Pancreatic Neuroendocrine Tumor in the Setting of Dorsal Agenesis of the Pancreas
Dorsal agenesis of the pancreas (DAP) is an uncommon embryological abnormality where there is absence of the distal pancreas. DAP is mostly asymptomatic, but common presenting symptoms include diabetes mellitus, abdominal pain, pancreatitis, enlarged pancreatic head, and, in a few cases, polysplenia...
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| Main Authors: | , , |
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| Format: | Article |
| Language: | English |
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Wiley
2016-01-01
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| Series: | Case Reports in Gastrointestinal Medicine |
| Online Access: | http://dx.doi.org/10.1155/2016/3801962 |
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| _version_ | 1832558692871962624 |
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| author | Samih Nassif Cecilia Ponchiardi Teviah Sachs |
| author_facet | Samih Nassif Cecilia Ponchiardi Teviah Sachs |
| author_sort | Samih Nassif |
| collection | DOAJ |
| description | Dorsal agenesis of the pancreas (DAP) is an uncommon embryological abnormality where there is absence of the distal pancreas. DAP is mostly asymptomatic, but common presenting symptoms include diabetes mellitus, abdominal pain, pancreatitis, enlarged pancreatic head, and, in a few cases, polysplenia. MRCP and ERCP are the gold standard imaging techniques to demonstrate the absence of the dorsal pancreatic duct. The literature on the association of pancreatic neoplasia and DAP is limited. We present the case of a pancreatic neuroendocrine tumor in a patient with dorsal agenesis of the pancreas, with a review of the related literature. |
| format | Article |
| id | doaj-art-e0501b76aea8488f8848f60f04444a42 |
| institution | Kabale University |
| issn | 2090-6528 2090-6536 |
| language | English |
| publishDate | 2016-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Gastrointestinal Medicine |
| spelling | doaj-art-e0501b76aea8488f8848f60f04444a422025-02-03T01:31:49ZengWileyCase Reports in Gastrointestinal Medicine2090-65282090-65362016-01-01201610.1155/2016/38019623801962Pancreatic Neuroendocrine Tumor in the Setting of Dorsal Agenesis of the PancreasSamih Nassif0Cecilia Ponchiardi1Teviah Sachs2Boston University School of Medicine, 72 East Concord St., Boston, MA 02118, USADepartment of Pathology and Laboratory Medicine, Boston University School of Medicine, 72 East Concord St., Boston, MA 02118, USABoston University School of Medicine, Moakley Building, 3rd Floor, 830 Harrison Avenue, Boston, MA 02118, USADorsal agenesis of the pancreas (DAP) is an uncommon embryological abnormality where there is absence of the distal pancreas. DAP is mostly asymptomatic, but common presenting symptoms include diabetes mellitus, abdominal pain, pancreatitis, enlarged pancreatic head, and, in a few cases, polysplenia. MRCP and ERCP are the gold standard imaging techniques to demonstrate the absence of the dorsal pancreatic duct. The literature on the association of pancreatic neoplasia and DAP is limited. We present the case of a pancreatic neuroendocrine tumor in a patient with dorsal agenesis of the pancreas, with a review of the related literature.http://dx.doi.org/10.1155/2016/3801962 |
| spellingShingle | Samih Nassif Cecilia Ponchiardi Teviah Sachs Pancreatic Neuroendocrine Tumor in the Setting of Dorsal Agenesis of the Pancreas Case Reports in Gastrointestinal Medicine |
| title | Pancreatic Neuroendocrine Tumor in the Setting of Dorsal Agenesis of the Pancreas |
| title_full | Pancreatic Neuroendocrine Tumor in the Setting of Dorsal Agenesis of the Pancreas |
| title_fullStr | Pancreatic Neuroendocrine Tumor in the Setting of Dorsal Agenesis of the Pancreas |
| title_full_unstemmed | Pancreatic Neuroendocrine Tumor in the Setting of Dorsal Agenesis of the Pancreas |
| title_short | Pancreatic Neuroendocrine Tumor in the Setting of Dorsal Agenesis of the Pancreas |
| title_sort | pancreatic neuroendocrine tumor in the setting of dorsal agenesis of the pancreas |
| url | http://dx.doi.org/10.1155/2016/3801962 |
| work_keys_str_mv | AT samihnassif pancreaticneuroendocrinetumorinthesettingofdorsalagenesisofthepancreas AT ceciliaponchiardi pancreaticneuroendocrinetumorinthesettingofdorsalagenesisofthepancreas AT teviahsachs pancreaticneuroendocrinetumorinthesettingofdorsalagenesisofthepancreas |