Amyloid myopathy mimicked with idiopathic inflammatory myopathy diagnosed using Congo red staining: a case report

Abstract Amyloid myopathy often occurs in the context of systemic amyloidosis, as a rare manifestation of “light chain” (AL) amyloidosis, accounting for 1% of its incidence. A 58-year-old man with two years history of weakness and edema of lower extremity, elevated creatine kinase (CK), and inflamma...

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Main Authors: Xingyu Han, Mohammadreza Kosari, Li Xu, Yue Li, Meng-ge Yang, Huajie Gao, Huizhen Ge, Bitao Bu, Suqiong Ji
Format: Article
Language:English
Published: BMC 2024-11-01
Series:BMC Neurology
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Online Access:https://doi.org/10.1186/s12883-024-03900-z
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author Xingyu Han
Mohammadreza Kosari
Li Xu
Yue Li
Meng-ge Yang
Huajie Gao
Huizhen Ge
Bitao Bu
Suqiong Ji
author_facet Xingyu Han
Mohammadreza Kosari
Li Xu
Yue Li
Meng-ge Yang
Huajie Gao
Huizhen Ge
Bitao Bu
Suqiong Ji
author_sort Xingyu Han
collection DOAJ
description Abstract Amyloid myopathy often occurs in the context of systemic amyloidosis, as a rare manifestation of “light chain” (AL) amyloidosis, accounting for 1% of its incidence. A 58-year-old man with two years history of weakness and edema of lower extremity, elevated creatine kinase (CK), and inflammatory lesions from muscle biopsy which was misdiagnosed as inflammatory myopathy. After immunotherapy, the original symptoms worsened. We later confirmed the disease through MRI, Congo red staining and bone marrow puncture results. Our purpose is that to increase awareness of amyloid myopathy to minimize the risk of misdiagnosis and emphasize the importance of Congo red staining in diagnosing similar conditions.
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issn 1471-2377
language English
publishDate 2024-11-01
publisher BMC
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series BMC Neurology
spelling doaj-art-ee6de7f93c714f0b86572daf9eb4aab12025-08-20T02:49:16ZengBMCBMC Neurology1471-23772024-11-012411510.1186/s12883-024-03900-zAmyloid myopathy mimicked with idiopathic inflammatory myopathy diagnosed using Congo red staining: a case reportXingyu Han0Mohammadreza Kosari1Li Xu2Yue Li3Meng-ge Yang4Huajie Gao5Huizhen Ge6Bitao Bu7Suqiong Ji8Department of Neurology, Tongji Hospital, Tongji Medical College, Huazhong University of Science and TechnologyMBBS student, Tongji Hospital, Tongji Medical College, Huazhong University of Science and TechnologyDepartment of Neurology, Tongji Hospital, Tongji Medical College, Huazhong University of Science and TechnologyDepartment of Neurology, Tongji Hospital, Tongji Medical College, Huazhong University of Science and TechnologyDepartment of Neurology, Tongji Hospital, Tongji Medical College, Huazhong University of Science and TechnologyDepartment of Neurology, Tongji Hospital, Tongji Medical College, Huazhong University of Science and TechnologyDepartment of Neurology, Tongji Hospital, Tongji Medical College, Huazhong University of Science and TechnologyDepartment of Neurology, Tongji Hospital, Tongji Medical College, Huazhong University of Science and TechnologyDepartment of Neurology, Tongji Hospital, Tongji Medical College, Huazhong University of Science and TechnologyAbstract Amyloid myopathy often occurs in the context of systemic amyloidosis, as a rare manifestation of “light chain” (AL) amyloidosis, accounting for 1% of its incidence. A 58-year-old man with two years history of weakness and edema of lower extremity, elevated creatine kinase (CK), and inflammatory lesions from muscle biopsy which was misdiagnosed as inflammatory myopathy. After immunotherapy, the original symptoms worsened. We later confirmed the disease through MRI, Congo red staining and bone marrow puncture results. Our purpose is that to increase awareness of amyloid myopathy to minimize the risk of misdiagnosis and emphasize the importance of Congo red staining in diagnosing similar conditions.https://doi.org/10.1186/s12883-024-03900-zAmyloid myopathyInflammatory myopathyCongo red stainingM proteinemia
spellingShingle Xingyu Han
Mohammadreza Kosari
Li Xu
Yue Li
Meng-ge Yang
Huajie Gao
Huizhen Ge
Bitao Bu
Suqiong Ji
Amyloid myopathy mimicked with idiopathic inflammatory myopathy diagnosed using Congo red staining: a case report
BMC Neurology
Amyloid myopathy
Inflammatory myopathy
Congo red staining
M proteinemia
title Amyloid myopathy mimicked with idiopathic inflammatory myopathy diagnosed using Congo red staining: a case report
title_full Amyloid myopathy mimicked with idiopathic inflammatory myopathy diagnosed using Congo red staining: a case report
title_fullStr Amyloid myopathy mimicked with idiopathic inflammatory myopathy diagnosed using Congo red staining: a case report
title_full_unstemmed Amyloid myopathy mimicked with idiopathic inflammatory myopathy diagnosed using Congo red staining: a case report
title_short Amyloid myopathy mimicked with idiopathic inflammatory myopathy diagnosed using Congo red staining: a case report
title_sort amyloid myopathy mimicked with idiopathic inflammatory myopathy diagnosed using congo red staining a case report
topic Amyloid myopathy
Inflammatory myopathy
Congo red staining
M proteinemia
url https://doi.org/10.1186/s12883-024-03900-z
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AT yueli amyloidmyopathymimickedwithidiopathicinflammatorymyopathydiagnosedusingcongoredstainingacasereport
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