Late diagnosed factor VII deficiency – a rare but significant haemorrhagic diathesis

Factor VII (FVII) deficiency is a rare but significant inherited autosomal recessive coagulation disorder, occurring with a frequency of 1 in 300,000-500,000 people. The disorder is characterised by a wide range of bleeding symptoms that do not always correlate with plasma FVII levels, from asymptom...

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Bibliographic Details
Main Authors: Karolina Małgorzata Różycka, Beata Kuczyńska, Kinga Podsiadło, Małgorzata Mitura-Lesiuk, Irena Woźnica- Karczmarz
Format: Article
Language:English
Published: Termedia Publishing House 2024-12-01
Series:Pediatria Polska
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Online Access:https://www.termedia.pl/Late-diagnosed-factor-VII-deficiency-a-rare-but-significant-haemorrhagic-diathesis,127,55422,1,1.html
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