Glioblastoma Multiforme in the Posterior Cranial Fossa in a Patient with Neurofibromatosis Type I

Patients with Neurofibromatosis type 1 (NF1) have an increased risk of developing neoplasms. The most common brain tumors, found in 15%–20% of NF1 patients, are hypothalamic-optic gliomas, followed by brainstem and cerebellar pilocytic astrocytomas. These tumors generally have a benign nature. NF1 p...

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Main Authors: Marike L. D. Broekman, Roelof Risselada, JooYeon Engelen-Lee, Wim G. M. Spliet, Bon H. Verweij
Format: Article
Language:English
Published: Wiley 2009-01-01
Series:Case Reports in Medicine
Online Access:http://dx.doi.org/10.1155/2009/757898
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author Marike L. D. Broekman
Roelof Risselada
JooYeon Engelen-Lee
Wim G. M. Spliet
Bon H. Verweij
author_facet Marike L. D. Broekman
Roelof Risselada
JooYeon Engelen-Lee
Wim G. M. Spliet
Bon H. Verweij
author_sort Marike L. D. Broekman
collection DOAJ
description Patients with Neurofibromatosis type 1 (NF1) have an increased risk of developing neoplasms. The most common brain tumors, found in 15%–20% of NF1 patients, are hypothalamic-optic gliomas, followed by brainstem and cerebellar pilocytic astrocytomas. These tumors generally have a benign nature. NF1 patients are predisposed to a 5-fold increased incidence of high-grade astrocytomas, which are usually located in supratentorial regions of the brain. We present an NF1 patient who developed a high-grade astrocytoma in the posterior fossa and discuss possible pathophysiological mechanisms.
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institution Kabale University
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publishDate 2009-01-01
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spelling doaj-art-dfd8109fffdb40f6bcc9f6623ddaebca2025-08-20T03:26:09ZengWileyCase Reports in Medicine1687-96271687-96352009-01-01200910.1155/2009/757898757898Glioblastoma Multiforme in the Posterior Cranial Fossa in a Patient with Neurofibromatosis Type IMarike L. D. Broekman0Roelof Risselada1JooYeon Engelen-Lee2Wim G. M. Spliet3Bon H. Verweij4Rudolf Magnus Institute of Neuroscience, University Medical Center Utrecht, 3508 GA Utrecht, The NetherlandsDepartment of Medical Informatics, Erasmus University Medical Center, 3051 GE Rotterdam, The NetherlandsDepartment of Pathology, University Medical Center Utrecht, 3508 GA Utrecht, The NetherlandsDepartment of Pathology, University Medical Center Utrecht, 3508 GA Utrecht, The NetherlandsRudolf Magnus Institute of Neuroscience, University Medical Center Utrecht, 3508 GA Utrecht, The NetherlandsPatients with Neurofibromatosis type 1 (NF1) have an increased risk of developing neoplasms. The most common brain tumors, found in 15%–20% of NF1 patients, are hypothalamic-optic gliomas, followed by brainstem and cerebellar pilocytic astrocytomas. These tumors generally have a benign nature. NF1 patients are predisposed to a 5-fold increased incidence of high-grade astrocytomas, which are usually located in supratentorial regions of the brain. We present an NF1 patient who developed a high-grade astrocytoma in the posterior fossa and discuss possible pathophysiological mechanisms.http://dx.doi.org/10.1155/2009/757898
spellingShingle Marike L. D. Broekman
Roelof Risselada
JooYeon Engelen-Lee
Wim G. M. Spliet
Bon H. Verweij
Glioblastoma Multiforme in the Posterior Cranial Fossa in a Patient with Neurofibromatosis Type I
Case Reports in Medicine
title Glioblastoma Multiforme in the Posterior Cranial Fossa in a Patient with Neurofibromatosis Type I
title_full Glioblastoma Multiforme in the Posterior Cranial Fossa in a Patient with Neurofibromatosis Type I
title_fullStr Glioblastoma Multiforme in the Posterior Cranial Fossa in a Patient with Neurofibromatosis Type I
title_full_unstemmed Glioblastoma Multiforme in the Posterior Cranial Fossa in a Patient with Neurofibromatosis Type I
title_short Glioblastoma Multiforme in the Posterior Cranial Fossa in a Patient with Neurofibromatosis Type I
title_sort glioblastoma multiforme in the posterior cranial fossa in a patient with neurofibromatosis type i
url http://dx.doi.org/10.1155/2009/757898
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