Open-Label Fosmetpantotenate, a Phosphopantothenate Replacement Therapy in a Single Patient with Atypical PKAN by Yiolanda-Panayiota Christou, George A. Tanteles, Elena Kkolou, Annita Ormiston, Kostas Konstantopoulos, Maria Beconi, Randall D. Marshall, Horacio Plotkin, Kleopas A. Kleopa

“…Pantothenate kinase-associated neurodegeneration (PKAN) is an autosomal recessive disorder with variable onset, rate of progression, and phenotypic expression. Later-onset, more slowly progressive PKAN often presents with neuropsychiatric as well as motor manifestations that include speech difficulties, progressive dystonia, rigidity, and parkinsonism. …”
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Justification on Choosing Screw Pumping Units as Energy Efficient Artificial Lift Technology by D. I. Sidorkin, K. S. Kupavykh

“…According to the research results, it has been revealed that from the point of view of energy efficiency, it is desirable to equip low- and low-yield wells with sucker rod progressive cavity pump units, medium-yield ones – with electric progressive cavity pumps driven by permanent magnet motor, medium- and high-yield wells – with electric progressive cavity pumps or electric submersible pumps driven by permanent magnet motor, depending on the characteristics of the pumpedout oil fluid.…”
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Primary liver lymphoma: review of the literature and clinical case presentation by A. K. Smolyaninova, A. V. Gubkin, Ye. Ye. Zvonkov, Yu. A. Kucheryavy

“…Laboratory tests revealed progressive signs of liver failure at normal level of alpha-fetoprotein and carcino-embryonic antigen; clinical signs included progressive manifestations of liver encephalopathy, skin hemorrhages, severe edema, ascites, pruritis and excoriations. …”
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Bimelic Hirayama Disease: Clinical Dilemma Solved by Imaging by Shalabh Jain, Siddharth Yadav, Swarna Gupta, Ritu Gupta

“…It is characterized by progressive muscular weakness and atrophy of unilateral or asymmetrically bilateral distal upper limbs. …”
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Bone Health in Patients with Multiple Sclerosis by Vit Zikan

“…Multiple sclerosis (MS) is a gait disorder characterized by acute episodes of neurological defects leading to progressive disability. Patients with MS have multiple risk factors for osteoporotic fractures, such as progressive immobilization, long-term glucocorticoids (GCs) treatment or vitamin D deficiency. …”
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Seismic Response Analysis of Jointed Rock Slope under Pulse-Like Ground Motions by Xijun Jia, Yu Zhang, Ziyi Zhang

“…The peak dynamic displacement of the jointed rock slope is about 5–6 cm, but the maximum residual displacement is only 11.3% of the peak dynamic displacement. In the progressive failure process, the displacement first appears at the slope toe, then the fractures in the slope crest are opened, and the rock blocks slide along the bottom surface. …”
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A riboflavin-responsive neuronopathy with unique characteristics: Brown-Vialetto- Van Laere syndrome by Soreya BELARBI, Samira Makri MOKRANE

“…We describe the clinical case of a 14 years-old boy with BVVLS who presented from a young age with progressive sensorineural hearing loss of insidious onset, followed by atrophy of the tongue with fasciculations. …”
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Surgical Management of Thoracic Osteomyelitis due to Escherichia Coli Sepsis by Mark K. Lyons, Maziyar Kalani, Matthew T. Neal, Naresh P. Patel

“…We discuss the neurosurgical evaluation of a patient with a progressive vertebral osteomyelitis and treatment options. …”
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Siltuximab-Related Favorable Clinical Outcome for a Patient Suffering from Idiopathic Multicentric Castleman Disease by Stamatios Chrysochoou, Andreas Kreft, Eberhard Schneider

“…First hospitalized due to unexplained progressive anemia, the patient was readmitted to the hospital 18 months later with suspected lymphoma. …”
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Religious Responses to Agricultural Crises: Exploring the Diverse Patterns in Garut, Indonesia by Asep Shodiqin

“…The findings indicate that while exclusive-protective patterns tend to foster passivity, participatory and progressive patterns encourage community engagement, innovation, and social cohesion. …”
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Genetic Rat Models of Parkinson's Disease by Ryan M. Welchko, Xavier T. Lévêque, Gary L. Dunbar

“…In this paper we focused on the various transgenic rat models of PD in terms of their ability to mimic key symptoms of PD in a progressive manner. In general, we found that most of these models provided useful tools for the early stages of PD, but the development of new transgenic rats that present significant neuropathologic and motoric deficits in a progressive manner that more accurately mimics PD is needed.…”
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Thrombosed Large Distal Posterior Inferior Cerebellar Artery Aneurysm Mimicking an Infratentorial Ependymoma by Peter Yat Ming Woo, Natalie Man Wai Ko, Kwong Yau Chan

“…We report a patient who experienced progressive hemiparesis with magnetic resonance imaging findings suggestive of an infratentorial ependymoma. …”
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Grammaticalization in the Korean Aspectual System by Bishwanath Kumar

“…In Middle Korean, these markers conveyed both resultative and progressive aspects, with -go is- -고 잇- indicating the duration of a resultant state and -eo is- -어 잇- serving broader aspectual functions. …”
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Grammatical aspect in Polish and the perception of event duration by Wojciech Milczarski

“…Earlier research showed that the progressive aspect in Dutch extends duration estimations for short events and shortens the perception of inherently medium and long events. …”
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Glycosaminoglycan Storage Disorders: A Review by Maria Francisca Coutinho, Lúcia Lacerda, Sandra Alves

“…Usually MPS are characterized by a chronic and progressive course, with different degrees of severity. …”
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THE EVOLUTION AND TRANSFORMATION OF POLITICAL IDEOLOGIES AND MOVEMENTS IN NIGERIA: A CASE STUDY OF LABOUR PARTY OF NIGERIA by Toye Manuwa

“…Finally, the paper assesses the impact of the LPN on Nigerian politics and society, and its prospects for the future, considering its role as a voice for the working class, a catalyst for progressive change and a partner for national unity. …”
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Case report of glomerular histiocytosis associated with non-crystalline IgG-kappa paraproteinemia by Aditya Kishore, Susanna A. McRae, David Telio, Monica C. Beaulieu

“…Case presentation Crystal storing histiocytosis (CSH) is a rare form of MGRS that typically deposits in the interstitium but rarely in the glomerulus to cause progressive kidney disease. We report a case of a male with known monoclonal protein and progressive proteinuria, whose biopsy showed glomerular histiocytosis with non-crystallizing IgG kappa inclusions. …”
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A riboflavin-responsive neuronopathy with unique characteristics: Brown-Vialetto- Van Laere syndrome by Soreya BELARBI, Samira Makri MOKRANE

“…We describe the clinical case of a 14 years-old boy with BVVLS who presented from a young age with progressive sensorineural hearing loss of insidious onset, followed by atrophy of the tongue with fasciculations. …”
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Emergency Veno-Arterial Extracorporeal Membrane Oxygenation for Pericardial Decompression Syndrome by Mohamed Laimoud, Patricia Machado, Andrea Rossi Zadra, Mary Maghirang, Ali Alenazy

“…Unfortunately, the patient developed acute progressive thrombocytopenia and bilaterally diffuse subarachnoid hemorrhage after 4 days of ECMO support. …”
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High-Dose Methotrexate for the Treatment of Relapsed Central Nervous System Erdheim-Chester Disease by Prahlad Ho, Carole Smith

“…High-dose methotrexate is effective in controlling rapidly progressive CNS ECD and should be considered as a salvage agent prior to commencement of more definitive treatment.…”
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