Sporadic, Nontrauma-Related, Desmoid Tumor of the Pancreas: A Rare Disease—Case Report and Literature Review
Desmoid tumors (DTs) are neoplasms of fibroblastic origin characterized by lack of a capsule. They are nonmetastatic and locally aggressive. Intraabdominal DTs are often observed in familial adenomatous polyposis and Gardner syndrome or subsequent to localized traumatic injury. Sporadic forms are de...
Saved in:
| Main Authors: | , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Wiley
2010-01-01
|
| Series: | Case Reports in Medicine |
| Online Access: | http://dx.doi.org/10.1155/2010/272760 |
| Tags: |
Add Tag
No Tags, Be the first to tag this record!
|
| _version_ | 1832556514037989376 |
|---|---|
| author | F. Polistina G. Costantin E. D'Amore G. Ambrosino |
| author_facet | F. Polistina G. Costantin E. D'Amore G. Ambrosino |
| author_sort | F. Polistina |
| collection | DOAJ |
| description | Desmoid tumors (DTs) are neoplasms of fibroblastic origin characterized by lack of a capsule. They are nonmetastatic and locally aggressive. Intraabdominal DTs are often observed in familial adenomatous polyposis and Gardner syndrome or subsequent to localized traumatic injury. Sporadic forms are defined as nontrauma- or nongenetic-related DTs. Isolated, sporadic pancreatic DTs have been considered anecdotal, with only 9 cases described in the literature. We report the case of a 68-year-old man with a case of sporadic cystic DT localized to the pancreatic tail. The tumor was discovered incidentally during computerized tomography performed for an unrelated condition. The patient was asymptomatic; however, biopsy was performed on the clinical suspicion of cystic cancer of the pancreas. Pathology analysis showed fibroblastic proliferation, and the diagnosis of DT was confirmed by immunohistochemical staining for beta-catenin. The patient underwent resection with no further treatment and remain disease-free 60 months after surgery. |
| format | Article |
| id | doaj-art-f427d02d0e8440f78d1958ca82ce4f97 |
| institution | Kabale University |
| issn | 1687-9627 1687-9635 |
| language | English |
| publishDate | 2010-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Medicine |
| spelling | doaj-art-f427d02d0e8440f78d1958ca82ce4f972025-02-03T05:45:17ZengWileyCase Reports in Medicine1687-96271687-96352010-01-01201010.1155/2010/272760272760Sporadic, Nontrauma-Related, Desmoid Tumor of the Pancreas: A Rare Disease—Case Report and Literature ReviewF. Polistina0G. Costantin1E. D'Amore2G. Ambrosino3Emergency and Trauma Department, Dolo Hospital, Dolo, 30031 Venice, ItalyDepartment of General Surgery, San Bortolo Hospital, 36100 Vicenza, ItalyDepartment of Human Pathology, San Bortolo Hospital, 36100 Vicenza, ItalySchool of General Surgery, University of Padua, 35128 Padua, ItalyDesmoid tumors (DTs) are neoplasms of fibroblastic origin characterized by lack of a capsule. They are nonmetastatic and locally aggressive. Intraabdominal DTs are often observed in familial adenomatous polyposis and Gardner syndrome or subsequent to localized traumatic injury. Sporadic forms are defined as nontrauma- or nongenetic-related DTs. Isolated, sporadic pancreatic DTs have been considered anecdotal, with only 9 cases described in the literature. We report the case of a 68-year-old man with a case of sporadic cystic DT localized to the pancreatic tail. The tumor was discovered incidentally during computerized tomography performed for an unrelated condition. The patient was asymptomatic; however, biopsy was performed on the clinical suspicion of cystic cancer of the pancreas. Pathology analysis showed fibroblastic proliferation, and the diagnosis of DT was confirmed by immunohistochemical staining for beta-catenin. The patient underwent resection with no further treatment and remain disease-free 60 months after surgery.http://dx.doi.org/10.1155/2010/272760 |
| spellingShingle | F. Polistina G. Costantin E. D'Amore G. Ambrosino Sporadic, Nontrauma-Related, Desmoid Tumor of the Pancreas: A Rare Disease—Case Report and Literature Review Case Reports in Medicine |
| title | Sporadic, Nontrauma-Related, Desmoid Tumor of the Pancreas: A Rare Disease—Case Report and Literature Review |
| title_full | Sporadic, Nontrauma-Related, Desmoid Tumor of the Pancreas: A Rare Disease—Case Report and Literature Review |
| title_fullStr | Sporadic, Nontrauma-Related, Desmoid Tumor of the Pancreas: A Rare Disease—Case Report and Literature Review |
| title_full_unstemmed | Sporadic, Nontrauma-Related, Desmoid Tumor of the Pancreas: A Rare Disease—Case Report and Literature Review |
| title_short | Sporadic, Nontrauma-Related, Desmoid Tumor of the Pancreas: A Rare Disease—Case Report and Literature Review |
| title_sort | sporadic nontrauma related desmoid tumor of the pancreas a rare disease case report and literature review |
| url | http://dx.doi.org/10.1155/2010/272760 |
| work_keys_str_mv | AT fpolistina sporadicnontraumarelateddesmoidtumorofthepancreasararediseasecasereportandliteraturereview AT gcostantin sporadicnontraumarelateddesmoidtumorofthepancreasararediseasecasereportandliteraturereview AT edamore sporadicnontraumarelateddesmoidtumorofthepancreasararediseasecasereportandliteraturereview AT gambrosino sporadicnontraumarelateddesmoidtumorofthepancreasararediseasecasereportandliteraturereview |