Systemic Comorbidity in Children with Cataracts in Nigeria: Advocacy for Rubella Immunization by Roseline Duke, Sidney Oparah, Adedayo Adio, Okon Eyo, Friday Odey

“…Cardiac disease was seen in 26 children (39.9%), followed by delayed milestone in 16 (24.2%), intellectual disability in 14 (21.2%), deafness in 11 (16.7%), epilepsy in 4 (6.1%), and physical handicap in 3 (4.5%) of them. …”
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Association of hearing loss with cognitive function and mental health in Africa: A systematic review by Abdulazeez Ahmed, Fatimah Tsiga-Ahmed, Nafisatu Bello-Muhammad, Abdulrazaq Ajiya, Mustapha Gudaji, Denes Stefler

“…Cohort, case‒control and cross-sectional studies were considered for inclusion if they reported the prevalence of any mental health conditions or levels of cognitive functioning among persons with hearing loss/deafness in comparison to those without hearing loss. …”
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Spontaneous Coronary Artery Dissection: A Rare Manifestation of Alport Syndrome by Amornpol Anuwatworn, Prince Sethi, Kelly Steffen, Orvar Jonsson, Marian Petrasko

“…The resulting disorder includes hereditary nephritis, corneal opacities, anterior lenticonus, fleck retinopathy, temporal retinal thinning, and sensorineural deafness. Aortic and aortic valve pathologies have been described as extrarenal manifestations of AS in multiple case reports. …”
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Quality Analysis of Long dan Xie gan Pill by a Combination of Fingerprint and Multicomponent Quantification with Chemometrics Analysis by Jing Liu, Hui Liu, Zhong Dai, Shuangcheng Ma

“…Long dan Xie gan pill is a traditional complex compound preparation with a long history for treatment of diseases, including hepatocolic hygropyrexia, dizziness, tinnitus, and deafness. Quality of products from different manufacturers may be varied. …”
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Bilateral Congenital Absence of the Stapes Superstructure in Two Siblings by Jose Ignacio Undabeitia, José Undabeitia, Laura Cianci, Luis Padilla, Eduardo Petreñas, Antonio Municio

“…We report the cases of two women, aged 19 and 22 , who presented with a long history of conductive deafness. An exploratory tympanotomy was performed and the absence of the stapes superstructure and an abnormal position of the facial nerve could be observed. …”
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Three MYO15A Mutations Identified in One Chinese Family with Autosomal Recessive Nonsyndromic Hearing Loss by Fengguo Zhang, Lei Xu, Yun Xiao, Jianfeng Li, Xiaohui Bai, Haibo Wang

“…The goal of this research is to explore the genetic cause of a Chinese deafness pedigree who was excluded of GJB2, SLC26A4, or MtDNA12SrRNA variants. …”
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Cochlear Implantation in Charcot-Marie-Tooth Disease: Case Report and Review of the Literature by C. Lane Anzalone, Sarah Nuhanovic, Amy P. Olund, Matthew L. Carlson

“…A 70-year-old male with CMT was referred for evaluation of progressive asymmetric SNHL and reported a 15-year duration of deafness involving the left ear. Audiometric testing confirmed profound SNHL in the left ear, while the right ear exhibited moderate-to-severe SNHL. …”
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Wolfram Syndrome: A Case Report and Review of Clinical Manifestations, Genetics Pathophysiology, and Potential Therapies by N. B. Toppings, J. M. McMillan, P. Y. B. Au, O. Suchowersky, L. E. Donovan

“…A constellation of other features contributes to the acronym DIDMOAD (Diabetes Insipidus, Diabetes Mellitus, Optic Atrophy, and Deafness). This review seeks to raise awareness of this rare form of diabetes so that individuals with WS are identified and provided with appropriate care. …”
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Characterization of post‐ictal clinical signs in dogs with idiopathic epilepsy: A questionnaire‐based study by Aran Nagendran, Julie A. Nettifee, Dani Carter, Karen R. Muñana

“…Groupings of co‐existing PI signs identified included disorientation, blindness and deafness. Conclusion Post‐ictal signs are a commonly reported aspect of seizures in dogs with idiopathic epilepsy, both in focal as well as generalized seizures. …”
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Methicillin-resistant Staphylococcus Aureus Bacteraemia in a Young Boy following Mumps Infection: A Case Report by Jayakanthan Saravanan, AP Krithika, M Geetha

“…Although mumps is considered one of the most innocuous infections, it can also cause serious complications such as meningoencephalitis, pancreatitis, myocarditis, and long-term issues like deafness and multiple cranial nerve palsies. Due to its predominantly benign nature, it has long been a neglected infection. …”
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Mitochondrial Dysfunction and Therapeutic Targets in Auditory Neuropathy by Baoyi Feng, Chenxi Jin, Zhenzhe Cheng, Xingle Zhao, Zhuoer Sun, Xiaofei Zheng, Xiang Li, Tingting Dong, Yong Tao, Hao Wu

