Noncirrhotic Extrahepatic Portosystemic Shunt Causing Adult-Onset Encephalopathy Treated with Endovascular Closure by Eldad Elnekave, Eugenia Belenky, Lindsley Van der Veer

“…Lactulose and rifaximin were discontinued, and confusion and ataxia resolved.…”
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Biochemical analysis to study wild-type and polyglutamine-expanded ATXN3 species. by Grégoire Quinet, María Cristina Paz-Cabrera, Raimundo Freire

“…Spinocerebellar ataxia type 3 (SCA3) is a cureless neurodegenerative disease recognized as the most prevalent form of dominantly inherited ataxia worldwide. …”
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Multiple-System Atrophy with Cerebellar Predominance Presenting as Respiratory Insufficiency and Vocal Cords Paralysis by Ramon Andrade Bezerra de Mello, Diana Ferreira, José Manuel Dias da Costa, Maria José Rosas, João Manuel Quinaz

“…MSA (Multiple System Atrophy) may be associated either with Parkinsonism or with cerebellar ataxia (MSA-c subtype). It is considered a rare disease, but many patients are misdiagnosed as suffering from idiopathic Parkinson's disease. …”
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Wernicke’s Encephalopathy: An Unusual Consequence of the Acquired Immune Deficiency Syndrome—Case Report and Literature Review by Timothy R. Larsen, Dritan Dragu, Michael Williams

“…Wernicke’s encephalopathy is a well-described syndrome characterized by the classic triad of confusion, ataxia, and ophthalmoplegia. Wernicke’s encephalopathy results from thiamine (vitamin B1) deficiency. …”
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Acute Disseminated Encephalomyelitis Presenting as Bilateral Ptosis in a Sri Lankan Child by Ishara Kumarasiri, Ruwan Samararathna, Udara Sandakelum, Oshanie Muthukumarana, Reha Balasubramaniam, Sachith Mettananda

“…On examination, he had bilateral ptosis, gait ataxia, and dysmetria. His vision, eye movements, and examination of other cranial nerves were normal. …”
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Unveiling the prenatal features of HADDS: A case report and literature review by Lina Hu, Dongzhi Li, Li Zhen, Yanan Wang

“…Hypotonia, Ataxia, and Delayed Development Syndrome (HADDS), triggered by EBF3 mutations, is a neurodevelopmental disorder syndrome characterized by hypotonia, ataxia, and developmental delay. …”
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Surface Electromyography for the Diagnosis of Tremor Syndrome: A Study of 97 Patients by Kartika Gulati, Sanjay Pandey

“…Conclusions: Synchronous bursts with co-contraction suggestive of DT were observed in most patients with tremor–ataxia syndrome and a small number of patients with ET syndrome. …”
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A Case of John Cunningham Virus Induced Rhombencephalitis after Rituximab Therapy for Idiopathic Thrombocytopenic Purpura by Silpita Katragadda, Varshaa Koneru, Genevieve Devany, Aaron S. DeWitt, Vasudev H. Tati

“…A 73-year-old man presented with ataxia and difficulty in speech which began 3 months after initiation of treatment for idiopathic thrombocytopenic purpura with rituximab. …”
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Clinical Features of Miller-Fisher Syndrome in Pregnancy by Masanori Ono, Hideki Sato, Mayu Shirahashi, Noriko Tomioka, Julia Maeda, Keiko Watanabe, Tomoko Amagata, Toshiyuki Ikeda, Kazumi Yakubo, Tatsuro Fukuiya

“…MFS is a rare disorder that is characterized by the acute onset of ophthalmoplegia, ataxia, and areflexia/hyporeflexia. MFS has a higher incidence in Asia, where the incidence is estimated to be 18%–26% of GBS compared with 3%–5% in the West. …”
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SEDACIÓN Y ANALGESIA CON BOLOS DE XILAZINA Y MORFINA EN INFUSIÓN CONTINUA EN UNA YEGUA CRIOLLA COLOMBIANA SOMETIDA A OVARIOECTOMÍA EN ESTACIÓN by D. A. Zuluaga, D. Duque, J. D. Ruiz, I. Ruiz, T. Escobar, M. C. Ochoa

“…Durante el procedimiento quirúrgico se observó una buena analgesia, sedación moderada y ataxia leve, sin alteraciones cardiovasculares o respiratorias, lo que favoreció el procedimiento quirúrgico; solamente se observó un corto periodo de amotilidad intestinal el cual fue superado espontáneamente. …”
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Gamma knife thalamotomy for essential and Parkinson’s tremor by A. Radžiūnas, O. Laucius, L. Kudrevičius, P. Sėdžius, I. Čelpačenko

