Dental Management of a Young Child Affected by Galactosialidosis and a Gigantic Abdominal Growth
Galactosialidosis (GS) is a rare form of lysosomal storage disease that involves a broad spectrum of skeletal and soft tissue abnormalities. We report here on a 4-year 7-month-old boy with mild mental retardation, exhibiting multiple caries cavities and associated infectious foci and macroglossia. A...
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| Format: | Article |
| Language: | English |
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Wiley
2018-01-01
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| Series: | Case Reports in Dentistry |
| Online Access: | http://dx.doi.org/10.1155/2018/2086157 |
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| author | Yoselín Méndez-Salado Paola De Ávila-Rojas Amaury Pozos-Guillén Raúl Márquez-Preciado Miguel Ángel Noyola-Frías Socorro Ruiz-Rodríguez Arturo Garrocho-Rangel |
| author_facet | Yoselín Méndez-Salado Paola De Ávila-Rojas Amaury Pozos-Guillén Raúl Márquez-Preciado Miguel Ángel Noyola-Frías Socorro Ruiz-Rodríguez Arturo Garrocho-Rangel |
| author_sort | Yoselín Méndez-Salado |
| collection | DOAJ |
| description | Galactosialidosis (GS) is a rare form of lysosomal storage disease that involves a broad spectrum of skeletal and soft tissue abnormalities. We report here on a 4-year 7-month-old boy with mild mental retardation, exhibiting multiple caries cavities and associated infectious foci and macroglossia. A huge abdominal enlargement due to peritoneal ascites was evident. Behavioral management and patient positioning on the dental chair represented a true challenge. The patient was treated under general anesthesia. However, life-threatening postoperative complications occurred because of the impossibility of extubating the patient. A very careful preanesthetic assessment is crucial in children affected by general conditions associated with airway anomalies, such as GS. |
| format | Article |
| id | doaj-art-e6cbae01122a4c7f96a246d60dd05b44 |
| institution | Kabale University |
| issn | 2090-6447 2090-6455 |
| language | English |
| publishDate | 2018-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Dentistry |
| spelling | doaj-art-e6cbae01122a4c7f96a246d60dd05b442025-02-03T01:31:21ZengWileyCase Reports in Dentistry2090-64472090-64552018-01-01201810.1155/2018/20861572086157Dental Management of a Young Child Affected by Galactosialidosis and a Gigantic Abdominal GrowthYoselín Méndez-Salado0Paola De Ávila-Rojas1Amaury Pozos-Guillén2Raúl Márquez-Preciado3Miguel Ángel Noyola-Frías4Socorro Ruiz-Rodríguez5Arturo Garrocho-Rangel6Pediatric Dentistry Postgraduate Program, Faculty of Dentistry, San Luis Potosi University, San Luis Potosi, SLP, MexicoPediatric Dentistry Postgraduate Program, Faculty of Dentistry, San Luis Potosi University, San Luis Potosi, SLP, MexicoPediatric Dentistry Postgraduate Program, Faculty of Dentistry, San Luis Potosi University, San Luis Potosi, SLP, MexicoPediatric Dentistry Postgraduate Program, Faculty of Dentistry, San Luis Potosi University, San Luis Potosi, SLP, MexicoPediatric Dentistry Postgraduate Program, Faculty of Dentistry, San Luis Potosi University, San Luis Potosi, SLP, MexicoPediatric Dentistry Postgraduate Program, Faculty of Dentistry, San Luis Potosi University, San Luis Potosi, SLP, MexicoPediatric Dentistry Postgraduate Program, Faculty of Dentistry, San Luis Potosi University, San Luis Potosi, SLP, MexicoGalactosialidosis (GS) is a rare form of lysosomal storage disease that involves a broad spectrum of skeletal and soft tissue abnormalities. We report here on a 4-year 7-month-old boy with mild mental retardation, exhibiting multiple caries cavities and associated infectious foci and macroglossia. A huge abdominal enlargement due to peritoneal ascites was evident. Behavioral management and patient positioning on the dental chair represented a true challenge. The patient was treated under general anesthesia. However, life-threatening postoperative complications occurred because of the impossibility of extubating the patient. A very careful preanesthetic assessment is crucial in children affected by general conditions associated with airway anomalies, such as GS.http://dx.doi.org/10.1155/2018/2086157 |
| spellingShingle | Yoselín Méndez-Salado Paola De Ávila-Rojas Amaury Pozos-Guillén Raúl Márquez-Preciado Miguel Ángel Noyola-Frías Socorro Ruiz-Rodríguez Arturo Garrocho-Rangel Dental Management of a Young Child Affected by Galactosialidosis and a Gigantic Abdominal Growth Case Reports in Dentistry |
| title | Dental Management of a Young Child Affected by Galactosialidosis and a Gigantic Abdominal Growth |
| title_full | Dental Management of a Young Child Affected by Galactosialidosis and a Gigantic Abdominal Growth |
| title_fullStr | Dental Management of a Young Child Affected by Galactosialidosis and a Gigantic Abdominal Growth |
| title_full_unstemmed | Dental Management of a Young Child Affected by Galactosialidosis and a Gigantic Abdominal Growth |
| title_short | Dental Management of a Young Child Affected by Galactosialidosis and a Gigantic Abdominal Growth |
| title_sort | dental management of a young child affected by galactosialidosis and a gigantic abdominal growth |
| url | http://dx.doi.org/10.1155/2018/2086157 |
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