Transumbilical Surgery for Duodenal Stenosis in a Child with Situs Inversus: The First Report

Background. Situs inversus is a rare congenital anomaly with a reported incidence of only 1 in 5,000 to 10,000 live births. Congenital duodenal stenosis complicated with situs inversus is an even rarer entity. Case Presentation. A 1-year-old girl with situs inversus who had undergone a hemi-Fontan p...

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Main Authors: Isamu Saeki, Yu Ueno, Wataru Mukai, Reisuke Imaji, Takashi Akiyama
Format: Article
Language:English
Published: Wiley 2017-01-01
Series:Case Reports in Pediatrics
Online Access:http://dx.doi.org/10.1155/2017/2074387
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author Isamu Saeki
Yu Ueno
Wataru Mukai
Reisuke Imaji
Takashi Akiyama
author_facet Isamu Saeki
Yu Ueno
Wataru Mukai
Reisuke Imaji
Takashi Akiyama
author_sort Isamu Saeki
collection DOAJ
description Background. Situs inversus is a rare congenital anomaly with a reported incidence of only 1 in 5,000 to 10,000 live births. Congenital duodenal stenosis complicated with situs inversus is an even rarer entity. Case Presentation. A 1-year-old girl with situs inversus who had undergone a hemi-Fontan procedure against a single ventricle in our hospital was referred to our department for vomiting and failure to thrive. An upper gastrointestinal contrast study and endoscopy revealed duodenal stenosis. A transumbilical radical operation as a minimally invasive surgery was successfully performed. After the surgery, she stopped vomiting, and the postoperative course was uneventful with good cosmetic results. Conclusions. To our knowledge, this is the first report of transumbilical surgery for congenital duodenal stenosis with situs inversus as minimally invasive surgery. Transumbilical surgery to situs inversus patient can be performed safely and lead to good cosmetic outcome.
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publishDate 2017-01-01
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series Case Reports in Pediatrics
spelling doaj-art-dc401d0ac40c44fbaa0c113fcb5cde4a2025-02-03T06:14:17ZengWileyCase Reports in Pediatrics2090-68032090-68112017-01-01201710.1155/2017/20743872074387Transumbilical Surgery for Duodenal Stenosis in a Child with Situs Inversus: The First ReportIsamu Saeki0Yu Ueno1Wataru Mukai2Reisuke Imaji3Takashi Akiyama4Department of Pediatric Surgery, Hiroshima City Hospital, 7-33 Motomachi Naka-ku, Hiroshima-shi, Hiroshima 730-8518, JapanDepartment of Pediatric Surgery, Hiroshima City Hospital, 7-33 Motomachi Naka-ku, Hiroshima-shi, Hiroshima 730-8518, JapanDepartment of Pediatric Surgery, Hiroshima City Hospital, 7-33 Motomachi Naka-ku, Hiroshima-shi, Hiroshima 730-8518, JapanDepartment of Pediatric Surgery, Hiroshima City Hospital, 7-33 Motomachi Naka-ku, Hiroshima-shi, Hiroshima 730-8518, JapanDepartment of Pediatric Surgery, Hiroshima City Hospital, 7-33 Motomachi Naka-ku, Hiroshima-shi, Hiroshima 730-8518, JapanBackground. Situs inversus is a rare congenital anomaly with a reported incidence of only 1 in 5,000 to 10,000 live births. Congenital duodenal stenosis complicated with situs inversus is an even rarer entity. Case Presentation. A 1-year-old girl with situs inversus who had undergone a hemi-Fontan procedure against a single ventricle in our hospital was referred to our department for vomiting and failure to thrive. An upper gastrointestinal contrast study and endoscopy revealed duodenal stenosis. A transumbilical radical operation as a minimally invasive surgery was successfully performed. After the surgery, she stopped vomiting, and the postoperative course was uneventful with good cosmetic results. Conclusions. To our knowledge, this is the first report of transumbilical surgery for congenital duodenal stenosis with situs inversus as minimally invasive surgery. Transumbilical surgery to situs inversus patient can be performed safely and lead to good cosmetic outcome.http://dx.doi.org/10.1155/2017/2074387
spellingShingle Isamu Saeki
Yu Ueno
Wataru Mukai
Reisuke Imaji
Takashi Akiyama
Transumbilical Surgery for Duodenal Stenosis in a Child with Situs Inversus: The First Report
Case Reports in Pediatrics
title Transumbilical Surgery for Duodenal Stenosis in a Child with Situs Inversus: The First Report
title_full Transumbilical Surgery for Duodenal Stenosis in a Child with Situs Inversus: The First Report
title_fullStr Transumbilical Surgery for Duodenal Stenosis in a Child with Situs Inversus: The First Report
title_full_unstemmed Transumbilical Surgery for Duodenal Stenosis in a Child with Situs Inversus: The First Report
title_short Transumbilical Surgery for Duodenal Stenosis in a Child with Situs Inversus: The First Report
title_sort transumbilical surgery for duodenal stenosis in a child with situs inversus the first report
url http://dx.doi.org/10.1155/2017/2074387
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