Bilateral Ocular and Facial with Unilateral Intracranial Involvement In Sturge Weber Syndrome: A Case Report and Review of Literature

The Sturge-Weber syndrome (SWS) is a rare congenital disorder involving the eye in the form of glaucoma and choroidal hemangioma, facial skin in the form of port wine stain, usually in the distribution of ophthalmic division of the trigeminal nerve, and the brain in the form of leptomeningeal angiom...

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Bibliographic Details
Main Authors: Mihika Dube, Rashmi Kujur, Swati Prajapati
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2017-04-01
Series:Delhi Journal of Ophthalmology
Subjects:
Online Access:https://journals.lww.com/10.7869/djo.311
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Summary:The Sturge-Weber syndrome (SWS) is a rare congenital disorder involving the eye in the form of glaucoma and choroidal hemangioma, facial skin in the form of port wine stain, usually in the distribution of ophthalmic division of the trigeminal nerve, and the brain in the form of leptomeningeal angiomas. We report a rare case of 6 year-old girl with Sturge-Weber syndrome with bilateral port wine stain involving the ophthalmic and maxillary division of trigeminal nerve, unilateral intracranial involvement, bilateral glaucoma and abnormal retinal vasculature, without the presence of choroidal hemangioma.
ISSN:0972-0200
2454-2784