“…Sensorineural hearing loss (SNHL) becomes an inevitable worldwide public health issue, and deafness treatment is urgently imperative; yet their current curative therapy is limited. …”
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Transcriptomic Analysis Reveals an Altered Hcy Metabolism in the Stria Vascularis of the Pendred Syndrome Mouse Model by Wenyue Xue, Yuxin Tian, Yuanping Xiong, Feng Liu, Yanmei Feng, Zhengnong Chen, Dongzhen Yu, Shankai Yin

“…Slc26a4-/- mice exhibit severer defects in the development of the cochlea and develop deafness, while the underlying mechanisms responsible for these effects remain unclear. …”
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Impaired network organization in mild age‐related hearing loss by Zhaopeng Tong, Chunhua Xing, Xiaomin Xu, Jin‐Jing Xu, Yuanqing Wu, Richard Salvi, Xindao Yin, Fei Zhao, Yu‐Chen Chen, Yuexin Cai

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A Strategy for Bone Conduction Device Adoption: Study of Non-Usage Challenges, Skin-Deep Insights and Patient Satisfaction by Jasmine Van de Kerkhof, Lore Bleyaert, Nicolas Verhaert, Bob Lerut

“…Complications requiring explantation were rare (3.4%). Single-sided deafness (SSD) and non-SSD patients exhibited similar satisfaction levels, but SSD patients reported higher non-use due to insufficient hearing benefits. …”
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Transcript Profiles of Stria Vascularis in Models of Waardenburg Syndrome by Linjun Chen, Lin Wang, Lei Chen, Fangyuan Wang, Fei Ji, Wei Sun, Hui Zhao, Weiju Han, Shiming Yang

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Efficacy and fibrinogen correlations of defibrinogen therapy in idiopathic sudden sensorineural hearing loss by Bing Wang, Wen Zhang, Jin Zhang, Qimei Yang, Bing Han, Hui Liu, Ziyu Zhao

“…Abstract This study aimed to assess the efficacy of Defibrinogen (DF) therapy in addressing total deafness of idiopathic sudden sensorineural hearing loss (TD-ISSNHL) and investigate the relationship between fibrinogen levels and auditory outcomes. …”
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A Neurophysiological Study of Musical Pitch Identification in Mandarin-Speaking Cochlear Implant Users by Jieqing Cai, Yimeng Liu, Minyun Yao, Muqing Xu, Hongzheng Zhang

“…Music perception in cochlear implant (CI) users is far from satisfactory, not only because of the technological limitations of current CI devices but also due to the neurophysiological alterations that generally accompany deafness. Early behavioral studies revealed that similar mechanisms underlie musical and lexical pitch perception in CI-based electric hearing. …”
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Resolution of unilateral sensorineural hearing loss in a pediatric patient with a severe phenotype of Muckle-Wells syndrome treated with Anakinra: a case report and review of the l... by Cinzia Marchica, Faisal Zawawi, Dania Basodan, Rosie Scuccimarri, Sam J. Daniel

“…Abstract Background Muckle-Wells syndrome (MWS) is a rare auto-inflammatory disease characterized by the presence of recurrent urticaria, deafness and amyloidosis. Progressive sensorineural hearing loss (SNHL) is reported to occur in up to 85% of patients occurring in the second and third decades and as early as the first decade in patients with a more severe phenotype, thus potentially having a significant impact on a child’s development. …”
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Use of Digital Health Interventions for Cancer Prevention Among People Living With Disabilities in the United States: A Scoping Review by Chinenye Lynette Ejezie, Lea Sacca, Sylvia Ayieko, Sara Burgoa, Yasmine Zerrouki, Diana Lobaina, Goodness Okwaraji, Christine Markham

“…The types of disabilities were cancer (n = 4), bipolar I or II disorder (n = 1), obesity (n = 1), and deafness (n = 1). Interventions focused on education (n = 4), screening (n = 3), smoking cessation (n = 3), physical activity (n = 1), and cessation support (n = 1). …”
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Identification of a pathogenic founder variant in the WFS1 gene that causes Wolfram syndrome in the Druze population by Inbal Halabi, Inbal Halabi, Yardena Tenenbaum-Rakover, Yardena Tenenbaum-Rakover, Lena Sagi-Dain, Lena Sagi-Dain, Lena Sagi-Dain, Ilana Koren, Ilana Koren, Ilana Koren

“…It is characterized by central diabetes insipidus, juvenile-onset diabetes mellitus (DM), optic atrophy (OA), and deafness. The natural history of WS is variable, even within the same family and with the same variant.ObjectiveTo report the phenotypes of five patients of Druze origin, all carrying the same autosomal recessive pathogenic variant in the WFS1 gene.Patients & methodsFive patients belonging to three core families were enrolled. …”
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