Kartagener syndrome complicated by pulmonary tuberculosis, HIV, and hepatitis B: a rare case report

Abstract Kartagener syndrome is a rare autosomal recessive genetic disorder characterized by situs inversus, bronchiectasis, and sinusitis. This case report describes a 23-year-old male presenting with chronic cough, shortness of breath, and dextrocardia on CXR. HRCT confirmed situs inversus totalis...

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Bibliographic Details
Main Authors: Thaodem Collin Singh, Sunanda Haorongbam, Saikat Bhowmik, Martina Thokchom
Format: Article
Language:English
Published: SpringerOpen 2025-07-01
Series:The Egyptian Journal of Bronchology
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Online Access:https://doi.org/10.1186/s43168-025-00433-y
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Summary:Abstract Kartagener syndrome is a rare autosomal recessive genetic disorder characterized by situs inversus, bronchiectasis, and sinusitis. This case report describes a 23-year-old male presenting with chronic cough, shortness of breath, and dextrocardia on CXR. HRCT confirmed situs inversus totalis and bronchiectasis. X-ray of PNS confirmed the presence of sinusitis, leading to the diagnosis of Kartagener syndrome. The patient also had coexisting hepatitis B, HIV, and pulmonary tuberculosis. The patient was managed with symptomatic treatment, antibiotics, ATT, ART, and antiviral therapy against hepatitis B. This case highlights the importance of considering Kartagener syndrome in patients with recurrent respiratory symptoms and situs inversus and the need for comprehensive evaluation and management of associated comorbidities.
ISSN:2314-8551