An unusual presentation of IgG4-related disease
IgG4-related disease (IgG4-RD) is an emerging disease concept that was first recognized in the 21st century. It has since then been attracting substantial attention in many fields of medicine as it tends to involve either synchronously or metachronously, various organs, including the pancreas, bile...
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| Format: | Article |
| Language: | English |
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SAGE Publishing
2020-01-01
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| Series: | Indian Journal of Rheumatology |
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| Online Access: | http://www.indianjrheumatol.com/article.asp?issn=0973-3698;year=2020;volume=15;issue=3;spage=229;epage=233;aulast=Rohit |
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| author | Upreti Rohit Hegde Arun Sengupta Prashant Gupta Vikas Jain Anurag Kovilapu Uday Bhanu |
| author_facet | Upreti Rohit Hegde Arun Sengupta Prashant Gupta Vikas Jain Anurag Kovilapu Uday Bhanu |
| author_sort | Upreti Rohit |
| collection | DOAJ |
| description | IgG4-related disease (IgG4-RD) is an emerging disease concept that was first recognized in the 21st century. It has since then been attracting substantial attention in many fields of medicine as it tends to involve either synchronously or metachronously, various organs, including the pancreas, bile duct, lacrimal gland, salivary gland, and many others. This umbrella diagnosis now successfully explains a substantial number of disorders, which were previously regarded as “idiopathic.” Reports of the manifestations of IgG4-RD in the head and neck are extremely rare. Otologic manifestations have been reported, but only a handful of cases are available in literature that have been confirmed by immunohistopathology. We, herein, present a case of IgG4-RD of the middle ear, which manifested as a growth in the left mastoid and middle ear cavity, and became symptomatic with symptoms of chronic otitis media in the left ear, and was subsequently diagnosed to have IgG4-RD. |
| format | Article |
| id | doaj-art-da02d90f4f3b4e60ab2c8cacdad93bec |
| institution | Kabale University |
| issn | 0973-3698 0973-3701 |
| language | English |
| publishDate | 2020-01-01 |
| publisher | SAGE Publishing |
| record_format | Article |
| series | Indian Journal of Rheumatology |
| spelling | doaj-art-da02d90f4f3b4e60ab2c8cacdad93bec2025-02-03T11:05:40ZengSAGE PublishingIndian Journal of Rheumatology0973-36980973-37012020-01-0115322923310.4103/injr.injr_12_20An unusual presentation of IgG4-related diseaseUpreti RohitHegde ArunSengupta PrashantGupta VikasJain AnuragKovilapu Uday BhanuIgG4-related disease (IgG4-RD) is an emerging disease concept that was first recognized in the 21st century. It has since then been attracting substantial attention in many fields of medicine as it tends to involve either synchronously or metachronously, various organs, including the pancreas, bile duct, lacrimal gland, salivary gland, and many others. This umbrella diagnosis now successfully explains a substantial number of disorders, which were previously regarded as “idiopathic.” Reports of the manifestations of IgG4-RD in the head and neck are extremely rare. Otologic manifestations have been reported, but only a handful of cases are available in literature that have been confirmed by immunohistopathology. We, herein, present a case of IgG4-RD of the middle ear, which manifested as a growth in the left mastoid and middle ear cavity, and became symptomatic with symptoms of chronic otitis media in the left ear, and was subsequently diagnosed to have IgG4-RD.http://www.indianjrheumatol.com/article.asp?issn=0973-3698;year=2020;volume=15;issue=3;spage=229;epage=233;aulast=Rohitigg4igg4-related diseasemiddle ear diseaselymphoplasmacytic infiltratestoriform fibrosis |
| spellingShingle | Upreti Rohit Hegde Arun Sengupta Prashant Gupta Vikas Jain Anurag Kovilapu Uday Bhanu An unusual presentation of IgG4-related disease Indian Journal of Rheumatology igg4 igg4-related disease middle ear disease lymphoplasmacytic infiltrate storiform fibrosis |
| title | An unusual presentation of IgG4-related disease |
| title_full | An unusual presentation of IgG4-related disease |
| title_fullStr | An unusual presentation of IgG4-related disease |
| title_full_unstemmed | An unusual presentation of IgG4-related disease |
| title_short | An unusual presentation of IgG4-related disease |
| title_sort | unusual presentation of igg4 related disease |
| topic | igg4 igg4-related disease middle ear disease lymphoplasmacytic infiltrate storiform fibrosis |
| url | http://www.indianjrheumatol.com/article.asp?issn=0973-3698;year=2020;volume=15;issue=3;spage=229;epage=233;aulast=Rohit |
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