“…Main disadvantages include several months of latency period and transient ataxia. …”
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Functional state of the nigrostriatal system of Krushinsky – Molodkina rats during audiogenic seizure expression by N. A. Dorofeeva, L. S. Nikitina, D. V. Zosen, M. V. Glazova, E. V. Chernigovskaya

“…We demonstrated activation of GABA in the substantia nigra pars reticulate, which probably results in the inhibition of glutamate neurons of the thalamus and could be one of the mechanisms inhibiting seizure activity during ataxia.…”
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Recurrent Diplopia in a Pediatric Patient with Bickerstaff Brainstem Encephalitis by Scott A. McLeod, Wallace Wee, Francois D. Jacob, Isabelle Chapados, Francois V. Bolduc

“…Ophthalmoplegia has been reported with acute ataxia in Miller Fisher syndrome (MFS) and Bickerstaff brainstem encephalitis (BBE). …”
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The case of Kinsburn’s Encephalopathy in a child with neuroblastoma of posterior mediastinum by T.I. Stetsenko, H.M. Fedushka, S.O. Rebenkov, T.P. Ivanova

“…Opsoclonus-myoclonus-ataxia syndrome (OMAS) is an autoimmune rare disease of the central nervous system with lesion of the cerebellum and its ligaments. …”
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Prenatal Counseling and Diagnosis of COX20 Gene-Related Mitochondrial Complex IV Deficiency: A Case Report and Literature Review by Su J, Zeng L, Chen H, Tong J, Chen Y, Huang L, Deng L, Huang Y

“…Moreover, this report delineated the process of prenatal counseling and diagnostic testing that was undertaken for the subsequent pregnancy of the patient’s mother.Conclusion: The presence of ataxia, cognitive impairment, and peripheral neuropathy in children should prompt consideration of COX20-related mitochondrial disease. …”
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Long-read sequencing revealed complex biallelic pentanucleotide repeat expansions in RFC1-related Parkinson’s disease by Peng Liu, Fan Zhang, Xinhui Chen, Xiaosheng Zheng, Miao Chen, Zhiru Lin, Shuqi Chen, Lebo Wang, Xinchen Wang, Nan Jin, Chenxin Ying, Fei Xie, Bo Wang, Sheng Wu, Zhidong Cen, Wei Luo

“…Abstract Biallelic intronic pentanucleotide repeat expansions, mainly (AAGGG)exp and/or (ACAGG)exp in RFC1, are detected in cerebellar ataxia, neuropathy and vestibular areflexia syndrome, late-onset ataxia, and in a wide disease spectrum including Charcot-Marie-Tooth disease, multiple system atrophy, and Parkinson’s disease (PD). …”
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Cerebellar lipid dysregulation in SCA3: A comparative study in patients and mice by Alexandra F. Putka, Varshasnata Mohanty, Stephanie M. Cologna, Hayley S. McLoughlin

“…Spinocerebellar ataxia type 3 (SCA3) is the most common dominantly inherited ataxia and belongs to the family of nine diseases caused by a polyglutamine expansion in the disease-causing protein. …”
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Surgical treatment of obstipation due to metabolic bone disease in a Savannah Monitor by Ts. Chaprazov

“…The monitor was pre-sented with a history of ataxia, anorexia and lack of defecation from several months. …”

Enhancing PDAC therapy: Decitabine-olaparib synergy targets KRAS-dependent tumors by Giorgia Anastasio, Michela Felaco, Alessia Lamolinara, Francesco del Pizzo, Elisa Cacciagrano, Carla Mottini, Margherita Mutarelli, Francesca Di Modugno, Manuela Iezzi, Luca Cardone

“…DEC induces DNA damage and activates the ataxia telangiectasia (ATR)/ataxia telangiectasia mutated (ATM)-mediated DNA damage response (DDR), with PARP1-mediated repair playing a key role. …”
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Identifying key signs of motor neurone disease in primary care: a nested case–control study using the QResearch database by Aleksandar Radunović, Carol Coupland, Julia Hippisley-Cox, Christopher J McDermott, Tom A Ranger, Judith Burchardt, Xue W Mei

“…Of these, seven were new to the Red Flag tool: ataxia, dysphasia, weight loss, wheeze, hoarseness of voice, urinary incontinence and constipation. …”
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