A Rare Case of Persistent Lactic Acidosis in the ICU: Glycogenic Hepatopathy and Mauriac Syndrome
Mauriac syndrome is a rare disorder that can present with the single feature of glycogenic hepatopathy in children and adults with poorly controlled diabetes mellitus. An often underrecognized finding of glycogenic hepatopathy is lactic acidosis and hyperlactatemia. Primary treatment of glycogenic h...
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| Format: | Article |
| Language: | English |
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Wiley
2016-01-01
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| Series: | Case Reports in Critical Care |
| Online Access: | http://dx.doi.org/10.1155/2016/6072909 |
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| _version_ | 1832551981718175744 |
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| author | Kirsten S. Deemer George F. Alvarez |
| author_facet | Kirsten S. Deemer George F. Alvarez |
| author_sort | Kirsten S. Deemer |
| collection | DOAJ |
| description | Mauriac syndrome is a rare disorder that can present with the single feature of glycogenic hepatopathy in children and adults with poorly controlled diabetes mellitus. An often underrecognized finding of glycogenic hepatopathy is lactic acidosis and hyperlactatemia. Primary treatment of glycogenic hepatopathy is improved long-term blood glucose control. Resolution of symptoms and hepatomegaly will occur with improvement in hemoglobin A1C. We present here a case of a young adult female presenting to the intensive care unit with Mauriac syndrome. This case demonstrates exacerbation of lactic acidosis in a patient with glycogenic hepatopathy treated for diabetic ketoacidosis with high dose insulin and dextrose. |
| format | Article |
| id | doaj-art-d54a0420b03543cd97778b0e18f2f165 |
| institution | Kabale University |
| issn | 2090-6420 2090-6439 |
| language | English |
| publishDate | 2016-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Critical Care |
| spelling | doaj-art-d54a0420b03543cd97778b0e18f2f1652025-02-03T05:59:53ZengWileyCase Reports in Critical Care2090-64202090-64392016-01-01201610.1155/2016/60729096072909A Rare Case of Persistent Lactic Acidosis in the ICU: Glycogenic Hepatopathy and Mauriac SyndromeKirsten S. Deemer0George F. Alvarez1Department of Critical Care Medicine, South Health Campus ICU, 4448 Front Street SE, Calgary, AB, T3M 1M4, CanadaDepartment of Critical Care Medicine, University of Calgary, AB, CanadaMauriac syndrome is a rare disorder that can present with the single feature of glycogenic hepatopathy in children and adults with poorly controlled diabetes mellitus. An often underrecognized finding of glycogenic hepatopathy is lactic acidosis and hyperlactatemia. Primary treatment of glycogenic hepatopathy is improved long-term blood glucose control. Resolution of symptoms and hepatomegaly will occur with improvement in hemoglobin A1C. We present here a case of a young adult female presenting to the intensive care unit with Mauriac syndrome. This case demonstrates exacerbation of lactic acidosis in a patient with glycogenic hepatopathy treated for diabetic ketoacidosis with high dose insulin and dextrose.http://dx.doi.org/10.1155/2016/6072909 |
| spellingShingle | Kirsten S. Deemer George F. Alvarez A Rare Case of Persistent Lactic Acidosis in the ICU: Glycogenic Hepatopathy and Mauriac Syndrome Case Reports in Critical Care |
| title | A Rare Case of Persistent Lactic Acidosis in the ICU: Glycogenic Hepatopathy and Mauriac Syndrome |
| title_full | A Rare Case of Persistent Lactic Acidosis in the ICU: Glycogenic Hepatopathy and Mauriac Syndrome |
| title_fullStr | A Rare Case of Persistent Lactic Acidosis in the ICU: Glycogenic Hepatopathy and Mauriac Syndrome |
| title_full_unstemmed | A Rare Case of Persistent Lactic Acidosis in the ICU: Glycogenic Hepatopathy and Mauriac Syndrome |
| title_short | A Rare Case of Persistent Lactic Acidosis in the ICU: Glycogenic Hepatopathy and Mauriac Syndrome |
| title_sort | rare case of persistent lactic acidosis in the icu glycogenic hepatopathy and mauriac syndrome |
| url | http://dx.doi.org/10.1155/2016/6072909 |
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