Familial Mediterranean Fever Complicated by a Triad of Adrenal Crisis: Amyloid Goiter and Cardiac Amyloidosis
Background. FMF is a common disease in the Mediterranean populations and may be complicated by AA amyloidosis. The coexistence of adrenal and thyroid amyloidosis in AA amyloidosis secondary to familial Mediterranean fever (FMF) is an extremely rare reported condition. We presented a previously unrep...
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| Format: | Article |
| Language: | English |
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Wiley
2020-01-01
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| Series: | Case Reports in Rheumatology |
| Online Access: | http://dx.doi.org/10.1155/2020/7865291 |
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| author | Sadi A. Abukhalaf Beesan W. Dandis Tasnim Za’tari Adham M. Amro Tareq Z. Alzughayyar Yazan A. Rajabi |
| author_facet | Sadi A. Abukhalaf Beesan W. Dandis Tasnim Za’tari Adham M. Amro Tareq Z. Alzughayyar Yazan A. Rajabi |
| author_sort | Sadi A. Abukhalaf |
| collection | DOAJ |
| description | Background. FMF is a common disease in the Mediterranean populations and may be complicated by AA amyloidosis. The coexistence of adrenal and thyroid amyloidosis in AA amyloidosis secondary to familial Mediterranean fever (FMF) is an extremely rare reported condition. We presented a previously unreported triad of adrenal, thyroid, and cardiac amyloidosis secondary to FMF. Presentation of Case. We reported a 23-year-old Palestinian male patient presented with hypotension, vomiting, diarrhea, and abdominal pain. The patient was subsequently diagnosed to have an adrenal crisis with both amyloid goiter and cardiac amyloidosis. Conclusion. It is crucial to recognize the adrenal crisis in patients with AA amyloidosis secondary to FMF who present similarly to acute FMF inflammatory episodes. The adrenal crisis has high morbidity and mortality, especially if not recognized early in the course of the disease. |
| format | Article |
| id | doaj-art-fd297ad94d294f779772e3713aa0a469 |
| institution | Kabale University |
| issn | 2090-6889 2090-6897 |
| language | English |
| publishDate | 2020-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Rheumatology |
| spelling | doaj-art-fd297ad94d294f779772e3713aa0a4692025-02-03T00:59:44ZengWileyCase Reports in Rheumatology2090-68892090-68972020-01-01202010.1155/2020/78652917865291Familial Mediterranean Fever Complicated by a Triad of Adrenal Crisis: Amyloid Goiter and Cardiac AmyloidosisSadi A. Abukhalaf0Beesan W. Dandis1Tasnim Za’tari2Adham M. Amro3Tareq Z. Alzughayyar4Yazan A. Rajabi5Al-Quds University Faculty of Medicine, Jerusalem, Palestine, IsraelAl-Quds University Faculty of Medicine, Jerusalem, Palestine, IsraelAl-Quds University Faculty of Medicine, Jerusalem, Palestine, IsraelMedicine Department, Ahli Hospital, Hebron, Palestine, IsraelMedicine Department, Ahli Hospital, Hebron, Palestine, IsraelMedicine Department, Ahli Hospital, Hebron, Palestine, IsraelBackground. FMF is a common disease in the Mediterranean populations and may be complicated by AA amyloidosis. The coexistence of adrenal and thyroid amyloidosis in AA amyloidosis secondary to familial Mediterranean fever (FMF) is an extremely rare reported condition. We presented a previously unreported triad of adrenal, thyroid, and cardiac amyloidosis secondary to FMF. Presentation of Case. We reported a 23-year-old Palestinian male patient presented with hypotension, vomiting, diarrhea, and abdominal pain. The patient was subsequently diagnosed to have an adrenal crisis with both amyloid goiter and cardiac amyloidosis. Conclusion. It is crucial to recognize the adrenal crisis in patients with AA amyloidosis secondary to FMF who present similarly to acute FMF inflammatory episodes. The adrenal crisis has high morbidity and mortality, especially if not recognized early in the course of the disease.http://dx.doi.org/10.1155/2020/7865291 |
| spellingShingle | Sadi A. Abukhalaf Beesan W. Dandis Tasnim Za’tari Adham M. Amro Tareq Z. Alzughayyar Yazan A. Rajabi Familial Mediterranean Fever Complicated by a Triad of Adrenal Crisis: Amyloid Goiter and Cardiac Amyloidosis Case Reports in Rheumatology |
| title | Familial Mediterranean Fever Complicated by a Triad of Adrenal Crisis: Amyloid Goiter and Cardiac Amyloidosis |
| title_full | Familial Mediterranean Fever Complicated by a Triad of Adrenal Crisis: Amyloid Goiter and Cardiac Amyloidosis |
| title_fullStr | Familial Mediterranean Fever Complicated by a Triad of Adrenal Crisis: Amyloid Goiter and Cardiac Amyloidosis |
| title_full_unstemmed | Familial Mediterranean Fever Complicated by a Triad of Adrenal Crisis: Amyloid Goiter and Cardiac Amyloidosis |
| title_short | Familial Mediterranean Fever Complicated by a Triad of Adrenal Crisis: Amyloid Goiter and Cardiac Amyloidosis |
| title_sort | familial mediterranean fever complicated by a triad of adrenal crisis amyloid goiter and cardiac amyloidosis |
| url | http://dx.doi.org/10.1155/2020/7865291 |
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