Mesenchymal hamartoma of the liver

Mesenchymal hamartoma of the liver is the second most common benign liver tumor in children, yet its biology and pathogenesis are poorly understood. Typically, it presents as a large benign multicystic liver mass in children younger than three years, amenable to complete resection. Most tumors gradu...

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Main Authors: Gupta Rahul, Parelkar Sandesh, Sanghvi Beejal
Format: Article
Language:English
Published: Thieme Medical and Scientific Publishers Pvt. Ltd. 2009-12-01
Series:Indian Journal of Medical and Paediatric Oncology
Subjects:
Online Access:http://www.ijmpo.org/article.asp?issn=0971-5851;year=2009;volume=30;issue=4;spage=141;epage=143;aulast=Gupta
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author Gupta Rahul
Parelkar Sandesh
Sanghvi Beejal
author_facet Gupta Rahul
Parelkar Sandesh
Sanghvi Beejal
author_sort Gupta Rahul
collection DOAJ
description Mesenchymal hamartoma of the liver is the second most common benign liver tumor in children, yet its biology and pathogenesis are poorly understood. Typically, it presents as a large benign multicystic liver mass in children younger than three years, amenable to complete resection. Most tumors gradually increase in size, some reaching enormous proportions, some can undergo incomplete spontaneous regression, and rarely, few have shown malignant transformation to undifferentiated (embryonal) sarcoma. Here, we report a 13 month-old child who presented with abdominal distension and respiratory distress. Ultrasonography, Computed Tomography (CT), and magnetic resonance imaging (MRI) of the abdomen were suggestive of a mesenchymal hamartoma of the liver. Right hepatectomy was performed. Postoperatively, the patient recovered well. An attempt was also made to understand the possible etiology of the tumor.
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series Indian Journal of Medical and Paediatric Oncology
spelling doaj-art-e85f43fcce2845faa472b4e49c011ffb2025-08-20T03:10:38ZengThieme Medical and Scientific Publishers Pvt. Ltd.Indian Journal of Medical and Paediatric Oncology0971-58510975-21292009-12-01304141143Mesenchymal hamartoma of the liverGupta RahulParelkar SandeshSanghvi BeejalMesenchymal hamartoma of the liver is the second most common benign liver tumor in children, yet its biology and pathogenesis are poorly understood. Typically, it presents as a large benign multicystic liver mass in children younger than three years, amenable to complete resection. Most tumors gradually increase in size, some reaching enormous proportions, some can undergo incomplete spontaneous regression, and rarely, few have shown malignant transformation to undifferentiated (embryonal) sarcoma. Here, we report a 13 month-old child who presented with abdominal distension and respiratory distress. Ultrasonography, Computed Tomography (CT), and magnetic resonance imaging (MRI) of the abdomen were suggestive of a mesenchymal hamartoma of the liver. Right hepatectomy was performed. Postoperatively, the patient recovered well. An attempt was also made to understand the possible etiology of the tumor.http://www.ijmpo.org/article.asp?issn=0971-5851;year=2009;volume=30;issue=4;spage=141;epage=143;aulast=GuptaHemangio-endotheliomamesenchymal hamartomaright hepatectomy
spellingShingle Gupta Rahul
Parelkar Sandesh
Sanghvi Beejal
Mesenchymal hamartoma of the liver
Indian Journal of Medical and Paediatric Oncology
Hemangio-endothelioma
mesenchymal hamartoma
right hepatectomy
title Mesenchymal hamartoma of the liver
title_full Mesenchymal hamartoma of the liver
title_fullStr Mesenchymal hamartoma of the liver
title_full_unstemmed Mesenchymal hamartoma of the liver
title_short Mesenchymal hamartoma of the liver
title_sort mesenchymal hamartoma of the liver
topic Hemangio-endothelioma
mesenchymal hamartoma
right hepatectomy
url http://www.ijmpo.org/article.asp?issn=0971-5851;year=2009;volume=30;issue=4;spage=141;epage=143;aulast=Gupta
work_keys_str_mv AT guptarahul mesenchymalhamartomaoftheliver
AT parelkarsandesh mesenchymalhamartomaoftheliver
AT sanghvibeejal mesenchymalhamartomaoftheliver