Unilateral Eyelid Edema as Initial Sign of Orbital Sarcoidosis

Introduction. Sarcoidosis is a rare multisystemic granulomatous inflammatory disease of unknown etiology affecting the respiratory system, skin, and eyes. Sarcoidosis outside the lacrimal gland is rare. The case study concerns a patient with a final diagnosis of orbital sarcoidosis. Case Report. A 3...

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Main Authors: Sílvia Miguéis Picado Petrarolha, Bruna Suda Rodrigues, Flávio David Haddad Filho, Rogério Aparecido Dedivitis, Samuel Brunini Petrarolha, Pedro Martins Tavares Scianni Morais
Format: Article
Language:English
Published: Wiley 2016-01-01
Series:Case Reports in Ophthalmological Medicine
Online Access:http://dx.doi.org/10.1155/2016/6912927
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author Sílvia Miguéis Picado Petrarolha
Bruna Suda Rodrigues
Flávio David Haddad Filho
Rogério Aparecido Dedivitis
Samuel Brunini Petrarolha
Pedro Martins Tavares Scianni Morais
author_facet Sílvia Miguéis Picado Petrarolha
Bruna Suda Rodrigues
Flávio David Haddad Filho
Rogério Aparecido Dedivitis
Samuel Brunini Petrarolha
Pedro Martins Tavares Scianni Morais
author_sort Sílvia Miguéis Picado Petrarolha
collection DOAJ
description Introduction. Sarcoidosis is a rare multisystemic granulomatous inflammatory disease of unknown etiology affecting the respiratory system, skin, and eyes. Sarcoidosis outside the lacrimal gland is rare. The case study concerns a patient with a final diagnosis of orbital sarcoidosis. Case Report. A 37-year-old male patient went to the ophthalmic emergency room complaining of pain in the left eye, diplopia, and decreased visual acuity. An external eye examination showed hard and cold edema of the lower eyelid, ocular motility with limitation of adduction, and discreet ipsilateral proptosis. Magnetic resonance of the orbit showed left eye proptosis and thickening and increase of soft tissues associated with heterogeneous impregnation of contrast in the infralateral region of the left eyelid. A biopsy of the lesion showed a chronic inflammatory process, with numerous compact nonnecrotizing granulomas surrounded by lamellar hyaline collagen, providing histological confirmation of sarcoidosis. Discussion. A biopsy of the orbital tumor is essential for the diagnosis of sarcoidosis, in addition to the search for systemic findings such as hilar adenopathy or parenchymal lung disease found in 90% of patients.
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spelling doaj-art-f318ba0099944f519023d77308337d272025-02-03T01:12:12ZengWileyCase Reports in Ophthalmological Medicine2090-67222090-67302016-01-01201610.1155/2016/69129276912927Unilateral Eyelid Edema as Initial Sign of Orbital SarcoidosisSílvia Miguéis Picado Petrarolha0Bruna Suda Rodrigues1Flávio David Haddad Filho2Rogério Aparecido Dedivitis3Samuel Brunini Petrarolha4Pedro Martins Tavares Scianni Morais5Department of Head and Neck Surgery, Hospital Ana Costa, 11050-120 Santos, SP, BrazilUniversidade Metropolitana de Santos (UNIMES), 11050-120 Santos, SP, BrazilUniversidade Metropolitana de Santos (UNIMES), 11050-120 Santos, SP, BrazilDepartment of Head and Neck Surgery, Hospital das Clínicas, University of São Paulo School of Medicine, São Paulo, SP, BrazilDepartment of Ophthalmology, Hospital Ana Costa, 11050-120 Santos, SP, BrazilDepartment of Ophthalmology, Hospital Ana Costa, 11050-120 Santos, SP, BrazilIntroduction. Sarcoidosis is a rare multisystemic granulomatous inflammatory disease of unknown etiology affecting the respiratory system, skin, and eyes. Sarcoidosis outside the lacrimal gland is rare. The case study concerns a patient with a final diagnosis of orbital sarcoidosis. Case Report. A 37-year-old male patient went to the ophthalmic emergency room complaining of pain in the left eye, diplopia, and decreased visual acuity. An external eye examination showed hard and cold edema of the lower eyelid, ocular motility with limitation of adduction, and discreet ipsilateral proptosis. Magnetic resonance of the orbit showed left eye proptosis and thickening and increase of soft tissues associated with heterogeneous impregnation of contrast in the infralateral region of the left eyelid. A biopsy of the lesion showed a chronic inflammatory process, with numerous compact nonnecrotizing granulomas surrounded by lamellar hyaline collagen, providing histological confirmation of sarcoidosis. Discussion. A biopsy of the orbital tumor is essential for the diagnosis of sarcoidosis, in addition to the search for systemic findings such as hilar adenopathy or parenchymal lung disease found in 90% of patients.http://dx.doi.org/10.1155/2016/6912927
spellingShingle Sílvia Miguéis Picado Petrarolha
Bruna Suda Rodrigues
Flávio David Haddad Filho
Rogério Aparecido Dedivitis
Samuel Brunini Petrarolha
Pedro Martins Tavares Scianni Morais
Unilateral Eyelid Edema as Initial Sign of Orbital Sarcoidosis
Case Reports in Ophthalmological Medicine
title Unilateral Eyelid Edema as Initial Sign of Orbital Sarcoidosis
title_full Unilateral Eyelid Edema as Initial Sign of Orbital Sarcoidosis
title_fullStr Unilateral Eyelid Edema as Initial Sign of Orbital Sarcoidosis
title_full_unstemmed Unilateral Eyelid Edema as Initial Sign of Orbital Sarcoidosis
title_short Unilateral Eyelid Edema as Initial Sign of Orbital Sarcoidosis
title_sort unilateral eyelid edema as initial sign of orbital sarcoidosis
url http://dx.doi.org/10.1155/2016/6912927
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