Assessing microvascular dysfunction and predicting long-term prognosis in patients with cardiac amyloidosis by cardiovascular magnetic resonance quantitative stress perfusion by Leting Tang, Wenjin Zhao, Kang Li, Lin Tian, Xiaoyue Zhou, Hu Guo, Mu Zeng

Subjects: “…Cardiac amyloidosis…”
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Suspicion, screening, and diagnosis of wild‐type transthyretin amyloid cardiomyopathy: a systematic literature review by Katrine Bay, Finn Gustafsson, Michael Maiborg, Anne Bagger‐Bahnsen, Anne Mette Strand, Trine Pilgaard, Steen Hvitfeldt Poulsen

Subjects: “…Amyloidosis…”
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Pharmacological enhancement of slow-wave activity at an early disease stage improves cognition and reduces amyloid pathology in a mouse model of Alzheimer’s disease by Sedef Kollarik, Sedef Kollarik, Sedef Kollarik, Dorita Bimbiryte, Aakriti Sethi, Inês Dias, Inês Dias, Inês Dias, Carlos G. Moreira, Daniela Noain, Daniela Noain, Daniela Noain, Daniela Noain

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Radiologically Guided Renal Artery Embolization with an Amplatzer Vascular Plug as a Rescue Therapy for Refractory Nephrotic Syndrome in AL-Amyloidosis by I. Spozio Züst, H. R. Räz, F. Burkhalter

“…Nephrotic syndrome is common in immunoglobulin light-chain (AL) amyloidosis and successful therapy may pose a challenge. …”
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Exercise-Stress Echocardiography Reveals Systolic Anterior Motion of the Mitral Valve as a Cause of Syncopes in a Cardiac Amyloidosis Patient by Tor Skibsted Clemmensen, Henning Mølgaard, Niels Frost Andersen, Steen Baerentzen, Steen Hvitfeldt Poulsen

“…Patients with cardiac amyloidosis are at increased AV-block and syncope risk. …”
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Suggestive Diagnostic Process in a Case of Multiple Myeloma with Gastrointestinal Immunoglobulin Light-Chain Amyloidosis Accompanied by Protein-Losing Enteropathy by Katsuya Endo, Takehito Ito, Jun Nomura, Keigo Murakami, Shiho Kondo, Tomonori Satoh, Daisuke Fukushi, Yuki Yoshino, Yoshiteru Sasaki, Atsuko Takasu, Takayuki Kogure, Morihisa Hirota, Takayoshi Meguro, Kazuhiro Murakami, Junichi Kameoka, Kennichi Satoh

“…Multiple myeloma is known to cause immunoglobulin light-chain (AL) amyloidosis, which frequently involves the kidney and heart. …”
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Development of Renal Failure without Proteinuria in a Patient with Monoclonal Gammopathy of Undetermined Significance: An Unusual Presentation of AL Kappa Amyloidosis by Yijuan Sun, Amarpreet Sandhu, Darlene Gabaldon, Jonathan Danaraj, Karen S. Servilla, Antonios H. Tzamaloukas

“…AL amyloidosis complicating monoclonal gammopathy of undetermined significance (MGUS) has usually a predominant glomerular deposition of lambda light chain. …”
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Childhood-onset enthesitis-related arthritis leading to nephrotic syndrome due to secondary amyloidosis complicated by acute pulmonary embolism - The domino effect by Vishal Mangal, Bhaskar Datt, Arun Hegde, A W Kashif, Ankit Kumar, Jaspreet Kaur, Nidhi Goel, Anil Shankar Menon

Subjects: “…amyloidosis…”
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Amorphous Extracellular Eosinophilic Material – The Diagnostic Challenge in Histopathology by P. Sivakumar, P. Rajkumar, S. K. Sridevi, L. Priyadharshini, M. Elancheran

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Amyloidogenic immunoglobulin light chains disturb contractile function and calcium transients in a human cardiac spheroid model of light chain (AL) amyloidosis by Mélanie Bézard, Jean-Sébastien Vartanian-Grimaldi, Julien Henri, Denisa Calin, Amira Zaroui, Mounira Kharoubi, Thibaud Damy, Onnik Agbulut, Ekaterini Kordeli

