Granulomatosis with Polyangiitis with Myocarditis and Ventricular Tachycardia
Granulomatosis with polyangiitis (GPA), previously known as Wegener’s granulomatosis, is a pulmonary-renal syndrome affecting small and medium sized blood vessels. The disease has a prevalence in studies ranging from 3 to 15.7 cases per 100,000, with a noted increasing incidence and prevalence in mo...
Saved in:
Main Authors: | , , |
---|---|
Format: | Article |
Language: | English |
Published: |
Wiley
2017-01-01
|
Series: | Case Reports in Medicine |
Online Access: | http://dx.doi.org/10.1155/2017/6501738 |
Tags: |
Add Tag
No Tags, Be the first to tag this record!
|
_version_ | 1832563397424578560 |
---|---|
author | Ramy Magdy Hanna Eduardo Lopez James Wilson |
author_facet | Ramy Magdy Hanna Eduardo Lopez James Wilson |
author_sort | Ramy Magdy Hanna |
collection | DOAJ |
description | Granulomatosis with polyangiitis (GPA), previously known as Wegener’s granulomatosis, is a pulmonary-renal syndrome affecting small and medium sized blood vessels. The disease has a prevalence in studies ranging from 3 to 15.7 cases per 100,000, with a noted increasing incidence and prevalence in more recent studies. Pulmonary manifestations include hemorrhage, lung cavitary lesions, and pulmonary fibrosis. Within the kidney, GPA is known to cause rapidly progressive pauci-immune crescentic glomerulonephritis. Rare and severe cardiovascular manifestations include pericarditis, arrhythmias, myocarditis, and aortic valve disease. Our patient is a 43-year-old female with typical pulmonary and renal lesions from GPA and also acute myocarditis, multiple episodes of ventricular tachycardia, and a severe reactive thrombocytosis. |
format | Article |
id | doaj-art-fb6c377babb24361a96d7305143043df |
institution | Kabale University |
issn | 1687-9627 1687-9635 |
language | English |
publishDate | 2017-01-01 |
publisher | Wiley |
record_format | Article |
series | Case Reports in Medicine |
spelling | doaj-art-fb6c377babb24361a96d7305143043df2025-02-03T01:20:22ZengWileyCase Reports in Medicine1687-96271687-96352017-01-01201710.1155/2017/65017386501738Granulomatosis with Polyangiitis with Myocarditis and Ventricular TachycardiaRamy Magdy Hanna0Eduardo Lopez1James Wilson2Division of Nephrology, Department of Medicine, David Geffen School of Medicine, Los Angeles, CA, USADivision of Nephrology, Department of Medicine, Kaiser Permanente Medical Center, Panorama City, Los Angeles, CA, USASurgical Consultative Nephrology, UCLA Stone Center, Los Angeles, CA, USAGranulomatosis with polyangiitis (GPA), previously known as Wegener’s granulomatosis, is a pulmonary-renal syndrome affecting small and medium sized blood vessels. The disease has a prevalence in studies ranging from 3 to 15.7 cases per 100,000, with a noted increasing incidence and prevalence in more recent studies. Pulmonary manifestations include hemorrhage, lung cavitary lesions, and pulmonary fibrosis. Within the kidney, GPA is known to cause rapidly progressive pauci-immune crescentic glomerulonephritis. Rare and severe cardiovascular manifestations include pericarditis, arrhythmias, myocarditis, and aortic valve disease. Our patient is a 43-year-old female with typical pulmonary and renal lesions from GPA and also acute myocarditis, multiple episodes of ventricular tachycardia, and a severe reactive thrombocytosis.http://dx.doi.org/10.1155/2017/6501738 |
spellingShingle | Ramy Magdy Hanna Eduardo Lopez James Wilson Granulomatosis with Polyangiitis with Myocarditis and Ventricular Tachycardia Case Reports in Medicine |
title | Granulomatosis with Polyangiitis with Myocarditis and Ventricular Tachycardia |
title_full | Granulomatosis with Polyangiitis with Myocarditis and Ventricular Tachycardia |
title_fullStr | Granulomatosis with Polyangiitis with Myocarditis and Ventricular Tachycardia |
title_full_unstemmed | Granulomatosis with Polyangiitis with Myocarditis and Ventricular Tachycardia |
title_short | Granulomatosis with Polyangiitis with Myocarditis and Ventricular Tachycardia |
title_sort | granulomatosis with polyangiitis with myocarditis and ventricular tachycardia |
url | http://dx.doi.org/10.1155/2017/6501738 |
work_keys_str_mv | AT ramymagdyhanna granulomatosiswithpolyangiitiswithmyocarditisandventriculartachycardia AT eduardolopez granulomatosiswithpolyangiitiswithmyocarditisandventriculartachycardia AT jameswilson granulomatosiswithpolyangiitiswithmyocarditisandventriculartachycardia |