Androgen producing oncocytic adrenocortical tumor in a 3.7-year-old female

We report a 3.7-year-old female who presented with clinical features of premature adrenarche. Workup revealed significantly elevated androgen levels and advanced bone maturation, prompting abdominal imaging that identified a 6.0 cm adrenal mass. She underwent unilateral adrenalectomy, and subsequent...

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Bibliographic Details
Main Authors: Kelli D Mans, Ghada A Elmahmudi, Jiri B Bedrnicek, Monina S Cabrera
Format: Article
Language:English
Published: Bioscientifica 2025-02-01
Series:Endocrinology, Diabetes & Metabolism Case Reports
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Online Access:https://edm.bioscientifica.com/view/journals/edm/2025/1/EDM-24-0143.xml
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Summary:We report a 3.7-year-old female who presented with clinical features of premature adrenarche. Workup revealed significantly elevated androgen levels and advanced bone maturation, prompting abdominal imaging that identified a 6.0 cm adrenal mass. She underwent unilateral adrenalectomy, and subsequent histopathology revealed a benign oncocytic adrenocortical adenoma. Post-adrenalectomy, androgen levels returned to pre-pubertal levels. A review of the literature on pediatric oncocytic adrenocortical neoplasms (OANs) is presented, and we add our case to the growing data of this rare disease in the pediatric population.
ISSN:2052-0573