Burkitt lymphoma in children and adolescents: a single-center analysis over a 30-year period

Introduction and Objectives: Burkitt lymphoma (BL) is a fast-growing and highly aggressive type of non-Hodgkin lymphoma. Nevertheless, 80-90% of patients on risk-adapted chemotherapy survive. The aim of this study was to characterize a pediatric population with BL in a center of reference, determine...

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Main Authors: Inês Pedrosa, Ana Mafalda Figueiredo, Ana Sofia Simões, Inês Luz, Mónica Jerónimo, Sónia Silva, Alice Carvalho, Manuel Brito
Format: Article
Language:English
Published: Publicaciones Permanyer 2025-01-01
Series:Portuguese Journal of Pediatrics
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Online Access:https://pjp.spp.pt/frame_eng.php?id=123
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author Inês Pedrosa
Ana Mafalda Figueiredo
Ana Sofia Simões
Inês Luz
Mónica Jerónimo
Sónia Silva
Alice Carvalho
Manuel Brito
author_facet Inês Pedrosa
Ana Mafalda Figueiredo
Ana Sofia Simões
Inês Luz
Mónica Jerónimo
Sónia Silva
Alice Carvalho
Manuel Brito
author_sort Inês Pedrosa
collection DOAJ
description Introduction and Objectives: Burkitt lymphoma (BL) is a fast-growing and highly aggressive type of non-Hodgkin lymphoma. Nevertheless, 80-90% of patients on risk-adapted chemotherapy survive. The aim of this study was to characterize a pediatric population with BL in a center of reference, determine the 30-year incidence and calculate event-free and overall survival. Methods: We performed a retrospective and observational analysis of all patients diagnosed with BL between January 1993 and December 2022. Demographic and clinical data was collected. Patients were staged according to the St. Jude classification system and treated with different protocols according to risk stratification. A descriptive analysis, Portuguese central region incidence calculation and survival analysis were performed. Results: A total of 48 patients were included, 85% of which were male, with a mean age of 7.8 ± 3.7 years. Most cases (95.8%) were sporadic. The mean incidence rate was 0.34 cases per 100,000 person-years. Most (50%) patients were St. Jude stage III. A total of 41% were admitted to the pediatric intensive care unit (PICU), mostly due to tumor lysis syndrome (78.9%). The mortality rate was 6.3%. The mean follow-up was 87.8 ± 59.0 months with a 3-year event-free survival rate of 88.9% and overall survival rate of 93.2%. Subgroup analysis showed no differences between chemotherapy protocols. Higher uric acid was independently associated with PICU admission. Discussion: Our results regarding incidence and mortality are in line with previously-published literature. Notably, the last patient who died in our center was diagnosed 18 years ago. In conclusion, our results contribute to a better understanding of the epidemiology, clinical course and outcomes of BL in Portugal’s pediatric population.
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spelling doaj-art-d8f87faa7484455eb3bf3725db6228922025-08-20T02:58:21ZengPublicaciones PermanyerPortuguese Journal of Pediatrics2184-44532025-01-0156110.24875/PJP.23000029Burkitt lymphoma in children and adolescents: a single-center analysis over a 30-year periodInês Pedrosa0Ana Mafalda Figueiredo1Ana Sofia Simões2Inês Luz3Mónica Jerónimo4Sónia Silva5Alice Carvalho6Manuel Brito7Serviço de Pediatria, Centro Hospitalar de Leiria, Leiria; Serviço de Oncologia Pediátrica, Centro Hospitalar e Universitário de Coimbra, Coimbra; PortugalFaculdade de Medicina, Universidade de Coimbra, Coimbra, PortugalServiço de Oncologia Pediátrica, Centro Hospitalar e Universitário de Coimbra, Coimbra; Faculdade de Medicina, Universidade de Coimbra, Coimbra. PortugalServiço de Oncologia Pediátrica, Centro Hospitalar e Universitário de Coimbra, Coimbra, PortugalServiço de Oncologia Pediátrica, Centro Hospitalar e Universitário de Coimbra, Coimbra, PortugalServiço de Oncologia Pediátrica, Centro Hospitalar e Universitário de Coimbra, Coimbra, PortugalServiço de Oncologia Pediátrica, Centro Hospitalar e Universitário de Coimbra, Coimbra, PortugalServiço de Oncologia Pediátrica, Centro Hospitalar e Universitário de Coimbra, Coimbra. PortugalIntroduction and Objectives: Burkitt lymphoma (BL) is a fast-growing and highly aggressive type of non-Hodgkin lymphoma. Nevertheless, 80-90% of patients on risk-adapted chemotherapy survive. The aim of this study was to characterize a pediatric population with BL in a center of reference, determine the 30-year incidence and calculate event-free and overall survival. Methods: We performed a retrospective and observational analysis of all patients diagnosed with BL between January 1993 and December 2022. Demographic and clinical data was collected. Patients were staged according to the St. Jude classification system and treated with different protocols according to risk stratification. A descriptive analysis, Portuguese central region incidence calculation and survival analysis were performed. Results: A total of 48 patients were included, 85% of which were male, with a mean age of 7.8 ± 3.7 years. Most cases (95.8%) were sporadic. The mean incidence rate was 0.34 cases per 100,000 person-years. Most (50%) patients were St. Jude stage III. A total of 41% were admitted to the pediatric intensive care unit (PICU), mostly due to tumor lysis syndrome (78.9%). The mortality rate was 6.3%. The mean follow-up was 87.8 ± 59.0 months with a 3-year event-free survival rate of 88.9% and overall survival rate of 93.2%. Subgroup analysis showed no differences between chemotherapy protocols. Higher uric acid was independently associated with PICU admission. Discussion: Our results regarding incidence and mortality are in line with previously-published literature. Notably, the last patient who died in our center was diagnosed 18 years ago. In conclusion, our results contribute to a better understanding of the epidemiology, clinical course and outcomes of BL in Portugal’s pediatric population. https://pjp.spp.pt/frame_eng.php?id=123Burkitt lymphoma. Survival. Pediatric oncology.
spellingShingle Inês Pedrosa
Ana Mafalda Figueiredo
Ana Sofia Simões
Inês Luz
Mónica Jerónimo
Sónia Silva
Alice Carvalho
Manuel Brito
Burkitt lymphoma in children and adolescents: a single-center analysis over a 30-year period
Portuguese Journal of Pediatrics
Burkitt lymphoma. Survival. Pediatric oncology.
title Burkitt lymphoma in children and adolescents: a single-center analysis over a 30-year period
title_full Burkitt lymphoma in children and adolescents: a single-center analysis over a 30-year period
title_fullStr Burkitt lymphoma in children and adolescents: a single-center analysis over a 30-year period
title_full_unstemmed Burkitt lymphoma in children and adolescents: a single-center analysis over a 30-year period
title_short Burkitt lymphoma in children and adolescents: a single-center analysis over a 30-year period
title_sort burkitt lymphoma in children and adolescents a single center analysis over a 30 year period
topic Burkitt lymphoma. Survival. Pediatric oncology.
url https://pjp.spp.pt/frame_eng.php?id=123
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