Lactulose to the Rescue: A Case of Toxic Hepatic Encephalopathy Caused by Portosystemic Shunting and Epistaxis in a Patient with Hereditary Hemorrhagic Telangiectasia

Hereditary hemorrhagic telangiectasia (HHT) is an uncommon autosomal dominant disorder characterized by telangiectasias and arteriovenous malformations. Multiple organ systems are involved including the skin, lungs, gastrointestinal tract, and brain. Hepatic encephalopathy is an extremely rare compl...

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Main Authors: Ruchit N. Shah, Michael Makar, Nasir Akhtar, Erin Forster
Format: Article
Language:English
Published: Wiley 2019-01-01
Series:Case Reports in Hepatology
Online Access:http://dx.doi.org/10.1155/2019/7573408
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author Ruchit N. Shah
Michael Makar
Nasir Akhtar
Erin Forster
author_facet Ruchit N. Shah
Michael Makar
Nasir Akhtar
Erin Forster
author_sort Ruchit N. Shah
collection DOAJ
description Hereditary hemorrhagic telangiectasia (HHT) is an uncommon autosomal dominant disorder characterized by telangiectasias and arteriovenous malformations. Multiple organ systems are involved including the skin, lungs, gastrointestinal tract, and brain. Hepatic encephalopathy is an extremely rare complication of HHT and early diagnosis and treatment can be life-saving. We present a rare case of hepatic encephalopathy caused by HHT-induced portosystemic shunting treated with lactulose.
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issn 2090-6587
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publishDate 2019-01-01
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series Case Reports in Hepatology
spelling doaj-art-fd90ca0c270f4388bdc45883e827b4932025-02-03T06:11:27ZengWileyCase Reports in Hepatology2090-65872090-65952019-01-01201910.1155/2019/75734087573408Lactulose to the Rescue: A Case of Toxic Hepatic Encephalopathy Caused by Portosystemic Shunting and Epistaxis in a Patient with Hereditary Hemorrhagic TelangiectasiaRuchit N. Shah0Michael Makar1Nasir Akhtar2Erin Forster3Geisinger Medical Center, Department of Internal Medicine, 100 N Academy Ave, Danville, PA 17822, USAGeisinger Commonwealth School of Medicine, 525 Pine Street, Scranton, PA 18510, USAGeisinger Medical Center, Department of Gastroenterology, 100 N Academy Ave, Danville, PA 17822, USAGeisinger Medical Center, Department of Gastroenterology, 100 N Academy Ave, Danville, PA 17822, USAHereditary hemorrhagic telangiectasia (HHT) is an uncommon autosomal dominant disorder characterized by telangiectasias and arteriovenous malformations. Multiple organ systems are involved including the skin, lungs, gastrointestinal tract, and brain. Hepatic encephalopathy is an extremely rare complication of HHT and early diagnosis and treatment can be life-saving. We present a rare case of hepatic encephalopathy caused by HHT-induced portosystemic shunting treated with lactulose.http://dx.doi.org/10.1155/2019/7573408
spellingShingle Ruchit N. Shah
Michael Makar
Nasir Akhtar
Erin Forster
Lactulose to the Rescue: A Case of Toxic Hepatic Encephalopathy Caused by Portosystemic Shunting and Epistaxis in a Patient with Hereditary Hemorrhagic Telangiectasia
Case Reports in Hepatology
title Lactulose to the Rescue: A Case of Toxic Hepatic Encephalopathy Caused by Portosystemic Shunting and Epistaxis in a Patient with Hereditary Hemorrhagic Telangiectasia
title_full Lactulose to the Rescue: A Case of Toxic Hepatic Encephalopathy Caused by Portosystemic Shunting and Epistaxis in a Patient with Hereditary Hemorrhagic Telangiectasia
title_fullStr Lactulose to the Rescue: A Case of Toxic Hepatic Encephalopathy Caused by Portosystemic Shunting and Epistaxis in a Patient with Hereditary Hemorrhagic Telangiectasia
title_full_unstemmed Lactulose to the Rescue: A Case of Toxic Hepatic Encephalopathy Caused by Portosystemic Shunting and Epistaxis in a Patient with Hereditary Hemorrhagic Telangiectasia
title_short Lactulose to the Rescue: A Case of Toxic Hepatic Encephalopathy Caused by Portosystemic Shunting and Epistaxis in a Patient with Hereditary Hemorrhagic Telangiectasia
title_sort lactulose to the rescue a case of toxic hepatic encephalopathy caused by portosystemic shunting and epistaxis in a patient with hereditary hemorrhagic telangiectasia
url http://dx.doi.org/10.1155/2019/7573408
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