Subjects: “…AL amyloidosis…”
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Epidemiological perspectives of amyloidosis in Argentina: a cohort study analysing incidence and mortality patterns among a population affiliated to a medical care programme by María Lourdes Posadas-Martínez, Delfina Cirelli, Florencia De Florio, María Adela Aguirre, Elsa Mercedes Nucifora, Patricia Beatriz Sorroche, María Soledad Sáez, Valeria Inés Aliperti, Jimena Vicens, Marcelina Carretero

“…Background Data on the epidemiology of amyloidosis are scarce worldwide, making it difficult to understand its true incidence and mortality.Aim The aim of this study is to estimate the incidence and mortality rate of systemic amyloidosis in people affiliated to a Medical Care Program in the city of Buenos Aires, Argentina.Methods This is a hospital-based prospective study. …”
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Healthcare resource use of patients with transthyretin amyloid cardiomyopathy by Rosa Lauppe, Johan Liseth Hansen, Anna Fornwall, Katarina Johansson, Mark H. Rozenbaum, Anne Mette Strand, Merja Vakevainen, Johanna Kuusisto, Einar Gude, J. Gustav Smith, Finn Gustafsson

Subjects: “…TTR amyloidosis…”
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Unusual hypertrophic cardiomyopathy: case report of an early onset wild-type ATTR amyloidosis accompanied by a chromosomal duplication involving the MYH6 and MYH7 gene by Jassin Hamidi, Yvonne Hanel, Sven Dittmann, Wanda Maria Gerding, Huu Phuc Nguyen, Karin Klingel, Eric Schulze-Bahr

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Gut-Heart Axis: Microbiome Involvement in Restrictive Cardiomyopathies by Samuel Jaimez-Alvarado, Itzel Ivonn López-Tenorio, Javier Barragán-De los Santos, Dannya Coral Bello-Vega, Francisco Javier Roldán Gómez, Amedeo Amedei, Enrique Alexander Berrios-Bárcenas, María Magdalena Aguirre-García

Subjects: “…amyloidosis…”
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Mitral and tricuspid stenosis caused by light chain cardiac amyloid deposition by Varinder K. Randhawa, Sneha Vakamudi, Dermot M. Phelan, Christy J. Samaras, Jesse K. McKenney, Mazen Hanna, Antonio L. Perez

Subjects: “…Light chain cardiac amyloidosis…”
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WALDENSTRÖM MACROGLOBULINEMIA - A STATE-OF-THE-ART REVIEW: PART 1: EPIDEMIOLOGY, PATHOGENESIS, CLINICOPATHOLOGIC CHARACTERISTICS, DIFFERENTIAL DIAGNOSIS, RISK STRATIFICATION, AND C... by Michele Bibas, Shayna Sarosiek, Jorge J. Castillo

Subjects: “…Amyloidosis, Anemia, B cells, BCL2, Bruton tyrosine kinase, Bing-Neel syndrome, Bruton Tyrosine Kinase Inhibitors, Cryoglobulinemia, CXCR4, flow cytometry, hyperviscosity, lymphoplasmacytic lymphoma, MYD88, Waldenström Macroglobulinemia, Peripheral neuropathy.…”
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Treating TNF Receptor Associated Periodic Fever Syndrome in End-Stage Renal Failure by J. Coutinho, R. S. Chorão, M. Oliveira, C. R. Santos

“…Its most severe manifestation is secondary amyloidosis. A 44-year-old male presented with nephrotic syndrome. …”
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Amyloid Goiter Secondary to Ulcerative Colitis by Bunyamin Aydin, Yavuz Savas Koca, Tugba Koca, Ihsan Yildiz, Sevda Gerek Celikden, Metin Ciris

“…AG may be associated with either primary or secondary amyloidosis. Secondary amyloidosis is rarely caused by inflammatory bowel diseases. …”
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A Tongue Lesion as a Sign of a Systemic Disease by Chrysoula I. Liakou, Joan Koh, Antonios Tsimpidakis, Katrina Rios, Charalabos Paskalis, Athanasios Pipilis, Dimitrios Kantianis, Thomas Georgiadis, Evangelia Razis

“…Amyloidosis is the extracellular fibril deposition of a variety of proteins, many of which circulate as plasma ingredients. …”
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Genetic disruption of Blimp-1 drastically augments the antitumor efficacy of BCMA-targeting CAR T cells by Anthony M. Battram, Joan Mañé-Pujol, David F. Moreno, Aina Oliver-Caldés, Judit Carpio, Oriol Cardus, Luis Gerardo Rodríguez-Lobato, Álvaro Urbano-Ispizua, Carlos Fernández de Larrea

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