Lupus Enteritis as an Initial Presentation of Systemic Lupus Erythematosus

Systemic lupus erythematosus (SLE) is an autoimmune disorder which can affect multiple organs and clinical presentation is often a myriad of symptoms; therefore, the index of suspicion should rise when evaluating patients with multiorgan symptomatology. Lupus enteritis is a distinct subset of SLE, d...

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Main Authors: Sisira Sran, Manpreet Sran, Narmisha Patel, Prachi Anand
Format: Article
Language:English
Published: Wiley 2014-01-01
Series:Case Reports in Gastrointestinal Medicine
Online Access:http://dx.doi.org/10.1155/2014/962735
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author Sisira Sran
Manpreet Sran
Narmisha Patel
Prachi Anand
author_facet Sisira Sran
Manpreet Sran
Narmisha Patel
Prachi Anand
author_sort Sisira Sran
collection DOAJ
description Systemic lupus erythematosus (SLE) is an autoimmune disorder which can affect multiple organs and clinical presentation is often a myriad of symptoms; therefore, the index of suspicion should rise when evaluating patients with multiorgan symptomatology. Lupus enteritis is a distinct subset of SLE, defined as either vasculitis or inflammation of the small bowel, with supportive image and/or biopsy findings. The clinical picture of lupus enteritis is often nonspecific, with mild to severe abdominal pain, diarrhea, and vomiting being the cardinal manifestations. Although considered a form of visceral or serosal vasculitis, lupus enteritis is seldom confirmed on histology, making computerized tomography (CT) the gold standard for diagnosis. Lupus enteritis is generally steroid-responsive, and the route of administration is based on clinical status and organ involvement, with preference for intravenous (IV) route in flares with significant tissue edema. The following case describes a young woman presenting with lupus enteritis and lupus panniculitis as an initial manifestation of SLE, the utilization of abdominal CT in diagnosis, and current treatment protocols used for lupus enteritis.
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spelling doaj-art-d4790a44775e4f83b34be4e781f5e8842025-02-03T01:02:12ZengWileyCase Reports in Gastrointestinal Medicine2090-65282090-65362014-01-01201410.1155/2014/962735962735Lupus Enteritis as an Initial Presentation of Systemic Lupus ErythematosusSisira Sran0Manpreet Sran1Narmisha Patel2Prachi Anand3Department of Medicine, Nassau University Medical Center, 2201 Hempstead Turnpike, East Meadow, NY 11554, USADepartment of Medicine, Nassau University Medical Center, 2201 Hempstead Turnpike, East Meadow, NY 11554, USADepartment of Medicine, Nassau University Medical Center, 2201 Hempstead Turnpike, East Meadow, NY 11554, USADepartment of Medicine, Nassau University Medical Center, 2201 Hempstead Turnpike, East Meadow, NY 11554, USASystemic lupus erythematosus (SLE) is an autoimmune disorder which can affect multiple organs and clinical presentation is often a myriad of symptoms; therefore, the index of suspicion should rise when evaluating patients with multiorgan symptomatology. Lupus enteritis is a distinct subset of SLE, defined as either vasculitis or inflammation of the small bowel, with supportive image and/or biopsy findings. The clinical picture of lupus enteritis is often nonspecific, with mild to severe abdominal pain, diarrhea, and vomiting being the cardinal manifestations. Although considered a form of visceral or serosal vasculitis, lupus enteritis is seldom confirmed on histology, making computerized tomography (CT) the gold standard for diagnosis. Lupus enteritis is generally steroid-responsive, and the route of administration is based on clinical status and organ involvement, with preference for intravenous (IV) route in flares with significant tissue edema. The following case describes a young woman presenting with lupus enteritis and lupus panniculitis as an initial manifestation of SLE, the utilization of abdominal CT in diagnosis, and current treatment protocols used for lupus enteritis.http://dx.doi.org/10.1155/2014/962735
spellingShingle Sisira Sran
Manpreet Sran
Narmisha Patel
Prachi Anand
Lupus Enteritis as an Initial Presentation of Systemic Lupus Erythematosus
Case Reports in Gastrointestinal Medicine
title Lupus Enteritis as an Initial Presentation of Systemic Lupus Erythematosus
title_full Lupus Enteritis as an Initial Presentation of Systemic Lupus Erythematosus
title_fullStr Lupus Enteritis as an Initial Presentation of Systemic Lupus Erythematosus
title_full_unstemmed Lupus Enteritis as an Initial Presentation of Systemic Lupus Erythematosus
title_short Lupus Enteritis as an Initial Presentation of Systemic Lupus Erythematosus
title_sort lupus enteritis as an initial presentation of systemic lupus erythematosus
url http://dx.doi.org/10.1155/2014/962735
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AT narmishapatel lupusenteritisasaninitialpresentationofsystemiclupuserythematosus
AT prachianand lupusenteritisasaninitialpresentationofsystemiclupuserythematosus