When the mask slips: A peripheral T-cell lymphoma disguised as lupus with myelofibrosis in a patient with May-Hegglin syndrome

We describe the case of a female patient with May-Hegglin syndrome who developed peripheral T-cell lymphoma not otherwise specified. The patient presents with systemic lupus erythematous phenotype and myelofibrosis secondary to T-cell lymphoma. Peripheral T-cell lymphoma not otherwise specified, rep...

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Main Authors: V Da Silva Constante, H Couvert, A Wolfromm, M Ilzkovitz
Format: Article
Language:English
Published: Elsevier 2025-01-01
Series:Leukemia Research Reports
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Online Access:http://www.sciencedirect.com/science/article/pii/S2213048924000888
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author V Da Silva Constante
H Couvert
A Wolfromm
M Ilzkovitz
author_facet V Da Silva Constante
H Couvert
A Wolfromm
M Ilzkovitz
author_sort V Da Silva Constante
collection DOAJ
description We describe the case of a female patient with May-Hegglin syndrome who developed peripheral T-cell lymphoma not otherwise specified. The patient presents with systemic lupus erythematous phenotype and myelofibrosis secondary to T-cell lymphoma. Peripheral T-cell lymphoma not otherwise specified, represents 25 % of all peripheral T-cell lymphoma. Its diagnosis remains challenging due to the polymorphous clinical presentation and pathological heterogeneity. Myelofibrosis associated with malignant lymphomas is rare and peripheral T-cell lymphoma is even rarer. To our knowledge, this is the first case to describe an association between May-Hegglin syndrome and a peripheral T-cell lymphoma.
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spelling doaj-art-edce5c3473014f4ea698204443e48aef2025-08-20T03:30:47ZengElsevierLeukemia Research Reports2213-04892025-01-012310049810.1016/j.lrr.2024.100498When the mask slips: A peripheral T-cell lymphoma disguised as lupus with myelofibrosis in a patient with May-Hegglin syndromeV Da Silva Constante0H Couvert1A Wolfromm2M Ilzkovitz3Hematology Department, Institut Jules Bordet – Hôpital Universitaire de Bruxelles (H.U.B.), Université Libre de Bruxelles (ULB), Brussels, BelgiumInternal Medicine Department, Institut Jules Bordet – Hôpital Universitaire de Bruxelles (H.U.B.), Université Libre de Bruxelles (ULB), Brussels, BelgiumHematology Department, Institut Jules Bordet – Hôpital Universitaire de Bruxelles (H.U.B.), Université Libre de Bruxelles (ULB), Brussels, BelgiumInternal Medicine Department, Institut Jules Bordet – Hôpital Universitaire de Bruxelles (H.U.B.), Université Libre de Bruxelles (ULB), Brussels, Belgium; Corresponding author at: Hôpital Universitaire de Bruxelles (H.U.B.), Université Libre de Bruxelles (ULB), Brussels Belgium. Rue Meylemeersch 90, 1070 Anderlecht- Brussels, Belgium.We describe the case of a female patient with May-Hegglin syndrome who developed peripheral T-cell lymphoma not otherwise specified. The patient presents with systemic lupus erythematous phenotype and myelofibrosis secondary to T-cell lymphoma. Peripheral T-cell lymphoma not otherwise specified, represents 25 % of all peripheral T-cell lymphoma. Its diagnosis remains challenging due to the polymorphous clinical presentation and pathological heterogeneity. Myelofibrosis associated with malignant lymphomas is rare and peripheral T-cell lymphoma is even rarer. To our knowledge, this is the first case to describe an association between May-Hegglin syndrome and a peripheral T-cell lymphoma.http://www.sciencedirect.com/science/article/pii/S2213048924000888Peripheral T-cell lymphomaPTCL, NOSMyelofibrosisSystemic lupus erythematosusMay-Hegglin syndrome
spellingShingle V Da Silva Constante
H Couvert
A Wolfromm
M Ilzkovitz
When the mask slips: A peripheral T-cell lymphoma disguised as lupus with myelofibrosis in a patient with May-Hegglin syndrome
Leukemia Research Reports
Peripheral T-cell lymphoma
PTCL, NOS
Myelofibrosis
Systemic lupus erythematosus
May-Hegglin syndrome
title When the mask slips: A peripheral T-cell lymphoma disguised as lupus with myelofibrosis in a patient with May-Hegglin syndrome
title_full When the mask slips: A peripheral T-cell lymphoma disguised as lupus with myelofibrosis in a patient with May-Hegglin syndrome
title_fullStr When the mask slips: A peripheral T-cell lymphoma disguised as lupus with myelofibrosis in a patient with May-Hegglin syndrome
title_full_unstemmed When the mask slips: A peripheral T-cell lymphoma disguised as lupus with myelofibrosis in a patient with May-Hegglin syndrome
title_short When the mask slips: A peripheral T-cell lymphoma disguised as lupus with myelofibrosis in a patient with May-Hegglin syndrome
title_sort when the mask slips a peripheral t cell lymphoma disguised as lupus with myelofibrosis in a patient with may hegglin syndrome
topic Peripheral T-cell lymphoma
PTCL, NOS
Myelofibrosis
Systemic lupus erythematosus
May-Hegglin syndrome
url http://www.sciencedirect.com/science/article/pii/S2213048924000888
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