Pseudoporphyria Associated with Nonhemodialyzed Renal Insufficiency, Successfully Treated with Oral N-Acetylcysteine
Pseudoporphyria (PP) is a relatively rare, photodistributed bullous dermatosis that resembles porphyria cutanea tarda (PCT), but it is not accompanied by porphyrin abnormalities in the serum, urine, or stool. It was initially described in renal failure patients on dialysis. Thereafter, it has been...
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| Format: | Article |
| Language: | English |
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Wiley
2013-01-01
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| Series: | Case Reports in Dermatological Medicine |
| Online Access: | http://dx.doi.org/10.1155/2013/271873 |
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| author | A. C. Katoulis D. Ferra E. Toumbis E. Papadavid A. Kanelleas I. Panayiotides D. Rigopoulos |
| author_facet | A. C. Katoulis D. Ferra E. Toumbis E. Papadavid A. Kanelleas I. Panayiotides D. Rigopoulos |
| author_sort | A. C. Katoulis |
| collection | DOAJ |
| description | Pseudoporphyria (PP) is a relatively rare, photodistributed bullous dermatosis that resembles porphyria cutanea tarda (PCT), but it is not accompanied by porphyrin abnormalities in the serum, urine, or stool. It was initially described in renal failure patients on dialysis. Thereafter, it has been associated with several aetiological factors. We report a case of PP in a 67-year-old woman with mild renal failure, successfully treated with N-acetylcysteine. This is the second reported case of PP developing in nondialyzed chronic renal failure. Such cases support the view that renal impairment itself may play a more important aetiological role in developing PP than it was originally considered. |
| format | Article |
| id | doaj-art-f9829cdc1ca344509ef54502d9a5e2cf |
| institution | Kabale University |
| issn | 2090-6463 2090-6471 |
| language | English |
| publishDate | 2013-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Dermatological Medicine |
| spelling | doaj-art-f9829cdc1ca344509ef54502d9a5e2cf2025-02-03T01:20:24ZengWileyCase Reports in Dermatological Medicine2090-64632090-64712013-01-01201310.1155/2013/271873271873Pseudoporphyria Associated with Nonhemodialyzed Renal Insufficiency, Successfully Treated with Oral N-AcetylcysteineA. C. Katoulis0D. Ferra1E. Toumbis2E. Papadavid3A. Kanelleas4I. Panayiotides5D. Rigopoulos6Second Department of Dermatology, “Attikon” General University Hospital, University of Athens, 1 Rimini Street, 124 62 Chaidari, GreeceSecond Department of Dermatology, “Attikon” General University Hospital, University of Athens, 1 Rimini Street, 124 62 Chaidari, GreeceSecond Department of Dermatology, “Attikon” General University Hospital, University of Athens, 1 Rimini Street, 124 62 Chaidari, GreeceSecond Department of Dermatology, “Attikon” General University Hospital, University of Athens, 1 Rimini Street, 124 62 Chaidari, GreeceSecond Department of Dermatology, “Attikon” General University Hospital, University of Athens, 1 Rimini Street, 124 62 Chaidari, GreeceHistopathology Department, “Attikon” General University Hospital, University of Athens, 124 62 Chaidari, GreeceSecond Department of Dermatology, “Attikon” General University Hospital, University of Athens, 1 Rimini Street, 124 62 Chaidari, GreecePseudoporphyria (PP) is a relatively rare, photodistributed bullous dermatosis that resembles porphyria cutanea tarda (PCT), but it is not accompanied by porphyrin abnormalities in the serum, urine, or stool. It was initially described in renal failure patients on dialysis. Thereafter, it has been associated with several aetiological factors. We report a case of PP in a 67-year-old woman with mild renal failure, successfully treated with N-acetylcysteine. This is the second reported case of PP developing in nondialyzed chronic renal failure. Such cases support the view that renal impairment itself may play a more important aetiological role in developing PP than it was originally considered.http://dx.doi.org/10.1155/2013/271873 |
| spellingShingle | A. C. Katoulis D. Ferra E. Toumbis E. Papadavid A. Kanelleas I. Panayiotides D. Rigopoulos Pseudoporphyria Associated with Nonhemodialyzed Renal Insufficiency, Successfully Treated with Oral N-Acetylcysteine Case Reports in Dermatological Medicine |
| title | Pseudoporphyria Associated with Nonhemodialyzed Renal Insufficiency, Successfully Treated with Oral N-Acetylcysteine |
| title_full | Pseudoporphyria Associated with Nonhemodialyzed Renal Insufficiency, Successfully Treated with Oral N-Acetylcysteine |
| title_fullStr | Pseudoporphyria Associated with Nonhemodialyzed Renal Insufficiency, Successfully Treated with Oral N-Acetylcysteine |
| title_full_unstemmed | Pseudoporphyria Associated with Nonhemodialyzed Renal Insufficiency, Successfully Treated with Oral N-Acetylcysteine |
| title_short | Pseudoporphyria Associated with Nonhemodialyzed Renal Insufficiency, Successfully Treated with Oral N-Acetylcysteine |
| title_sort | pseudoporphyria associated with nonhemodialyzed renal insufficiency successfully treated with oral n acetylcysteine |
| url | http://dx.doi.org/10.1155/2013/271873 |
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