicating routine treatment of a pulmonary exacerbation with intravenous piperacillin-tazobactam. …”
Get full text

Exercise Training in Children and Adolescents with Cystic Fibrosis: Theory into Practice by Craig A. Williams, Christian Benden, Daniel Stevens, Thomas Radtke

“…Physical activity and exercise training play an important role in the clinical management of patients with cystic fibrosis (CF). Exercise training is more common and recognized as an essential part of rehabilitation programmes and overall CF care. …”
Get full text

A new era of cystic fibrosis therapy with CFTR modulators by Laura Gomes Boabaid de Barros, Laura Menestrino Prestes, Maria Fernanda Gonçalves Meirelles Fernandes, Luiz Vicente Ribeiro Ferreira da Silva-Filho, Leonardo Araújo Pinto

Get full text

Quantitative ultrasound rating of liver fibrosis in children with cystic fibrosis by G. M. Dvoryakovskaya, O. I. Simonova, S. A. Ivleva, I. V. Dvoryakovsky, A. N. Surkov, M. O. Gorbunova, I. E. Smirnov

Subjects: “…cystic fibrosis in children…”
Get full text

Treatment of Pseudomonas and Staphylococcus Bronchopulmonary Infection in Patients with Cystic Fibrosis by Rashmi Ranjan Das, Sushil Kumar Kabra, Meenu Singh

“…The optimal antibiotic regimen is unclear in management of pulmonary infections due to pseudomonas and staphylococcus in cystic fibrosis (CF). We systematically searched all the published literature that has considered the evidence for antimicrobial therapies in CF till June 2013. …”
Get full text

Celiac Disease in Patients with Cystic Fibrosis-Related Bone Disease by Melissa S. Putman, Alexandra Haagensen, Isabel Neuringer, Leonard Sicilian

“…Both cystic fibrosis (CF) and celiac disease can cause low bone mineral density (BMD) and fractures. …”
Get full text

Extracellular vesicles in sputum of children with cystic fibrosis pulmonary exacerbations by Elad Ben-Meir, Lina Antounians, Shafinaz Eisha, Felix Ratjen, Augusto Zani, Hartmut Grasemann

“…Background The aim of this study was to quantify mediators of neutrophilic inflammation within airway extracellular vesicles (EVs) of children treated for a cystic fibrosis (CF) pulmonary exacerbation (PEx). Methods EVs were isolated from stored sputum samples collected before and after antibiotic therapy for PEx between 2011 and 2013, and characterised by nanoparticle tracking analysis (NTA) and transmission electron microscopy (TEM). …”
Get full text

Cystic Fibrosis and Reproductive Outcomes: The Latest Insights into Fertility and Pregnancy by Weronika Małagocka, Karol Zagórski, Mateusz Kozik, Nina Skalska-Dziobek, Karolina Chybowska, Maria Naruszewicz, Przemysław Cetnarowski

Subjects: “…Cystic fibrosis…”
Get full text

An Unusual Case of Cystic Fibrosis Associated Pneumocystis jiroveci Pneumonia in an Infant by Ravinder Kaur, Priyanka Katariya, Megh Singh Dhakad, Bhanu Mehra, Urmila Jhamb, A. P. Dubey

“…Sweat chloride test for diagnosis of cystic fibrosis was positive. Bronchoalveolar lavage (BAL) fluid was collected and Pseudomonas aeruginosa was isolated on culture. …”
Get full text