Lymphedema in Klippel-Trenaunay Syndrome: Is It Possible to Normalize?

The aim of this study is to report the results of intensive therapy of lymphedema associated with Klippel-Trenaunay syndrome. A 24-year-old female patient reported that her family had observed edema in her right leg and port wine stains from birth. For ten years, they consulted with different specia...

Full description

Saved in:
Bibliographic Details
Main Authors: Jose Maria Pereira de Godoy, Angela Río, Paloma Domingo Garcia, Maria de Fatima Guerreiro Godoy
Format: Article
Language:English
Published: Wiley 2016-01-01
Series:Case Reports in Vascular Medicine
Online Access:http://dx.doi.org/10.1155/2016/5230634
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1832565131051008000
author Jose Maria Pereira de Godoy
Angela Río
Paloma Domingo Garcia
Maria de Fatima Guerreiro Godoy
author_facet Jose Maria Pereira de Godoy
Angela Río
Paloma Domingo Garcia
Maria de Fatima Guerreiro Godoy
author_sort Jose Maria Pereira de Godoy
collection DOAJ
description The aim of this study is to report the results of intensive therapy of lymphedema associated with Klippel-Trenaunay syndrome. A 24-year-old female patient reported that her family had observed edema in her right leg and port wine stains from birth. For ten years, they consulted with different specialists in the region but the prognosis did not change and no specific treatment was found. In 2014, at the age of 24, with massive lymphedema, a leg ulcer, and recurrent infections, she started treatment at the Clínica Godoy in São José do Rio Preto. She was evaluated by clinical history, physical examination, water displacement volumetry, and bioimpedance. Intensive therapy (8 hours daily) was proposed using Manual Lymphatic Therapy (Godoy & Godoy), Cervical Stimulation Therapy, Mechanical Lymphatic Therapy, a grosgrain stocking adjusted several times a day, and the use of Unna boot in the region of the ulcer. The volume of edema was reduced by about 44% within the first week with further reductions in the following weeks and healing of the ulcer. Subsequently, it was possible to control and maintain the reduction in swelling with less intense treatment. It is possible to reduce and maintain the treatment results of lymphedema associated with Klippel-Trenaunay syndrome.
format Article
id doaj-art-db16905d7e1346118b582bd47c6ee947
institution Kabale University
issn 2090-6986
2090-6994
language English
publishDate 2016-01-01
publisher Wiley
record_format Article
series Case Reports in Vascular Medicine
spelling doaj-art-db16905d7e1346118b582bd47c6ee9472025-02-03T01:09:29ZengWileyCase Reports in Vascular Medicine2090-69862090-69942016-01-01201610.1155/2016/52306345230634Lymphedema in Klippel-Trenaunay Syndrome: Is It Possible to Normalize?Jose Maria Pereira de Godoy0Angela Río1Paloma Domingo Garcia2Maria de Fatima Guerreiro Godoy3Cardiology and Cardiovascular Surgery Department, The Medicine School in São José do Rio Preto (FAMERP) and CNPq (National Council for Research and Development), São José do Rio Preto, SP, BrazilUniversidad Europea of Madrid, Madrid, SpainResearch Group of Godoy Clinic, Sao Jose do Rio Preto, SP, BrazilMedicine School in São José do Rio Preto (FAMERP) and Research Group of the Godoy Clinic, Sao Jose do Rio Preto, SP, BrazilThe aim of this study is to report the results of intensive therapy of lymphedema associated with Klippel-Trenaunay syndrome. A 24-year-old female patient reported that her family had observed edema in her right leg and port wine stains from birth. For ten years, they consulted with different specialists in the region but the prognosis did not change and no specific treatment was found. In 2014, at the age of 24, with massive lymphedema, a leg ulcer, and recurrent infections, she started treatment at the Clínica Godoy in São José do Rio Preto. She was evaluated by clinical history, physical examination, water displacement volumetry, and bioimpedance. Intensive therapy (8 hours daily) was proposed using Manual Lymphatic Therapy (Godoy & Godoy), Cervical Stimulation Therapy, Mechanical Lymphatic Therapy, a grosgrain stocking adjusted several times a day, and the use of Unna boot in the region of the ulcer. The volume of edema was reduced by about 44% within the first week with further reductions in the following weeks and healing of the ulcer. Subsequently, it was possible to control and maintain the reduction in swelling with less intense treatment. It is possible to reduce and maintain the treatment results of lymphedema associated with Klippel-Trenaunay syndrome.http://dx.doi.org/10.1155/2016/5230634
spellingShingle Jose Maria Pereira de Godoy
Angela Río
Paloma Domingo Garcia
Maria de Fatima Guerreiro Godoy
Lymphedema in Klippel-Trenaunay Syndrome: Is It Possible to Normalize?
Case Reports in Vascular Medicine
title Lymphedema in Klippel-Trenaunay Syndrome: Is It Possible to Normalize?
title_full Lymphedema in Klippel-Trenaunay Syndrome: Is It Possible to Normalize?
title_fullStr Lymphedema in Klippel-Trenaunay Syndrome: Is It Possible to Normalize?
title_full_unstemmed Lymphedema in Klippel-Trenaunay Syndrome: Is It Possible to Normalize?
title_short Lymphedema in Klippel-Trenaunay Syndrome: Is It Possible to Normalize?
title_sort lymphedema in klippel trenaunay syndrome is it possible to normalize
url http://dx.doi.org/10.1155/2016/5230634
work_keys_str_mv AT josemariapereiradegodoy lymphedemainklippeltrenaunaysyndromeisitpossibletonormalize
AT angelario lymphedemainklippeltrenaunaysyndromeisitpossibletonormalize
AT palomadomingogarcia lymphedemainklippeltrenaunaysyndromeisitpossibletonormalize
AT mariadefatimaguerreirogodoy lymphedemainklippeltrenaunaysyndromeisitpossibletonormalize